EXPANDING THE OCULAR HORIZON: SUBPERIOSTEAL ORBITAL HEMATOMA AND ROTH SPOTS IN KNOWN CASE OF SICKLE CELL DISEASE

Rajvardhan Ravindra Patil^*Sourya AcharyaVineet KarwaRushikesh DhondgeSuhail ShaikhManjeet Kothari

• Datta Meghe Institute of Higher Education and Research, Wardha, India

Sickle cell disease is a prevalent hemoglobinopathy that is hereditary. People with sickle cell disease frequently experience vaso-occlusive crises, which lead to substantial morbidity from end-organ ischaemia and infarction. Numerous organs, including the bones, brain, lungs, spleen, retina and penis may be affected. As a result, symptoms may include painful bone crises, cerebrovascular accidents, acute chest syndrome, sequestration crises, retinal haemorrhage and priapism. In sickle cell disease, Subperiosteal orbital haemorrhage is a rare Vaso-Occlusive Crisis (VOC). Roth spots (white-centred, flame-shaped retinal haemorrhages), occurring commonly in subacute bacterial endocarditis, can also be seen in leukaemia, pre-eclampsia and hypertensive retinopathy. A 19year-old male patient with sickle cell disease(HbSS) presented to the hospital with ptosis and swelling in his right periorbital region three days after being brought to the hospital for a sickle cell crisis. It was later determined to be an acute subperiosteal orbital hematoma along with Roth spots, an uncommon clinical manifestation of sickle cell disease, only after a through clinical and radiological assessment.