AUTHOR=Kadakia Nevil , Lobritto Steven J. , Ovchinsky Nadia , Remotti Helen E. , Yamashiro Darrell J. , Emond Jean C. , Martinez Mercedes TITLE=A Challenging Case of Hepatoblastoma Concomitant with Autosomal Recessive Polycystic Kidney Disease and Caroli Syndrome—Review of the Literature JOURNAL=Frontiers in Pediatrics VOLUME=Volume 5 - 2017 YEAR=2017 URL=https://www.frontiersin.org/journals/pediatrics/articles/10.3389/fped.2017.00114 DOI=10.3389/fped.2017.00114 ISSN=2296-2360 ABSTRACT=We report a rare case of an 18-month-old female with autosomal recessive polycystic kidney disease, Caroli syndrome and pure fetal type hepatoblastoma. The liver tumor was surgically resected with no chemotherapy given. Now nine years post resection she demonstrates no local or distant recurrence and stable renal function.