AUTHOR=Liu Jianwen , Zhang Ling , Chen Shuo , Lu Xin , Li Shanshan 

TITLE=Pneumatosis cystoides intestinalis in dermatomyositis: a case series report and literature review

JOURNAL=Frontiers in Immunology

VOLUME=Volume 14 - 2023

YEAR=2023

URL=https://www.frontiersin.org/journals/immunology/articles/10.3389/fimmu.2023.1194721

DOI=10.3389/fimmu.2023.1194721

ISSN=1664-3224

ABSTRACT=Pneumatosis cystoides intestinalis (PCI) in adult dermatomyositis(DM) is rarely described. We describe the clinical features and prognosis of PCI in 6 adult DM patients(4 with anti-MDA5 antibody, 1 with anti-SAE antibody and 1 with anti-TIF-1r antibody). Except for 1 patient with transient abdominal pain, the remaining five patients were asymptomatic. PCI occurred in the ascending colon in all patients, where 5 had free gas in the abdominal cavity. All of the patients did not receive excessive treatment, and PCI disappeared in 3 patients during the follow-up. In addition, we reviewed previous literature concerning on this complication.