AUTHOR=Yang Hongna , Du Binfeng , Liu Han , Yao Yong , Li Chen 

TITLE=Case Report: Life-Threatening Post-operative Hemorrhage in Klippel–Trenaunay Syndrome Associated With Hypofibrinogenemia

JOURNAL=Frontiers in Medicine

VOLUME=Volume 8 - 2021

YEAR=2021

URL=https://www.frontiersin.org/journals/medicine/articles/10.3389/fmed.2021.669793

DOI=10.3389/fmed.2021.669793

ISSN=2296-858X

ABSTRACT=Klippel-Trenaunay Syndrome (KTS) is a rare congenital disorder, characterized by venous and lymphatic malformations of the skin, soft tissue, and bone causing limb hypertrophy. Although ruptured hemorrhagic corpus luteum is the rare condition in women of reproductive age, it can result in the lethal outcome. Here, we described a patient with KTS and hypofibrinogenemia, who went through recurrent lethal postoperative bleeding due to ruptured hemorrhagic corpus luteum. This case suggested that conservative therapy might the first choice and effective therapy for the patients with KTS, who suffered from bleeding complication of surgical therapy.