AUTHOR=Aghetti Agnès , Sène Damien , Polivka Marc , Shor Natalia , Lechtman Sarah , Chabriat Hugues , Jouvent Eric , Guey Stéphanie 

TITLE=Cerebral Amyloid Angiopathy Related Inflammation With Prominent Meningeal Involvement. A Report of 2 Cases

JOURNAL=Frontiers in Neurology

VOLUME=Volume 10 - 2019

YEAR=2019

URL=https://www.frontiersin.org/journals/neurology/articles/10.3389/fneur.2019.00984

DOI=10.3389/fneur.2019.00984

ISSN=1664-2295

ABSTRACT=Cerebral amyloid angiopathy related inflammation (CAA-RI) is a rare form of CAA characterized by subacute encephalitic symptoms (cognitive decline, seizures, focal deficits) characterized on brain MRI by extensive and confluent white matter lesions colocalizing with lobar microbleeds. We report two cases of unusual CAA-RI mimicking meningoencephalitis without typical brain lesions on FLAIR and T2* sequences, which diagnoses were delayed. These 2 cases may extend the spectrum of CAA-RI by suggesting the possible occurrence of quite purely meningeal forms of CAA-RI.