AUTHOR=Lo Y. L. , Lim K. H. , Cheng X. M. , Mesenas S. 

TITLE=Steroid Responsive Mononeuritis Multiplex in the Cronkhite–Canada Syndrome

JOURNAL=Frontiers in Neurology

VOLUME=7

YEAR=2016

URL=https://www.frontiersin.org/journals/neurology/articles/10.3389/fneur.2016.00207

DOI=10.3389/fneur.2016.00207

ISSN=1664-2295

ABSTRACT=<p>The Cronkhite–Canada syndrome (CCS) is a rare disorder of unknown origin characterized by generalized gastrointestinal polyposis, alopecia, hyperpigmentation, and onychodystrophy. We report a case of CCS with concomitant presentation of mononeuritis multiplex. The electrophysiological findings and steroid responsiveness suggests presence of an autoimmune mechanism.</p>