AUTHOR=Ammar Nour , El-Tekeya Magda M. 

TITLE=Hallermann–Streiff syndrome: Case report with abnormal pulp calcifications

JOURNAL=Frontiers in Dental Medicine

VOLUME=Volume 3 - 2022

YEAR=2022

URL=https://www.frontiersin.org/journals/dental-medicine/articles/10.3389/fdmed.2022.965560

DOI=10.3389/fdmed.2022.965560

ISSN=2673-4915

ABSTRACT=The Hallermann-Steriff syndrome (HSS) is a disorder of development of rare occurrence affecting the craniofacial complex, with about 200 cases reported in the literature. Nonetheless, it’s distinctive facial features render it highly recognizable. We present the case of a 5 year old girl with the syndrome and review the dental manifestations and management in this patient.  In addition to the diagnostic facial features of brachycephaly with frontal bossing, beak-shaped nose, microphthalmia, and mandibular retrusion, multiple dental manifestations were noted including absence of the mandibular condyle, ghost teeth, and unusual pulpal calcifications in both the primary and permanent teeth, that have not been previously reported in a case of HSS. There is no consensus on the suitable treatment plan for HSS patients from a young age due to underreporting in of these cases the literature. In this report, we discuss pediatric dental management options for a patient with HSS condition and share their perspective of the treatment.