CASE REPORT article
Front. Med.
Sec. Hepatobiliary Diseases
Polysplenia Syndrome Complicated by Multiple Intrahepatic Bile Duct Stones in an Adult: A Case Report
Provisionally accepted
- 1Shandong Second Medical University, Weifang, China
- 2Linyi People's Hospital, Linyi, China
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Polysplenia syndrome is a rare congenital disorder characterized by multiple spleens and complex visceral and vascular anomalies. We report an adult case admitted for multiple intrahepatic bile duct stones. Imaging revealed multiple congenital abnormalities, including polysplenia, a truncated pancreas, and absence of the superior inferior vena cava segment. Intraoperative findings confirmed extensive intrahepatic bile duct stones and biliary malformations. Surgical treatment included partial hepatectomy, bile duct exploration, and T-tube drainage. Postoperatively, the patient developed bacteremia, which resolved with targeted antibiotics. This case highlights the link between polysplenia syndrome and hepatobiliary anomalies, emphasizing the need for careful anatomical evaluation, early recognition of biliary complications, and close clinical monitoring in affected patients.
Keywords: case report, hepatobiliary anomalies, imaging, multiple intrahepatic bile duct stones, Polysplenia syndrome
Received: 29 Sep 2025; Accepted: 13 Jan 2026.
Copyright: © 2026 Zhang, Lu, Liang, Chen, Wang, Liu and Liu. This is an open-access article distributed under the terms of the Creative Commons Attribution License (CC BY). The use, distribution or reproduction in other forums is permitted, provided the original author(s) or licensor are credited and that the original publication in this journal is cited, in accordance with accepted academic practice. No use, distribution or reproduction is permitted which does not comply with these terms.
* Correspondence: Jinghua Liu
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