AUTHOR=Du Runsen , Zheng Lihua , Liu Peng , Zhao Yaheng , Yang Yan , Zhang Lei , Zhao Zengren 

TITLE=Case report: Paroxysmal nocturnal hemoglobinuria presenting with hemorrhagic esophageal varices

JOURNAL=Frontiers in Medicine

VOLUME=Volume 10 - 2023

YEAR=2023

URL=https://www.frontiersin.org/journals/medicine/articles/10.3389/fmed.2023.1276030

DOI=10.3389/fmed.2023.1276030

ISSN=2296-858X

ABSTRACT=We report the case of a woman who was cured of hemorrhagic esophageal varices caused by Paroxysmal nocturnal hemoglobinuria (PNH) through the treatment of Transjugular intrahepatic portosystemic shunt (TIPS). PNH complicated by portal vein and visceral veins thrombosis without hepatic veins is extremely rare, and as such, may be easy to be treated incorrectly due to lack of awareness. Hemorrhagic esophageal varices due to PNH with PVT have been reported in 1 case in 1974, and We report the second.