AUTHOR=Ramirez Lucas , D’Auria Andrea , Popalzai Adeel , Sanossian Nerses 

TITLE=Bilateral Vision Loss Secondary to Pachymeningitis in a Patient with IgG4-Related Disease

JOURNAL=Frontiers in Neurology

VOLUME=5

YEAR=2014

URL=https://www.frontiersin.org/journals/neurology/articles/10.3389/fneur.2014.00192

DOI=10.3389/fneur.2014.00192

ISSN=1664-2295

ABSTRACT=<p>IgG4-related disease (IgG4-RD) is a recently recognized fibroinflammatory condition associated with disease in nearly every organ, including the meninges. A proportion of idiopathic hypertrophic pachymeningitis cases may involve a component of meningeal IgG4-RD. We present a patient with severe bilateral vision loss found to have thickening of the dura mater on MRI, and subsequently diagnosed with IgG4-RD after dural biopsy.</p>