AUTHOR=Xu Zhufei , Wang Jinhu , Mao Junqing , Xu Dan , Wu Lei , Zhou Yunlian , Li Xuejing , Chen Zhimin , Wang Yingshuo TITLE=Case report: Primary alveolar soft-part sarcoma of the lung in a child JOURNAL=Frontiers in Surgery VOLUME=Volume 10 - 2023 YEAR=2023 URL=https://www.frontiersin.org/journals/surgery/articles/10.3389/fsurg.2023.927597 DOI=10.3389/fsurg.2023.927597 ISSN=2296-875X ABSTRACT=The alveolar soft-part sarcoma involving the lung is mostly metastatic, while the primary alveolar soft-part sarcoma involving the lung occurs more rarely. Herein, we reported on a rare case of primary alveolar soft-part sarcoma of the lung, which might be with the earliest onset reported thus far. In this report, surgery was used to excise the lesion as much as possible, and its combination with chemoradiotherapy and anti-angiogenic agent may provide an important reference for the development of standard treatment or first-line treatment for these children patients.