REVIEW article

Front. Cell Dev. Biol., 22 February 2022

Sec. Molecular and Cellular Pathology

Volume 10 - 2022 | https://doi.org/10.3389/fcell.2022.816517

Modulation of Type I Interferon Responses to Influence Tumor-Immune Cross Talk in PDAC

  • 1. Bioscience, Early Oncology, AstraZeneca, Cambridge, United Kingdom

  • 2. Institute of Cancer Sciences, University of Glasgow, Glasgow, United Kingdom

  • 3. Department of Surgery, University of Heidelberg, Heidelberg, Germany

  • 4. Section Surgical Research, University Clinic Heidelberg, Heidelberg, Germany

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Abstract

Immunotherapy has revolutionized the treatment of many cancer types. However, pancreatic ductal adenocarcinomas (PDACs) exhibit poor responses to immune checkpoint inhibitors with immunotherapy-based trials not generating convincing clinical activity. PDAC tumors often have low infiltration of tumor CD8+ T cells and a highly immunosuppressive microenvironment. These features classify PDAC as immunologically “cold.” However, the presence of tumor T cells is a favorable prognostic feature in PDAC. Intrinsic tumor cell properties govern interactions with the immune system. Alterations in tumor DNA such as genomic instability, high tumor mutation burden, and/or defects in DNA damage repair are associated with responses to both immunotherapy and chemotherapy. Cytotoxic or metabolic stress produced by radiation and/or chemotherapy can act as potent immune triggers and prime immune responses. Damage- or stress-mediated activation of nucleic acid-sensing pathways triggers type I interferon (IFN-I) responses that activate innate immune cells and natural killer cells, promote maturation of dendritic cells, and stimulate adaptive immunity. While PDAC exhibits intrinsic features that have the potential to engage immune cells, particularly following chemotherapy, these immune-sensing mechanisms are ineffective. Understanding where defects in innate immune triggers render the PDAC tumor–immune interface less effective, or how T-cell function is suppressed will help develop more effective treatments and harness the immune system for durable outcomes. This review will focus on the pivotal role played by IFN-I in promoting tumor cell–immune cell cross talk in PDAC. We will discuss how PDAC tumor cells bypass IFN-I signaling pathways and explore how these pathways can be co-opted or re-engaged to enhance the therapeutic outcome.

Introduction

PDAC accounts for more than 90% of pancreatic malignancies and is currently the third leading cause of cancer-related death in Western countries (Luchini et al., 2016; Pishvaian and Brody, 2017; McGuigan et al., 2018). High mortality rates are mainly due to late detection, a high level of tumor heterogeneity, and a desmoplastic immunosuppressive microenvironment (Ryan et al., 2014). Although advances in treatment have significantly increased 5-year survival rates for many other cancer types (Brahmer et al., 2012; Nixon et al., 2018), the overall 5-year survival rate for PDAC is only 10% (Siegel et al., 2021). Mono- and multi-agent chemotherapy regimens are the standard treatments. Conventional cytotoxic therapies in PDAC include the nucleoside analog gemcitabine which may be combined with the microtubule poison nab-paclitaxel, and FOLFIRINOX (folinic acid, fluorouracil, irinotecan, and oxaliplatin) (Mohammad, 2018). Both treatment regimens improve the overall survival for patients with localized disease but are less effective for the majority of patients who are diagnosed with advanced or metastatic disease (Bliss et al., 2014). Improvements in progression-free survival have been achieved for patients with BRCA-mutated tumors when PARP inhibitors are used as maintenance treatment following chemotherapy (Golan et al., 2019). Therefore, despite incremental advances, there is an urgent need for new therapeutic approaches.

Immune checkpoint inhibitors (ICIs) are revolutionizing the treatment of cancer, mainly when used in combination with chemotherapy or radiotherapy. In ICI-sensitive diseases such as non-small-cell lung cancer (Lim et al., 2020), head and neck squamous cell carcinoma (Burtness et al., 2018), and triple-negative breast cancer (Schmid et al., 2018), combining chemotherapy and immunotherapy generates durable responses in a subset of patients (Reck, 2018). Combining standard-of-care chemotherapy with ICIs has been largely unsuccessful in PDACs [reviewed in Henriksen et al. (2019)], albeit in trials where patients were not selected based on any favorable biomarker.

PDAC is generally considered immunologically cold with a low incidence of tumor-infiltrating lymphocytes (TILs) (Stromnes et al., 2017; Blando et al., 2019; Gorchs et al., 2019; Seo et al., 2019), thought to be a result of poor T-priming by the tumor. Poor T-cell priming or activation in PDAC is commonly attributed to low neo-antigen content, although PDAC tumors do have potentially actionable neo-epitopes. Indeed PDAC tumors with good quality neo-antigens are associated with better outcomes (Bailey et al., 2016a; Balachandran et al., 2017). How PDAC tumor cells evade the immune system is unclear. Tumor cell intrinsic mechanisms play important roles in regulating both intrinsic and therapy-induced engagement or avoidance of the innate or adaptive immune systems (reviewed in Wellenstein and de Visser (2018)). Tumor cells can evade the immune system by reducing antigen processing, cell surface antigen presentation, or expression of cell surface proteins that engage innate immune cells. They also secrete growth factors, chemokines, and cytokines that shape an immunosuppressive microenvironment (Grivennikov et al., 2010; Gonzalez et al., 2018). In addition to high tumor T-cell infiltration, “immunologically hot” tumors that respond well to immunotherapy-based treatment typically express IFN-I (IFN-α, -β), type II interferons (IFN-II) (IFN-γ), and high levels of interferon-stimulated genes (ISGs) that sustain antitumor immune responses (Gajewski et al., 2013; Corrales et al., 2015; Wang and Wang, 2017). PDAC does not commonly show high expression of interferons or ISG signatures, but if tumor-targeted therapies such as chemotherapy or targeted agents induce robust IFN-I and/or innate responses, immune system engagement is more likely to occur. Understanding why this fails in PDAC could guide new therapeutic or patient selection approaches that will ultimately harness the immune system to deliver more durable clinical responses.

IFN Cascade in Tumors

The IFN cascade in tumors is complex, as shown in Figure 1. Type I interferons (IFN-α and -β) can be expressed as a result of stress damage to tumor cells or stromal cells such as macrophages (Medrano et al., 2017). Type I interferons stimulate many cells in the TME driving both tumor cell and immune cell responses (Zitvogel et al., 2015). The secretion of type I interferons can kill or senesce tumor cells and directly or indirectly stimulate T cells, natural killer (NK) cells (Fenton et al., 2021), and potentially macrophages or dendritic cells to secrete the type II interferon (IFN-γ). The type II interferon is one marker of cytotoxic immune effector cells in the TME (Bhat et al., 2017). The IFN system can be self-enhancing. For example, chemotherapy-mediated damage may induce the secretion of IFNs from both tumor cells and cells in the TME amplifying immune cell activation throughout the tumor (Budhwani et al., 2018). Understanding the cause and effect in this pivotal cascade is challenging as both type I and -II interferons drive common signaling cascades. IFN responses in tumors are commonly monitored using bulk RNA gene expression signatures which, in the absence of single-cell sequencing approaches, are unable to distinguish which cells initiate, or which cells respond to IFN-driven signals. This complex interplay between cells in tumors presents different opportunities to drive IFN induction and activation of antitumor immune cell activity, even when normal pathways are dysfunctional.

FIGURE 1

Chemotherapy and Immunomodulation in PDAC

Chemotherapeutic agents are first-line standard-of-care treatments for PDAC. Despite that the combination of gemcitabine with nab-paclitaxel and FOLFIRINOX increases efficacy compared to gemcitabine alone, patients’ overall survival rates remain particularly low, and toxicity limits their use (Conroy et al., 2011; Von Hoff et al., 2013; Javed et al., 2019). PDAC patients rapidly develop resistance to chemotherapy through both tumor cell intrinsic and tumor microenvironmental factors (Chand et al., 2016). Despite the limited benefit, there is evidence of chemosensitivity in subsets of PDAC patients. For instance, several clinical trials report increased sensitivity to platinum-based chemotherapy in DNA damage repair (DDR)-deficient patients (Pishvaian et al., 2019; Golan et al., 2014; O'Reilly et al., 2020; Blair et al., 2018).

In addition to tumor cell cytotoxic activity, chemotherapies may also potentiate immunomodulatory responses (Bailly et al., 2020; Piadel et al., 2020). Treatment of PDAC with gemcitabine has been associated with enhanced T-cell-mediated responses through increased naive T-cell activation (Plate et al., 2005) and CD8+ T-cell function, which is in part dependent on dendritic cell (DC) activity (Plate and Harris, 2004). In addition, following gemcitabine or FOLFIRINOX treatment, suppressive immune populations such as regulatory T cells (Tregs) (Kan et al., 2012; Homma et al., 2014; Liu et al., 2017; Hui et al., 2021; Sams et al., 2021) and myeloid-derived suppressor cells (MDSCs) (Suzuki et al., 2005; Vincent et al., 2010; Eriksson et al., 2016; Wu et al., 2020a) are downregulated in patients and in preclinical models. In mice, gemcitabine also increases the immunogenicity of tumor cells (Liu et al., 2010). Therefore, global changes in the immune profile of tumors following treatment can be both direct and indirect. Consistent with these findings, an in vitro analysis of the proteasome and immunopeptidome of human PDAC cell lines showed that gemcitabine induces overexpression of MHC-I molecules (Gravett et al., 2018) with novel peptides. Similarly, in KPC tumor-bearing mice, prolonged treatment with gemcitabine leads to increased MHC-I along with increased secretion of CCL/CXCL chemokines (Principe et al., 2020). Gemcitabine and oxaliplatin (the platinum-based element of the FOLFIRINOX regimen) also induce the expression of immunogenic cell death-associated damage-associated molecular patterns (DAMPs) including ATP and HMGB1 (Hayashi et al., 2020; Smith et al., 2021), which can signal NK cells and potentiate the innate immune system. Finally, in PDAC patients, chemotherapy has been shown to stimulate the immune response by increasing T-cell response to tumor-associated antigens (Mandili et al., 2020).

The immunostimulatory effects of these chemotherapeutics highlight their potential use in combination with immuno-oncology therapies. Especially with ICIs, in vitro and in vivo studies suggest that gemcitabine increases the expression of immune checkpoint molecules such as PD-L1 (Principe et al., 2020; Smith et al., 2021). While favorable changes in the immune profile of tumors can be seen following treatment, why these changes do not translate into more sustained benefit alone or in combination with other therapies remains unclear. This may be because the impact of chemotherapy on tumor cells is rapidly reversed or because the TME remodels quickly restraining the potential benefits. Understanding the kinetics of induction and recovery in the tumor cells versus TME following chemotherapy treatment would give useful insights.

Treatments Targeting Immune Cells Alone Are Not Active in PDAC

Clinically, antitumor immune responses are stimulated by therapeutic antibodies that target T-cell checkpoints such as PD-1/PD-L1 and, to a lesser extent, CTLA-4/B7H4, which act to inhibit T-cell function. In PDAC, both PD-L1 and CTLA-4 are upregulated and associated with poor prognosis (Nomi et al., 2007; Cancer Genome Atlas Resea, 2017). Early trials showed no beneficial response to ipilimumab (anti-CTLA-4 monoclonal antibody) in patients with metastatic and locally advanced PDAC (NCT00112580), although treatment was associated with advanced toxicity (Royal et al., 2010). These results were mirrored with another anti-CTLA-4 monoclonal antibody (NCT02527434), tremelimumab (Sharma et al., 2018). Anti-PD-L1 monoclonal antibodies showed no objective response in the 14 PDAC patients in a phase I clinical trial (NCT00729664) (Brahmer et al., 2012), while disease control (partial response or stable disease) was observed in 21% of the 29 PDAC patients in another phase I trial with durvalumab (NCT01693562) (Segal et al., 2014). Interestingly, PD-1 blockade with pembrolizumab showed a 62% objective response in a phase II clinical trial in 8 PDAC patients harboring mismatch repair (MMR) deficiency (NCT01876511) (Le et al., 2015). Pembrolizumab has now been approved by the Food and Drug Administration (FDA) for solid tumors harboring MMR defects including PDAC (Le et al., 2017); however, these only represent about 1% of PDAC patients (Hu et al., 2018). In the other patients, very limited responses to ICIs have been observed. Some studies are still ongoing such as a phase II trial of atezolizumab (NCT03829501), as well as combinations of antibodies targeting CTLA-4 and PD1/PD-L1 (NCT01928394). Consistent with findings in other tumor types, it is probable that combination approaches, for example, with chemotherapy, will be required.

Cell-based vaccines alone or combined with chemotherapy and ICI present alternative strategies to achieve tumor-targeted immune stimulation. The granulocyte–macrophage colony-stimulating factor (GM-CSF)-secreting allogeneic pancreatic tumor cell vaccine (GVAX) consists of irradiated human allogeneic pancreatic tumor cells that secrete GM-CSF (Lutz et al., 2011). It is given as a cellular vaccine to present pancreatic cancer cell epitopes and also improve antigen presentation by inducing GM-CSF-mediated maturation of dendritic cells. Despite showing positive changes in the immune microenvironment and potential efficacy in early clinical trials (Lutz et al., 2014), a more extensive phase II trial in combination with the CTLA4 targeting ICI ipilimumab failed to show increased clinical benefit (Wu et al., 2020b). Studies like this which assess immune biomarker changes suggest that while the activation of immune cells can be achieved in PDAC, they do not translate into a durable effect. The use of GM-CSF in GVAX is interesting as it has both positive and negative effects. In addition to promoting dendritic cell recruitment, increased GM-CSF can promote pancreatic tumor development (Pylayeva-Gupta et al., 2012) and drive recruitment of immunosuppressive immune cells (Bayne et al., 2012).

Chemotherapy and Immunotherapy Combinations in PDAC

Greatest response to ICI treatment is observed in combination with chemotherapy. Both chemotherapy and radiotherapy can increase antitumor immunity by inducing immunogenic tumor cell death and cell stress signaling pathways, and depleting immunosuppressive cells or stimulation of T cells to complement the effects of ICI treatment (Burtness et al., 2018; Galluzzi et al., 2020; Salas-Benito et al., 2021). In PDAC, the combination of ICI with chemotherapy is marginally more effective than monotherapy ICI treatment; however, benefits remain limited. Combining ipilimumab with gemcitabine in a phase Ib trial (NCT01473940) resulted in 2 partial responses and five stable diseases out of 11 patients (Kamath et al., 2020). In a larger phase I clinical trial that combined tremelimumab and gemcitabine (NCT00556023), 2 out of 28 PDAC patients showed a partial response and seven stable diseases (Aglietta et al., 2014). Chemotherapy in combinations with ICIs compared to chemotherapy alone conferred longer overall survival in a clinical trial comprising 58 patients with advanced PDAC (Ma et al., 2020). Other phase I and Ib trials have combined nivolumab or pembrolizumab with nab-paclitaxel and gemcitabine. In the first of these trials (NCT02309177), nearly half of the 50 PDAC patients had stable disease, 8 partially responded and one completely responded (Wainberg et al., 2020). In the second trial (NCT02331251), all patients achieved disease control, of which 3 showed partial response (Weiss et al., 2018). In a large phase II clinical study looking at the combination of gemcitabine and nab-paclitaxel with or without durvalumab and tremelimumab (NCT02879318), no benefits in terms of progression-free and overall survival were observed in the 191 metastatic PDAC patients; however, disease response rates were improved (Renouf et al., 2020).

Overall, chemoimmunotherapy improves response rates in PDAC compared to ICI or chemo monotherapies; however, these benefits remain limited and do not impact survival. Hence, the combination of ICI and chemotherapy is relevant in PDAC, but further potentiation of the immune system is needed to obtain significant benefit.

PDAC Immune Microenvironment and IFN-I

PDAC is characterized by a dense tumor stroma mainly composed of the extracellular matrix, fibroblasts, and vasculature (Hosein et al., 2020). It also contains immunosuppressive cell types such as MDSCs and Tregs, which accumulate during disease progression to suppress CD4+ and CD8+ T-cell function, contributing to poor prognosis (Clark et al., 2007; Bayne et al., 2012; Thyagarajan et al., 2019; Huber et al., 2020).

Transcriptomic profiling of PDAC has identified 2 broad consensus subtypes, namely, classical and basal-like, which largely represent predominant neoplastic gene programs (Collisson et al., 2011; Moffitt et al., 2015; Bailey et al., 2016b). Additional transcriptomic subtypes, such as ADEX/exocrine-like and immunogenic, exhibit significant overlap with the classical subtype (Bailey et al., 2016b). Deconvolution of bulk transcriptomic RNAseq data using validated immune cell type signatures has demonstrated that the 2 consensus subtypes of PDAC are associated with distinct immune profiles (Bailey et al., 2016b; Karamitopoulou, 2019; Santiago et al., 2019). The basal-like subtype is usually associated with an “immune escaping” phenotype, with high Tregs and suppressive macrophages (M2 or m-MDSC) and low cytotoxic T cells (Wartenberg et al., 2018; Karamitopoulou, 2019). The classical subtype appears relatively “immune rich,” with lower Tregs and M2 macrophages and a higher percentage of CD4+ and CD8+ T cells as well as inflammatory (M1) macrophages (Wartenberg et al., 2018). IFN-I plays a pivotal role in regulating immunomodulatory chemokines and cytokines that in turn reshape the tumor immune microenvironment. In addition, IFN-I upregulates the expression of MHC-I and antigen presentation (Yang et al., 2004; Wan et al., 2012), increasing tumor cell recognition by the immune system. However, the presentation of neoantigens at the cell surface by MHC-I may be reduced by the targeted degradation of MHC-I in PDAC cells (Yamamoto et al., 2020). With respect to immune cells, IFN-I also enhances antigen presentation and cross-priming of the immune system as it stimulates DC activation and maturation (Lorenzi et al., 2011; Binnewies et al., 2019). In PDAC, DCs are rare and decrease upon disease progression, further limiting antigen cross-presentation and T-cell activity (Hiraoka et al., 2011). Similarly, IFN-I mediated activation of NK cell cytotoxicity (Swann et al., 2007; Bergamaschi et al., 2020) is impaired in PDAC (Marcon et al., 2020). Tumor-associated macrophages (TAMs) represent a dominant immune cell population in PDAC. High levels of the M2 or suppressive macrophage phenotype are associated with poor prognosis and disease progression (Kurahara et al., 2011; Candido et al., 2018). IFN-I can promote the antitumor M1 or inflammatory macrophage phenotype and enhance phagocytic functions (U'Ren et al., 2010; Sampson et al., 1991).

The PDAC TME is accepted as being highly immunosuppressive (Figure 2). Many preclinical studies have shown the potential for TME modulators to enhance immunotherapy. Few have yet to translate to the clinic, but a number of agents targeting myeloid cells or stromal cells are being tested clinically with ICI or in chemotherapy/ICI combinations (Liu et al., 2019; Roma-Rodrigues et al., 2019; Ho et al., 2020; Zhong et al., 2020). CD4+ and CD8+ T cells are abundant at the initial stages of PDAC tumor development, and their presence and activation decrease during disease progression due to an immunosuppressive microenvironment (Knudsen et al., 2017). The dense fibroblastic stroma limits T-cell trafficking and access to the TME. MDSCs and Tregs suppress T-cell activation, which is already limited by poor antigen cross-presentation. Type I IFNs induce the secretion of cytokines such as CCL5, CXCL9, and CXCL10, which can attract T cells (Lorenzi et al., 2011) along with factors that negatively modulate immunosuppressive regulatory T cells (Gangaplara et al., 2018), facilitating effective cytotoxic T-cell functions. However, targeting different elements of the TME by modulation of myeloid cells with CXCR2, CCR2, or CSF1R (Steele et al., 2016; Candido et al., 2018; Nywening et al., 2018; Siolas et al., 2021) or CXCR4 antagonists (Feig et al., 2013; Biasci et al., 2020) can regulate the TME through changes in myeloid cells and stroma, improving preclinical responses to immune checkpoint inhibitors. Myeloid cells and the stroma can initiate IFN-I responses or be triggered as a result of tumor cell damage. The suppressive cell phenotypes in the TME may have limited capacity to enhance IFN-I or other innate signals. Targeting stromal cells in addition to tumor cells and T cells with chemotherapy and ICI may yield better clinical responses.

FIGURE 2

Genetic Features of PDAC May Influence Immune Cell Function

PDAC tumors exhibit genetic characteristics that may underpin the lack of observed intrinsic responses to immune checkpoint therapy. Mutational heterogeneity is associated with a better response to ICI (Reuben et al., 2017; Iyer et al., 2021; Vitale et al., 2021). While PDAC tumors have many low-abundance mutations, there are four dominant driver mutations, namely, oncogenic activation of KRAS and inactivation of the tumor suppressors TP53, CDKN2A, and SMAD4 (Jones et al., 2008). CDKN2A loss correlates with reduced immune infiltrates in several tumor types, including PDAC (Siemers et al., 2017). Retrospective analysis of clinical data in different tumor types revealed an association of CDKN2A loss with worse overall and progression-free survival following ICI treatment in combination with chemotherapy (Horn et al., 2018; Gutiontov et al., 2021). Preclinically, specific loss of CDKN2A has also induced resistance to immunotherapy (Gutiontov et al., 2021; Han et al., 2021). CDKN2A is located on the human chromosome 9p21 locus (Sasaki et al., 2003), in close proximity to MTAP, JAK2, and a large cluster region coding for 16 IFN-I genes (Diaz, 1995). Co-deletion of these genes is common, for example, concomitant mutation of CDKN2A and MTAP in PDAC is estimated at 26% according to The Cancer Genome Atlas (TCGA) dataset (Mavrakis et al., 2016) and may also contribute to resistance to ICI-based therapy. In melanoma, CDKN2A-associated JAK2 mutation leads to loss of functional IFN-γ signaling which also limits response to immunotherapy (Horn et al., 2018). CDKN2A loss results in the activation of CDK4/6 kinases. In preclinical models, treatment with CDK4/6 inhibitors re-sensitized melanoma tumors (Jerby-Arnon et al., 2018) and syngeneic models (Deng et al., 2018) to treatment. In preclinical pancreatic cancer models, CDK4/6 inhibitors can influence tumor growth (Chou et al., 2018) and combine to sustain antitumor effects following chemotherapy (Salvador-Barbero et al., 2020). Combining the CDK4/6 inhibitor palbociclib and the MEK inhibitor trametinib not only reduced growth of patient-derived xenograft models but also enhanced response to PD-1 inhibition in a transplantable tumor model derived from the KPC model (Knudsen et al., 2021). This suggests that appropriate combinations with CDK4/6 inhibitors in PDAC may enhance immune response in tumors with loss of CDKN2A through tumor-centric and possibly TME mechanisms. In addition, it is not known whether loss of SMAD4 and p53 and mutation of KRAS also cooperate with CDKN2A/B loss to further increase the tumor immune-resistant status. For example, in lung cancer, loss of the tumor suppressor STK11 is regarded as driving resistance to both chemotherapy and immunotherapy (Skoulidis et al., 2018). Interestingly, it is the co-occurrence of a RAS mutation that renders these tumors most resistant to ICI-based treatments (Ricciuti et al., 2021). Therefore, given the dominant mutations in pancreatic cancer, it may be challenging to achieve strong immune activation.

The IFN-I genes are also expressed on Chr9 (close to CDKN2A and MTAP) and can sometimes be lost. It is also possible that even when not deleted, the disruption of other genes in the locus may reduce gene expression. Tumor cells with reduced IFN-I expression may evade immune cells due to a lack of IFN-α and -ß cross talk to the immune system. Loss or reduction of this central coordinator mechanism for the tumor–immune interaction would contribute to immune escape and ICI resistance (Grard et al., 2021), especially in the context of tumor-targeted combination approaches.

Less than 4% of PDAC tumors comprise mutations in DNA damage repair genes, such as BRCA1, BRCA2, or PALB2 (Waddell et al., 2015; Bailey et al., 2016b). BRCA1- and BRCA2-deficient tumors are associated with increased immune infiltrates in some patients; however, rates of response to ICI are low (Sønderstrup et al., 2019; Wen and Leong, 2019; Mei et al., 2020). Recent evidence in mouse models of breast and colorectal cancers suggests that BRCA2-deficient tumors are more susceptible to ICI than BRCA1-deficient tumors (Samstein et al., 2020; Zhou and Li, 2021). ARID1A alteration is found in about 6% of PDAC patients (Cancer Genome Atlas Resea, 2017) and has been observed to modulate responses to immunotherapy. In fact, ARID1A deficiency has been shown to lead to the inactivation of MMR genes, increase in PD-L1 expression, increase in tumor mutation burden through DDR dysfunction via ATR inhibition, and TIL recruitment and inflammatory response by IL-6 production (Hu et al., 2020; Wang et al., 2020). Consistently, ARID1A-mutated patients showed better response to ICI with prolonged progression-free and overall survival observed in various solid cancer types, suggesting that ARID1A deficiency may be a patient selection biomarker for ICI combinations (Jiang et al., 2020; Okamura et al., 2020). It is unlikely that mutation status alone will be sufficient to drive patient segmentation in PDAC; therefore, new strategies to define patient subsets for specific combination treatments will be important.

Triggering Innate Immune Responses in PDAC

To maintain immunological homeostasis, an organism must discriminate self from non-self. Upon infection, viral nucleic acids stimulate antiviral responses, but the same innate pathways can also recognize damaged self-DNA and/or RNA (Iurescia et al., 2018). Activation or dysfunctional regulation of proteins involved in these pathways causes disorders known as interferonopathies, which are associated with increased interferon production. For example, the Mendelian autoinflammatory disorder Aicardi–Goutieres syndrome is a type I interferonopathy caused by mutations in genes such as TREX1, which plays a pivotal role in endogenous nucleic acid sensing (Tao et al., 2019; Baris et al., 2021).

Chromosome instability (CIN) is a hallmark of cancer (Pikor et al., 2013), and damaged DNA within micronuclei has been demonstrated to induce innate immune responses (Mackenzie et al., 2017). Although nuclear DNA is shielded from cytoplasmic nucleic acid sensors by the nuclear membrane, membrane rupture during mitosis and/or cytotoxic stress can expose nucleic acids to pattern recognition receptors (PRRs). PRR stimulation activates the immune system through the modulation of the tumor cell surface and secreted proteins (Maciejowski and Hatch, 2020). PDAC is characterized by DDR deficiency, CIN, and metabolic stress (Bailey et al., 2016b; Aguirre et al., 2018). These tumor cell intrinsic properties should trigger canonical innate immune pathways. However, responses are limited in PDAC because of the activation of anti-autoimmune regulatory mechanisms that facilitate immune evasion and disease progression (Moskovitz et al., 2003; Waddell et al., 2015; Bailey et al., 2016b).

DNA- and RNA-Sensing Signaling Pathways in PDAC

Chemotherapy, radiation, and therapeutics that damage DNA can prime immune responses through the stimulation of nucleic acid-sensing pathways. DNA or RNA fragments stimulate innate immune pathways in the tumor, including the secretion of IFN-I, which cross talks to immune cells (Figure 3). Double-stranded DNA (dsDNA) is generally located in the nucleus. However, in cells with CIN, due to DNA damage and/or defects in DNA damage repair machinery, cell cycle regulation (Fenech et al., 2011; Crasta et al., 2012; Sahin et al., 2016), or drug treatment dsDNA is found in the cytoplasm. Canonically, cytoplasmic dsDNA is sensed by cGAS (cyclic GMP-AMP synthase), a DNA-binding protein that catalyzes the production of the second messenger cGAMP (2′-3′ cyclic GMP-AMP) (Li et al., 2013). cGAMP interacts with the adaptor protein stimulator of interferon genes (STING) (Ablasser et al., 2013; Kato et al., 2017), causing dimerization and translocation from the endoplasmic reticulum to the Golgi (Ishikawa and Barber, 2008; Ishikawa et al., 2009). STING activates the kinase TBK1, driving translocation of the transcription factor IRF3 to the nucleus and inducing the expression of IFN-I (Liu et al., 2015). This sensing pathway can also be triggered in non-tumor cells with build-up of cytoplasmic dsDNA in the TME, with a transfer of dsDNA and/or cGAMP from tumor to host cells (Schadt et al., 2019; Zou et al., 2021). STING and TBK1 activation trigger the recruitment of IκB kinases (IKK), which results in NF-κB pathway activation by phosphorylation of the inhibitory IκB, thus enabling the translocation of NF-κB transcription factors to the nucleus (Abe and Barber, 2014; Yum et al., 2021). Similarly, the NF-κB and IFN-I pathways can be activated by sensing DNA through endosomal TLR3 and TLR9 (Kawai and Akira, 2007). The STING-TBK1 signaling axis has shown functionality in several PDAC models upon stimulation with STING agonists or modulators (Jing et al., 2019; Ren et al., 2020; Liang et al., 2021; Miller et al., 2021). However, it is not clear whether STING responses are functional in the majority of PDAC tumors, or whether the pathway is attenuated as tumors progress. Interestingly, cGAS-STING pathway agonists show efficacy in preclinical PDAC tumors by targeting macrophages in the TME (Ager et al., 2021), suggesting that tumor cells or cells within the TME may respond to activation of this pathway.

FIGURE 3

RNA sensing allows cells to detect cytoplasmic double-stranded RNAs and specific single-stranded RNAs, which are usually signs of viral infection. However, following treatment (Ranoa et al., 2016), cytoplasmic dsRNAs may accumulate in treated cells and be recognized by RNA-sensing pathways. Cytoplasmic dsRNAs are sensed, according to their size and location, by toll-like receptors such as TLR3 located in endosomes (Alexopoulou et al., 2001) or cytosolic ubiquitously expressed RIG-I-like receptors (RLRs) such as RIG-I and melanoma differentiation associated gene-5 (MDA5) (Hornung et al., 2006; Kato et al., 2006). The former signals through the adaptor protein TRIF, while the latter induces the activation of mitochondrial antiviral signaling protein (MAVS). Following a cascade of downstream events, both converged on TBK1, and subsequent IRF3 activation results in IFN-I and NF-kB responses (Seth et al., 2005; Sun et al., 2006; Kawai and Akira, 2018). These pathways are functional in preclinical models of PDAC following stimulation by PRR agonists (Duewell et al., 2014; Metzger et al., 2019). It is therefore possible that triggering these pathways with radiation or chemotherapy, or directly with pathway agonists to target STING or RIG-I in both tumor and the TME could add benefit as part of a combination strategy with ICI.

Mechanisms Regulating DNA- and RNA-Induced IFN Responses in PDAC

As cancer cells are altered-self cells, recognition by the immune system can be facilitated by damage-associated molecular patterns (DAMPs). The term DAMP encompasses a group of molecules that can signal in a cell-intrinsic manner or trigger cross talk to the innate immune system after being released from damaged cells (e.g., cGAMP, DNA or RNA fragments, or intracellular proteins such as actin, HMGB1, and histones) (reviewed in depth in Gong et al. (2020)). DAMPs commonly activate a range of PRRs and trigger IFN-I responses (Teijaro, 2016; Musella et al., 2017) as a result of genetic changes or drug treatments (Stetson and Medzhitov, 2006; Reikine et al., 2014). Tumor cells commonly undergo changes that abrogate or make these sensing pathways less effective or reduce the secretion of DAMPs.

TREX1 and ENPP1 can antagonize signals resulting from damaged DNA (Figure 3). Both enzymes are highly expressed in PDAC (Carozza et al., 2020), and overexpression reduces the activation of the cGAS-STING pathway. TREX1 is an ER-associated exonuclease that degrades cytosolic dsDNA and therefore restrains cGAS-STING activation (Mohr et al., 2021). ENPP1 is a transmembrane protein with a hydrolase extracellular domain capable of cleaving a variety of substrates including cGAMP preventing activation of the cGAS-STING pathway in surrounding cells (Li et al., 2021). In preclinical studies, cGAMP plays a role in driving cross talk to the TME following radiation treatment (Vijayan et al., 2017). Moreover, cGAMP hydrolysis by ENPP1 results in the formation of AMP, a substrate of NT5E, a transmembrane hydrolase that catalyzes the formation of adenosine (Allard et al., 2019) which also drives immunosuppression in the TME (Stagg et al., 2010; Vijayan et al., 2017). Whether cGAMP and ENPP1 play a similar role in PDAC has not been explored in detail.

Epigenetic regulation is another strategy cancer cells use to modulate response to DAMPs and attenuate PRR activation or downstream signaling. cGAS and STING are epigenetically silenced by the methylation of their respective promoter regions in PDAC (Konno et al., 2018). KRAS and MYC aberrations, which are among the most common in PDAC, suppress IFN-I response by inducing binding of the Myc–MIZ1 complex to IFN regulator promoters (IRF5, IRF7, STAT1, and STAT2) (Muthalagu et al., 2020). Posttranslational modifications such as methylation, phosphorylation, sumoylation, acetylation, and ubiquitination also modulate constituents of the cGAS-STING pathway in different cancer types (Brown et al., 2018; Tan et al., 2018; Wu et al., 2019; Zhang et al., 2020; Ma et al., 2021). Interestingly, the epigenetic factor PRMT5, which is upregulated in PDAC and correlates with poorer survival (Qin et al., 2019), directly methylates cGAS and limits binding to dsDNA (Muthalagu et al., 2020). It is possible that inhibiting TREX1 or ENPP1 function could result in more effective activation of DNA-sensing pathways in specific subsets of PDAC (e.g., subsets with defects in DNA repair pathways), or following treatment with chemotherapy or radiation.

RNA-sensing pathways can also initiate damage signals, and proteins that prevent sensing of dsRNA can be upregulated in tumors (Figure 3). For example, the protein STAU1 stabilizes dsRNA, preventing recognition by RNA-sensing proteins (Chengjin et al., 2018), while ADAR1 targets modified RNA fragments, assisting evasion from triggering of RNA-sensing complexes (Mehdipour et al., 2020). ADAR1 destabilizes specific inverted Alu repeats in dsRNA motifs by catalyzing adenosine-to-inosine editing. Alu repeats are a major source of drug-induced dsRNA, and their destabilization by ADAR1 limits activation of MDA5 and RIG-I (Pichlmair and Reis e Sousa, 2007; Liddicoat et al., 2015; Wang et al., 2017; Herbert, 2019). While the regulation of the RNA-sensing machinery has not been widely explored in PDAC, ADAR1 is upregulated in PDAC and is associated with poor prognosis (Sun et al., 2020). Interestingly, IFN-I also induces tumor cell apoptosis and DAMP release in cell lines (Kimura et al., 2003; Gómez-Benito et al., 2007; Kazaana et al., 2019), including PDAC cells (Vitale et al., 2007) (Figure 1).

The potential to harness these pathways to initiate an immune trigger in PDAC is underexplored. Chemotherapy may trigger responses in the tumor cells or the TME, while fragments released from the tumor may stimulate the TME. Given the high density of macrophage-like cells found in PDAC and the high stromal content, agonists of DNA- or RNA-sensing pathways could also play an important role in enhancing more sustained immune responses in the appropriate treatment regimens.

Therapeutic Strategies to Restore Tumor IFN-I or Innate Responses in PDAC to Maximize Immune Cell Engagement

There are a variety of pathways that can be activated or inhibited to elicit an interferon response. Reducing the presence of DAMPs is a strategy for cancer cells to evade NA sensing; therefore, increasing DAMP expression could initiate an effective IFN-I response. This could be achieved by targeting the DNA damage response. Conventional treatments such as chemo- and radiotherapy act as potent DNA-damaging agents that can induce IFN-I and recruit antigen-presenting cells (Lugade et al., 2005). PARP inhibition leads to the accumulation of cytosolic DNA by blocking DNA repair. Recently, the PARP inhibitor (PARPi) olaparib has been approved by the FDA for the treatment of BRCA-mutated metastatic PDAC after having shown promising results in the POLO clinical trial (Golan et al., 2019). Interestingly, phase II and III clinical trials have shown PARPi efficacy in patients with non-mutated BRCA1/2 ovarian cancer, suggesting a potential use in a broader spectrum of patients (Gelmon et al., 2011; Mirza et al., 2016). In subcutaneous mouse syngeneic tumor models, the combination of PARPi and anti-PD-L1 treatment increases therapeutic efficacy in BRCA-deficient tumors (Shen et al., 2019). In PDAC tumors with BRCA mutation, inhibiting PARP in combination with ICI may give further enhanced benefits. This same principle could apply to other PDAC subtypes with deficient DNA repair pathways, perhaps giving similar but more sustained IFN-I and innate stimulation than that achieved with chemotherapy.

Inhibiting the function of ATM which repairs double-stranded breaks also increases cytoplasmic DNA (Zhang et al., 2019), TBK1 phosphorylation, and IFN-I expression in preclinical PDAC models. Interestingly, ATM loss of function (which renders cells dependent on the alternative DNA repair enzyme ATR) has been associated with an immune-rich phenotype in PDAC (Wartenberg et al., 2018). Preclinically inhibiting ATR alone or in combination with PARP inhibition has shown therapeutic benefit (Dunlop et al., 2020; Dreyer et al., 2021; Gout et al., 2021; Parsels et al., 2021). Finally, inhibiting DNA-PK, which facilitates non-homologous end joining in combination with radiotherapy increases micronuclei formation and DNA damage, activates IFN-I and increases CD8+ T-cell response (Ciszewski et al., 2014). Therefore, in specific patient subgroups, PARP, ATM, ATR, or DNA-PK inhibitors given chronically (alone or in combination) may sustain DNA damage to trigger immune engagement. Indeed targeting these enzymes with more chronic treatment may be more effective at driving IFN-I and other damage responses than chemotherapy, which only achieve short transient stimulation of these pathways (Reisländer et al., 2020).

There are other ways to increase nucleic acid-mediated activation of DNA damage or stress pathways. Although not investigated in PDAC, the nucleoside analog 6-thio-DG, which induces DNA damage and telomerase stress, activates STING, IFN-I signaling, and CD8+ T cells in colorectal cancer models (Mender et al., 2020). The DNA-sensing cGAS-STING pathway can also be targeted directly with agonists. Intratumoral injection of the STING agonist ADU-S100 combined with radiotherapy increased tumor interferon-stimulated gene expression and T-cell infiltration, causing a reduction in local and distal tumor burden in PDAC murine models (Vonderhaar et al., 2021). Combining STING agonists with anti-PD-1 also showed promising antitumor activity in preclinical mouse syngeneic models (Ghaffari et al., 2018; Kim et al., 2019; Lemos et al., 2020). STING activation in PDAC can occur within either tumor or macrophages to drive a response. Despite these promising preclinical studies, selectively triggering STING also presents challenges. Overactivation of STING may also drive systemic toxicity through the release of TNFα and other cytokines and may limit the activation that can be achieved, or the duration of treatment. Preclinical tool compounds capable of stimulating the RIG-I RNA-sensing pathway have also shown interesting proof of concept in PDAC models (Ellermeier et al., 2013; Bhoopathi et al., 2014; Das et al., 2019) and may provide an alternate approach in tumors where the cGAS-STING pathway is not functional.

Activating PRRs or reducing suppression by inhibiting negative regulators will also drive IFN-I induction. Although not explored extensively in PDAC, administration of TLR7/8 agonists such as R848 has shown promising results in preclinical models (Michaelis et al., 2019). However, as with STING agonists, these agents can be limited by toxicity, requiring careful scheduling of treatment or the requirement for intratumoral injection to mitigate toxicity (Mullins et al., 2019). TLR9 agonists SD-10-1 and CMP0001 sensitized ICI-resistant mouse models of the colon (Wang et al., 2016) and head and neck squamous cell carcinoma (Sato-Kaneko et al., 2017) to PD-1 blockade. Response was linked to IFN-I stimulation, increase in interferon-stimulated gene expression, and subsequently expansion of CD8+ T cells. Approaches to stimulate these pathways may be worth considering for PDAC to enhance the triggering of immune responses.

Modulators of the DNA methylation state can cause DNA or RNA stress within cells. DNA methyltransferase inhibitors (DNMTi) reduce methylation of endogenous retroelements (Roulois et al., 2015) and increase levels of cytosolic dsRNA (Goel et al., 2017). 5-Azacytidine (a DNMTi) induced re-expression of silenced genes leading to increased T-cell-stimulating chemokines in vitro and increased T-cell infiltration in PDAC in vivo models (Ebelt et al., 2020). Effects of epigenetic modulators can however be context-dependent. The inhibition of PRMT5 with EPZ015666 increased IFN-I and cGAMP production upon stimulation with DNA fragments in vitro (Ma et al., 2021). However, in another study, EPZ015666 decreased IFN-I expression and impaired interferon-stimulated gene expression upon stimulation with poly(I:C) (Cui et al., 2020). Last, consistent with ADAR1 being associated with dampening RNA-sensing pathways, knockout in tumor cells conferred vulnerability to immune checkpoint inhibitors (Ishizuka et al., 2019).

Vaccines or oncolytic viruses can stimulate IFN-I responses, while delivery of recombinant IFN-α or -β to tumors agonizes the pathway directly. Early trials with IFN-I conjugates were not successful, largely due to toxicity issues; however, next-generation approaches that deliver IFN-I conjugates more safely are being developed. Tumor vaccines will stimulate broad innate immune responses. Both cell-based tumor vaccine approaches such as GVAX (Wu et al., 2020b) and GVAX, and a Listeria-based vaccine expressing mesothelin (an antigen upregulated in pancreatic cancer) have been trialed (Le et al., 2019). Unfortunately, these vaccine-based approaches have not yielded positive clinical signals. Oncolytic viruses can stimulate significant IFN-I induction (reviewed in Harrington et al. (2019); Evgin et al. (2020); Cao et al. (2021); Rosewell Shaw et al. (2021)) and drive sustained T-cell activation. Novel strategies combining oncolytic viruses with CAR-T therapy are being developed to drive targeted sustained responses in preclinical pancreatic cancer tumor models.

There are many different strategies to increase tumor immune cross talk through IFN-I responses. However, these approaches are challenging, and therapeutic index is likely to be an issue requiring careful dose selection clinically and the ability to focus on specific patient subsets to induce an effective innate immune response (Konno et al., 2018) (Salvador-Barbero et al., 2020) (Muthalagu et al., 2020). Moreover, IFN-I may act differently when induced acutely or with sustained chronic upregulation. How the IFN-I response is modulated and for how long needs to be considered as complicated regulatory mechanisms can have both activating and suppressive effects, depending on the context.

Conclusion

PDAC has limited sensitivity to chemotherapy and resistance to most current immunotherapy approaches. While chemoimmunotherapy shows better overall responses than chemotherapy or immunotherapy alone, this benefit is marginal for most patients. In PDAC, many mechanisms may prevent the activation of the immune response, from failure to sustain tumor damage- and stress-related immune triggers (e.g., IFN-I release, antigen presentation, or DAMP release) to indirect resistance in the TME. IFN responses can however be stimulated with tumor-targeted treatment (e.g., chemotherapy and DDR inhibitors) or induced in the TME. Improved clinical responses could be achieved by enhancing the cross talk between the tumor and TME through the induction of IFN-I signaling, and there are promising approaches to achieve this in the right setting. A number of clinical translational programs such as Pan Can, ESPAC, and Precision Panc are using multi-omic assessments of human clinical trial samples to look at features that influence response to treatment. Studies such as these can provide new ways to look at where and how IFN response may be suppressed in patients as well as identify tumors that may respond well to specific treatment strategies. This work will contribute to our understanding of the intrinsic tumor cell-initiated immunomodulatory pathways in PDAC. Moreover, focusing on treating subsets of tumors in a biomarker and mechanism linked way will hopefully enable the field to identify and build on efficacy signals with more confidence. Ultimately, this will guide the development of improved combination strategies that potentiate immune response in this challenging disease.

Statements

Author contributions

CC wrote the initial draft. All authors contributed to the conception of the manuscript and revision and editing, and approved the submitted version.

Funding

This review was supported with financial grants by PRECODE (EU grant number: 861196).

Acknowledgments

We are extremely grateful to Ulla-Maja Bailey for critical review and proofreading of the manuscript.

Conflict of interest

CC and SB are current AstraZeneca employees and shareholders.

The remaining author declares that the research was conducted in the absence of any commercial or financial relationships that could be construed as a potential conflict of interest.

Publisher’s note

All claims expressed in this article are solely those of the authors and do not necessarily represent those of their affiliated organizations or those of the publisher, the editors, and the reviewers. Any product that may be evaluated in this article, or claim that may be made by its manufacturer, is not guaranteed or endorsed by the publisher.

References

  • 1

    AbeT.BarberG. N. (2014). Cytosolic-DNA-Mediated, STING-dependent Proinflammatory Gene Induction Necessitates Canonical NF- B Activation through TBK1. J. Virol.88 (10), 53285341. 10.1128/jvi.00037-14

  • 2

    AblasserA.GoldeckM.CavlarT.DeimlingT.WitteG.RöhlI.et al (2013). cGAS Produces a 2′-5′-linked Cyclic Dinucleotide Second Messenger that Activates STING. Nature498, 380384. 10.1038/nature12306

  • 3

    AgerC. R.BodaA.RajapaksheK.LeaS. T.Di FrancescoM. E.JayaprakashP.et al (2021). High Potency STING Agonists Engage Unique Myeloid Pathways to Reverse Pancreatic Cancer Immune Privilege. J. Immunother. Cancer9 (8), e003246. 10.1136/jitc-2021-003246

  • 4

    AgliettaM.BaroneC.SawyerM. B.MooreM. J.MillerW. H.JrBagalàC.et al (2014). A Phase I Dose Escalation Trial of Tremelimumab (CP-675,206) in Combination with Gemcitabine in Chemotherapy-Naive Patients with Metastatic Pancreatic Cancer. Ann. Oncol.25 (9), 17501755. 10.1093/annonc/mdu205

  • 5

    AguirreA. J.NowakJ. A.CamardaN. D.MoffittR. A.GhazaniA. A.Hazar-RethinamM.et al (2018). Real-time Genomic Characterization of Advanced Pancreatic Cancer to Enable Precision Medicine. Cancer Discov.8 (9), 10961111. 10.1158/2159-8290.cd-18-0275

  • 6

    AlexopoulouL.HoltA. C.MedzhitovR.FlavellR. A. (2001). Recognition of Double-Stranded RNA and Activation of NF-Κb by Toll-like Receptor 3. Nature413 (6857), 732738. 10.1038/35099560

  • 7

    AllardB.CousineauI.SpringK.StaggJ. (2019). Measurement of CD73 Enzymatic Activity Using Luminescence-Based and Colorimetric Assays. Methods Enzymol.629, 269289. 10.1016/bs.mie.2019.10.007

  • 8

    BaileyP.ChangD. K.NonesK.JohnsA. L.PatchA. M.GingrasM. C.et al (2016). Genomic Analyses Identify Molecular Subtypes of Pancreatic Cancer. Nature531 (7592), 4752. 10.1038/nature16965

  • 9

    BaileyP.ChangD. K.ForgetM.-A.LucasF. A. S.AlvarezH. A.HaymakerC.et al (2016). Exploiting the Neoantigen Landscape for Immunotherapy of Pancreatic Ductal Adenocarcinoma. Sci. Rep.6, 35848. 10.1038/srep35848

  • 10

    BaillyC.ThuruX.QuesnelB. (2020). Combined Cytotoxic Chemotherapy and Immunotherapy of Cancer: Modern Times. NAR Cancer2 (1), zcaa002. 10.1093/narcan/zcaa002

  • 11

    BalachandranV. P.ŁukszaM.ŁukszaM.ZhaoJ. N.MakarovV.MoralJ. A.et al (2017). Identification of Unique Neoantigen Qualities in Long-Term Survivors of Pancreatic Cancer. Nature551 (7681), 512516. 10.1038/nature24462

  • 12

    BarisA. M.Fraile-BethencourtE.AnandS. (2021). Nucleic Acid Sensing in the Tumor Vasculature. Cancers13 (17), 4452. 10.3390/cancers13174452

  • 13

    BayneL. J.BeattyG. L.JhalaN.ClarkC. E.RhimA. D.StangerB. Z.et al (2012). Tumor-derived Granulocyte-Macrophage colony-stimulating Factor Regulates Myeloid Inflammation and T Cell Immunity in Pancreatic Cancer. Cancer Cell21 (6), 822835. 10.1016/j.ccr.2012.04.025

  • 14

    BergamaschiC.PanditH.NagyB. A.StellasD.JensenS. M.BearJ.et al (2020). Heterodimeric IL-15 Delays Tumor Growth and Promotes Intratumoral CTL and Dendritic Cell Accumulation by a Cytokine Network Involving XCL1, IFN-γ, CXCL9 and CXCL10. J. Immunother. Cancer8 (1), e000599. 10.1136/jitc-2020-000599

  • 15

    BhatP.LeggattG.WaterhouseN.FrazerI. H. (2017). Interferon-γ Derived from Cytotoxic Lymphocytes Directly Enhances Their Motility and Cytotoxicity. Cell Death Dis8 (6), e2836. 10.1038/cddis.2017.67

  • 16

    BhoopathiP.QuinnB. A.GuiQ.ShenX.-N.GrossmanS. R.DasS. K.et al (2014). Pancreatic Cancer-specific Cell Death Induced In Vivo by Cytoplasmic-Delivered Polyinosine-Polycytidylic Acid. Cancer Res.74 (21), 62246235. 10.1158/0008-5472.can-14-0819

  • 17

    BiasciD.SmoragiewiczM.ConnellC. M.WangZ.GaoY.ThaventhiranJ. E. D.et al (2020). CXCR4 Inhibition in Human Pancreatic and Colorectal Cancers Induces an Integrated Immune Response. Proc. Natl. Acad. Sci. USA117 (46), 2896028970. 10.1073/pnas.2013644117

  • 18

    BinnewiesM.MujalA. M.PollackJ. L.CombesA. J.HardisonE. A.BarryK. C.et al (2019). Unleashing Type-2 Dendritic Cells to Drive Protective Antitumor CD4+ T Cell Immunity. Cell177 (3), 556571. 10.1016/j.cell.2019.02.005

  • 19

    BlairA. B.GrootV. P.GemenetzisG.WeiJ.CameronJ. L.WeissM. J.et al (2018). BRCA1/BRCA2 Germline Mutation Carriers and Sporadic Pancreatic Ductal Adenocarcinoma. J. Am. Coll. Surgeons226 (4), 630637. e1. 10.1016/j.jamcollsurg.2017.12.021

  • 20

    BlandoJ.SharmaA.HigaM. G.ZhaoH.VenceL.YadavS. S.et al (2019). Comparison of Immune Infiltrates in Melanoma and Pancreatic Cancer Highlights VISTA as a Potential Target in Pancreatic Cancer. Proc. Natl. Acad. Sci. USA116 (5), 16921697. 10.1073/pnas.1811067116

  • 21

    BlissL. A.WitkowskiE. R.YangC. J.TsengJ. F.TsangJ. F. (2014). Outcomes in Operative Management of Pancreatic Cancer. J. Surg. Oncol.110 (5), 592598. 10.1002/jso.23744

  • 22

    BrahmerJ. R.TykodiS. S.ChowL. Q. M.HwuW.-J.TopalianS. L.HwuP.et al (2012). Safety and Activity of Anti-PD-L1 Antibody in Patients with Advanced Cancer. N. Engl. J. Med.366 (26), 24552465. 10.1056/nejmoa1200694

  • 23

    BrownJ. S.SundarR.LopezJ. (2018). Combining DNA Damaging Therapeutics with Immunotherapy: More Haste, Less Speed. Br. J. Cancer118 (3), 312324. 10.1038/bjc.2017.376

  • 24

    BudhwaniM.MazzieriR.DolcettiR. (2018). Plasticity of Type I Interferon-Mediated Responses in Cancer Therapy: From Anti-tumor Immunity to Resistance. Front. Oncol.8, 322. 10.3389/fonc.2018.00322

  • 25

    BurtnessB.HarringtonK. J.GreilR.SoulieresD.TaharaM.De CasroG.et al (2018). KEYNOTE-048: PhaseIII Study of First-Line Pembrolizumab (P) for Recurrent/metastatic Head and Neck Squamous Cell Carcinoma (R/M HNSCC). Ann. Oncol.29 (abstr), VIII729. 10.1093/annonc/mdy424.045

  • 26

    Cancer Genome Atlas Research Network (2017). Integrated Genomic Characterization of Pancreatic Ductal Adenocarcinoma. Cancer Cell32 (2), 185e13. 10.1016/j.ccell.2017.07.007

  • 27

    CandidoJ. B.MortonJ. P.BaileyP.CampbellA. D.KarimS. A.JamiesonT.et al (2018). CSF1R+ Macrophages Sustain Pancreatic Tumor Growth through T Cell Suppression and Maintenance of Key Gene Programs that Define the Squamous Subtype. Cel Rep.23 (5), 14481460. 10.1016/j.celrep.2018.03.131

  • 28

    CaoX.LiangY.HuZ.LiH.YangJ.HsuE. J.et al (2021). Next Generation of Tumor-Activating Type I IFN Enhances Anti-tumor Immune Responses to Overcome Therapy Resistance. Nat. Commun.12, 5866. 10.1038/s41467-021-26112-2

  • 29

    CarozzaJ. A.BöhnertV.NguyenK. C.SkariahG.ShawK. E.BrownJ. A.et al (2020). Extracellular cGAMP Is a Cancer-Cell-Produced Immunotransmitter Involved in Radiation-Induced Anticancer Immunity. Nat. Cancer1 (2), 184196. 10.1038/s43018-020-0028-4

  • 30

    ChandS.O'HayerK.BlancoF. F.WinterJ. M.BrodyJ. R. (2016). The Landscape of Pancreatic Cancer Therapeutic Resistance Mechanisms. Int. J. Biol. Sci.12 (3), 273282. 10.7150/ijbs.14951

  • 31

    ChengjinY.ZhaoliY.YiweiX.YuW.YinaR.YuepingG.et al (2018). STAU1 Binds to IBDV Genomic Double-Stranded RNA and Promotes Viral Replication via Attenuation of MDA5-dependent β Interferon Induction. Faseb J.33 (1), 286300. 10.1096/fj.201800062RR

  • 32

    ChouA.FroioD.NagrialA. M.ParkinA.MurphyK. J.ChinV. T.et al (2018). Tailored First-Line and Second-Line CDK4-Targeting Treatment Combinations in Mouse Models of Pancreatic Cancer. Gut67 (12), 21422155. 10.1136/gutjnl-2017-315144

  • 33

    CiszewskiW. M.TavecchioM.DastychJ.CurtinN. J. (2014). DNA-PK Inhibition by NU7441 Sensitizes Breast Cancer Cells to Ionizing Radiation and Doxorubicin. Breast Cancer Res. Treat.143 (1), 4755. 10.1007/s10549-013-2785-6

  • 34

    ClarkC. E.HingoraniS. R.MickR.CombsC.TuvesonD. A.VonderheideR. H. (2007). Dynamics of the Immune Reaction to Pancreatic Cancer from Inception to Invasion. Cancer Res.67 (19), 95189527. 10.1158/0008-5472.can-07-0175

  • 35

    CollissonE. A.SadanandamA.OlsonP.GibbW. J.TruittM.GuS.et al (2011). Subtypes of Pancreatic Ductal Adenocarcinoma and Their Differing Responses to Therapy. Nat. Med.17 (4), 500503. 10.1038/nm.2344

  • 36

    ConroyT.DesseigneF.YchouM.BouchéO.GuimbaudR.BécouarnY.et al (2011). FOLFIRINOX versus Gemcitabine for Metastatic Pancreatic Cancer. N. Engl. J. Med.364 (19), 18171825. 10.1056/nejmoa1011923

  • 37

    CorralesL.GlickmanL. H.McWhirterS. M.KanneD. B.SivickK. E.KatibahG. E.et al (2015). Direct Activation of STING in the Tumor Microenvironment Leads to Potent and Systemic Tumor Regression and Immunity. Cel Rep.11 (7), 10181030. 10.1016/j.celrep.2015.04.031

  • 38

    CrastaK.GanemN. J.DagherR.LantermannA. B.IvanovaE. V.PanY.et al (2012). DNA Breaks and Chromosome Pulverization from Errors in Mitosis. Nature482 (7383), 5358. 10.1038/nature10802

  • 39

    CuiS.YuQ.ChuL.CuiY.DingM.WangQ.et al (2020). Nuclear cGAS Functions Non-canonically to Enhance Antiviral Immunity via Recruiting Methyltransferase Prmt5. Cel Rep.33 (10), 108490. 10.1016/j.celrep.2020.108490

  • 40

    DasM.ShenL.LiuQ.GoodwinT. J.HuangL. (2019). Nanoparticle Delivery of RIG-I Agonist Enables Effective and Safe Adjuvant Therapy in Pancreatic Cancer. Mol. Ther.27 (3), 507517. 10.1016/j.ymthe.2018.11.012

  • 41

    DengJ.WangE. S.JenkinsR. W.LiS.DriesR.YatesK.et al (2018). CDK4/6 Inhibition Augments Antitumor Immunity by Enhancing T-Cell Activation. Cancer Discov.8 (2), 216233. 10.1158/2159-8290.cd-17-0915

  • 42

    DiazM. O. (1995). The Human Type I Interferon Gene Cluster. Semin. Virol.6 (3), 143149.

  • 43

    DreyerS. B.Upstill-GoddardR.Paulus-HockV.ParisC.LamprakiE. M.DrayE.et al (2021). Targeting DNA Damage Response and Replication Stress in Pancreatic Cancer. Gastroenterology160 (1), 362e13. 10.1053/j.gastro.2020.09.043

  • 44

    DuewellP.StegerA.LohrH.BourhisH.HoelzH.KirchleitnerS. V.et al (2014). RIG-I-like Helicases Induce Immunogenic Cell Death of Pancreatic Cancer Cells and Sensitize Tumors toward Killing by CD8+ T Cells. Cell Death Differ21 (12), 18251837. 10.1038/cdd.2014.96

  • 45

    DunlopC. R.WallezY.JohnsonT. I.Bernaldo de Quirós FernándezS.DurantS. T.CadoganE. B.et al (2020). Complete Loss of ATM Function Augments Replication Catastrophe Induced by ATR Inhibition and Gemcitabine in Pancreatic Cancer Models. Br. J. Cancer123 (9), 14241436. 10.1038/s41416-020-1016-2

  • 46

    EbeltN. D.ZunigaE.JohnsonB. L.DiamondD. J.ManuelE. R. (2020). 5-Azacytidine Potentiates Anti-tumor Immunity in a Model of Pancreatic Ductal Adenocarcinoma. Front. Immunol.11, 538. 10.3389/fimmu.2020.00538

  • 47

    EllermeierJ.WeiJ.DuewellP.HovesS.StiegM. R.AdunkaT.et al (2013). Therapeutic Efficacy of Bifunctional siRNA Combining TGF-Β1 Silencing with RIG-I Activation in Pancreatic Cancer. Cancer Res.73 (6), 17091720. 10.1158/0008-5472.can-11-3850

  • 48

    ErikssonE.WentheJ.IrenaeusS.LoskogA.UllenhagG. (2016). Gemcitabine Reduces MDSCs, Tregs and TGFβ-1 while Restoring the Teff/treg Ratio in Patients with Pancreatic Cancer. J. Transl Med.14, 282. 10.1186/s12967-016-1037-z

  • 49

    EvginL.HuffA. L.WongthidaP.ThompsonJ.KottkeT.TonneJ.et al (2020). Oncolytic Virus-Derived Type I Interferon Restricts CAR T Cell Therapy. Nat. Commun.11 (1), 3187. 10.1038/s41467-020-17011-z

  • 50

    FeigC.JonesJ. O.KramanM.WellsR. J. B.DeonarineA.ChanD. S.et al (2013). Targeting CXCL12 from FAP-Expressing Carcinoma-Associated Fibroblasts Synergizes with Anti-PD-L1 Immunotherapy in Pancreatic Cancer. Proc. Natl. Acad. Sci.110 (50), 2021220217. 10.1073/pnas.1320318110

  • 51

    FenechM.Kirsch-VoldersM.NatarajanA. T.SurrallesJ.CrottJ. W.ParryJ.et al (2011). Molecular Mechanisms of Micronucleus, Nucleoplasmic Bridge and Nuclear Bud Formation in Mammalian and Human Cells. Mutagenesis26 (1), 125132. 10.1093/mutage/geq052

  • 52

    FentonS. E.SaleiroD.PlataniasL. C. (2021). Type I and II Interferons in the Anti-tumor Immune Response. Cancers13 (5), 1037. 10.3390/cancers13051037

  • 53

    GajewskiT. F.WooS.-R.ZhaY.SpaapenR.ZhengY.CorralesL.et al (2013). Cancer Immunotherapy Strategies Based on Overcoming Barriers within the Tumor Microenvironment. Curr. Opin. Immunol.25 (2), 268276. 10.1016/j.coi.2013.02.009

  • 54

    GalluzziL.HumeauJ.BuquéA.ZitvogelL.KroemerG. (2020). Immunostimulation with Chemotherapy in the Era of Immune Checkpoint Inhibitors. Nat. Rev. Clin. Oncol.17 (12), 725741. 10.1038/s41571-020-0413-z

  • 55

    GangaplaraA.MartensC.DahlstromE.MetidjiA.GokhaleA. S.GlassD. D.et al (2018). Type I Interferon Signaling Attenuates Regulatory T Cell Function in Viral Infection and in the Tumor Microenvironment. Plos Pathog.14 (4), e1006985. 10.1371/journal.ppat.1006985

  • 56

    GelmonK. A.TischkowitzM.MackayH.SwenertonK.RobidouxA.TonkinK.et al (2011). Olaparib in Patients with Recurrent High-Grade Serous or Poorly Differentiated Ovarian Carcinoma or Triple-Negative Breast Cancer: a Phase 2, Multicentre, Open-Label, Non-randomised Study. Lancet Oncol.12 (9), 852861. 10.1016/s1470-2045(11)70214-5

  • 57

    GhaffariA.PetersonN.KhalajK.VitkinN.RobinsonA.FrancisJ.-A.et al (2018). STING Agonist Therapy in Combination with PD-1 Immune Checkpoint Blockade Enhances Response to Carboplatin Chemotherapy in High-Grade Serous Ovarian Cancer. Br. J. Cancer119 (4), 440449. 10.1038/s41416-018-0188-5

  • 58

    GoelS.DeCristoM. J.WattA. C.BrinJonesH.SceneayJ.LiB. B.et al (2017). CDK4/6 Inhibition Triggers Anti-tumour Immunity. Nature548 (7668), 471475. 10.1038/nature23465

  • 59

    GolanT.HammelP.ReniM.Van CutsemE.MacarullaT.HallM. J.et al (2019). Maintenance Olaparib for Germline BRCA-Mutated Metastatic Pancreatic Cancer. N. Engl. J. Med.381, 317327. 10.1056/nejmoa1903387

  • 60

    GolanT.KanjiZ. S.EpelbaumR.DevaudN.DaganE.HolterS.et al (2014). Overall Survival and Clinical Characteristics of Pancreatic Cancer in BRCA Mutation Carriers. Br. J. Cancer111 (6), 11321138. 10.1038/bjc.2014.418

  • 61

    Gómez-BenitoM.BalsasP.Carvajal-VergaraX.PandiellaA.AnelA.MarzoI.et al (2007). Mechanism of Apoptosis Induced by IFN-Alpha in Human Myeloma Cells: Role of Jak1 and Bim and Potentiation by Rapamycin. Cell Signal19 (4), 844854. 10.1016/j.cellsig.2006.10.009

  • 62

    GongT.LiuL.JiangW.ZhouR. (2020). DAMP-sensing Receptors in Sterile Inflammation and Inflammatory Diseases. Nat. Rev. Immunol.20, 95112. 10.1038/s41577-019-0215-7

  • 63

    GonzalezH.HagerlingC.WerbZ. (2018). Roles of the Immune System in Cancer: from Tumor Initiation to Metastatic Progression. Genes Dev.32 (19-20), 12671284. 10.1101/gad.314617.118

  • 64

    GorchsL.Fernández MoroC.BankheadP.KernK. P.SadeakI.MengQ.et al (2019). Human Pancreatic Carcinoma-Associated Fibroblasts Promote Expression of Co-inhibitory Markers on CD4+ and CD8+ T-Cells. Front. Immunol.10, 847. 10.3389/fimmu.2019.00847

  • 65

    GoutJ.PerkhoferL.MoraweM.ArnoldF.IhleM.BiberS.et al (2021). Synergistic Targeting and Resistance to PARP Inhibition in DNA Damage Repair-Deficient Pancreatic Cancer. Gut70 (4), 743760. 10.1136/gutjnl-2019-319970

  • 66

    GrardM.ChatelainC.DelaunayT.Pons-TostivintE.BennounaJ.FonteneauJ.-F. (2021). Homozygous Co-deletion of Type I Interferons and CDKN2A Genes in Thoracic Cancers: Potential Consequences for Therapy. Front. Oncol.11, 695770. 10.3389/fonc.2021.695770

  • 67

    GravettA. M.StevanovićS.DalgleishA. G.CopierJ.CopierJ. (2018). Gemcitabine Alters the Proteasome Composition and Immunopeptidome of Tumour Cells. OncoImmunology7 (6), e1438107. 10.1080/2162402x.2018.1438107

  • 68

    GrivennikovS. I.GretenF. R.KarinM. (2010). Immunity, Inflammation, and Cancer. Cell140 (6), 883899. 10.1016/j.cell.2010.01.025

  • 69

    GutiontovS. I.TurchanW. T.SpurrL. F.RouhaniS. J.ChervinC. S.SteinhardtG.et al (2021). CDKN2A Loss-Of-Function Predicts Immunotherapy Resistance in Non-small Cell Lung Cancer. Sci. Rep.11, 20059. 10.1038/s41598-021-99524-1

  • 70

    HanG.YangG.HaoD.LuY.TheinK.SimpsonB. S.et al (2021). 9p21 Loss Confers a Cold Tumor Immune Microenvironment and Primary Resistance to Immune Checkpoint Therapy. Nat. Commun.12 (1), 5606. 10.1038/s41467-021-25894-9

  • 71

    HarringtonK.FreemanD. J.KellyB.HarperJ.SoriaJ.-C. (2019). Optimizing Oncolytic Virotherapy in Cancer Treatment. Nat. Rev. Drug Discov.18, 689706. 10.1038/s41573-019-0029-0

  • 72

    HayashiK.NikolosF.LeeY. C.JainA.TsoukoE.GaoH.et al (2020). Tipping the Immunostimulatory and Inhibitory DAMP Balance to Harness Immunogenic Cell Death. Nat. Commun.11 (1), 6299. 10.1038/s41467-020-19970-9

  • 73

    HenriksenA.Dyhl-PolkA.ChenI.NielsenD. (2019). Checkpoint Inhibitors in Pancreatic Cancer. Cancer Treat. Rev.78, 1730. 10.1016/j.ctrv.2019.06.005

  • 74

    HerbertA. (2019). ADAR and Immune Silencing in Cancer. Trends Cancer5 (5), 272282. 10.1016/j.trecan.2019.03.004

  • 75

    HiraokaN.Yamazaki–ItohR.InoY.MizuguchiY.YamadaT.HirohashiS.et al (2011). CXCL17 and ICAM2 Are Associated with a Potential Anti-tumor Immune Response in Early Intraepithelial Stages of Human Pancreatic Carcinogenesis. Gastroenterology140, 310321. e314. 10.1053/j.gastro.2010.10.009

  • 76

    HoW. J.JaffeeE. M.ZhengL. (2020). The Tumour Microenvironment in Pancreatic Cancer - Clinical Challenges and Opportunities. Nat. Rev. Clin. Oncol.17 (9), 527540. 10.1038/s41571-020-0363-5

  • 77

    HommaY.TaniguchiK.NakazawaM.MatsuyamaR.MoriR.TakedaK.et al (2014). Changes in the Immune Cell Population and Cell Proliferation in Peripheral Blood after Gemcitabine-Based Chemotherapy for Pancreatic Cancer. Clin. Transl Oncol.16, 330335. 10.1007/s12094-013-1079-0

  • 78

    HornS.LeonardelliS.SuckerA.SchadendorfD.GriewankK. G.PaschenA. (2018). Tumor CDKN2A-Associated JAK2 Loss and Susceptibility to Immunotherapy Resistance. Natl. Cancer Inst.110 (6), 677681. 10.1093/jnci/djx271

  • 79

    HornungV.EllegastJ.KimS.BrzózkaK.JungA.KatoH.et al (2006). 5'-Triphosphate RNA Is the Ligand for RIG-I. Science314 (5801), 994997. 10.1126/science.1132505

  • 80

    HoseinA. N.BrekkenR. A.MaitraA. (2020). Pancreatic Cancer Stroma: an Update on Therapeutic Targeting Strategies. Nat. Rev. Gastroenterol. Hepatol.17, 487505. 10.1038/s41575-020-0300-1

  • 81

    HuG.TuW.YangL.PengG.YangL. (2020). ARID1A Deficiency and Immune Checkpoint Blockade Therapy: From Mechanisms to Clinical Application. Cancer Lett.473, 148155. 10.1016/j.canlet.2020.01.001

  • 82

    HuZ. I.ShiaJ.StadlerZ. K.VargheseA. M.CapanuM.Salo-MullenE.et al (2018). Evaluating Mismatch Repair Deficiency in Pancreatic Adenocarcinoma: Challenges and Recommendations. Clin. Cancer Res.24 (6), 13261336. 10.1158/1078-0432.ccr-17-3099

  • 83

    HuberM.BrehmC. U.GressT. M.BuchholzM.Alashkar AlhamweB.von StrandmannE.et al (2020). The Immune Microenvironment in Pancreatic Cancer. Ijms21 (19), 7307. 10.3390/ijms21197307

  • 84

    HuiP.JamesA.CullinanD. R.MuddJ.TakchiR.DeNardoD.et al (2021). Neoadjuvant FOLFIRINOX Therapy Is Associated with Increased Effector T Cells and Reduced Suppressor Cells in Patients with Pancreatic Cancer. Clin. Cancer Res.1, 1.

  • 85

    IshikawaH.BarberG. N. (2008). STING Is an Endoplasmic Reticulum Adaptor that Facilitates Innate Immune Signalling. Nature455 (7213), 674678. 10.1038/nature07317

  • 86

    IshikawaH.MaZ.BarberG. N. (2009). STING Regulates Intracellular DNA-Mediated, Type I Interferon-dependent Innate Immunity. Nature461 (7265), 788792. 10.1038/nature08476

  • 87

    IshizukaJ. J.MangusoR. T.CheruiyotC. K.BiK.PandaA.Iracheta-VellveA.et al (2019). Loss of ADAR1 in Tumours Overcomes Resistance to Immune Checkpoint Blockade. Nature565, 4348. 10.1038/s41586-018-0768-9

  • 88

    IuresciaS.FiorettiD.RinaldiM. (2018). Nucleic Acid Sensing Machinery: Targeting Innate Immune System for Cancer Therapy. Recent Pat Anticancer Drug Discov.13 (1), 217. 10.2174/1574892812666171030163804

  • 89

    IyerS.ZhangS.YucelS.HornH.SmithS. G.ReinhardtF.et al (2021). Genetically Defined Syngeneic Mouse Models of Ovarian Cancer as Tools for the Discovery of Combination Immunotherapy. Cancer Discov.11 (2), 384407. 10.1158/2159-8290.cd-20-0818

  • 90

    JavedM. A.BeyerG.LeN.VinciA.WongH.PalmerD.et al (2019). Impact of Intensified Chemotherapy in Metastatic Pancreatic Ductal Adenocarcinoma (PDAC) in Clinical Routine in Europe. Pancreatology19 (1), 97104. 10.1016/j.pan.2018.10.003

  • 91

    Jerby-ArnonL.ShahP.CuocoM. S.RodmanC.SuM.-J.MelmsJ. C.et al (2018). A Cancer Cell Program Promotes T Cell Exclusion and Resistance to Checkpoint Blockade. Cell175 (4), 984997. 10.1016/j.cell.2018.09.006

  • 92

    JiangT.ChenX.SuC.RenS.ZhouC. (2020). Pan-cancer Analysis of ARID1A Alterations as Biomarkers for Immunotherapy Outcomes. J. Cancer11 (4), 776780. 10.7150/jca.41296

  • 93

    JingW.McAllisterD.VonderhaarE. P.PalenK.RieseM. J.GershanJ.et al (2019). STING Agonist Inflames the Pancreatic Cancer Immune Microenvironment and Reduces Tumor burden in Mouse Models. J. Immunotherapy Cancer7 (1), 115. 10.1186/s40425-019-0573-5

  • 94

    JonesS.ZhangX.ParsonsD. W.LinJ. C.-H.LearyR. J.AngenendtP.et al (2008). Core Signaling Pathways in Human Pancreatic Cancers Revealed by Global Genomic Analyses. Science321 (5897), 18011806. 10.1126/science.1164368

  • 95

    KamathS. D.KalyanA.KircherS.NimeiriH.FoughtA. J.BensonA.et al (2020). Ipilimumab and Gemcitabine for Advanced Pancreatic Cancer: A Phase Ib Study. Oncologist25 (5), e808e815. 10.1634/theoncologist.2019-0473

  • 96

    KanS.HazamaS.MaedaK.InoueY.HommaS.KoidoS.et al (2012). Suppressive Effects of Cyclophosphamide and Gemcitabine on Regulatory T-Cell Induction In Vitro. Anticancer Res.32 (12), 53635369.

  • 97

    KaramitopoulouE. (2019). Tumour Microenvironment of Pancreatic Cancer: Immune Landscape Is Dictated by Molecular and Histopathological Features. Br. J. Cancer121 (1), 514. 10.1038/s41416-019-0479-5

  • 98

    KatoH.TakeuchiO.SatoS.YoneyamaM.YamamotoM.MatsuiK.et al (2006). Differential Roles of MDA5 and RIG-I Helicases in the Recognition of RNA Viruses. Nature441 (7089), 101105. 10.1038/nature04734

  • 99

    KatoK.OmuraH.IshitaniR.NurekiO. (2017). Cyclic GMP-AMP as an Endogenous Second Messenger in Innate Immune Signaling by Cytosolic DNA. Annu. Rev. Biochem.86, 541566. 10.1146/annurev-biochem-061516-044813

  • 100

    KawaiT.AkiraS. (2018). Toll-like Receptor and RIG-I-like Receptor Signaling. Ann. N. Y. Acad. Sci.1143, 120. 10.1196/annals.1443.020

  • 101

    KawaiT.AkiraS. (2007). Signaling to NF-Κb by Toll-like Receptors. Trends Mol. Med.13 (11), 460469. 10.1016/j.molmed.2007.09.002

  • 102

    KazaanaA.SanoE.YoshimuraS.MakitaK.HaraH.YoshinoA.et al (2019). Promotion of TRAIL/Apo2L‐induced Apoptosis by Low‐dose Interferon‐β in Human Malignant Melanoma Cells. J. Cel Physiol234, 1351013524. 10.1002/jcp.28029

  • 103

    KimC.KimW.HanY.KimJ.ChonH. (2019). Cancer Immunotherapy with STING Agonist and PD-1 Immune Checkpoint Inhibitor Effectively Suppresses Peritoneal Carcinomatosis of colon Cancer. Ann. Oncol.30 (4), iv35. 10.1093/annonc/mdz155.130

  • 104

    KimuraM.HaisaM.UetsukaH.TakaokaM.OhkawaT.KawashimaR.et al (2003). TNF Combined with IFN-α Accelerates NF-Κb-Mediated Apoptosis through Enhancement of Fas Expression in colon Cancer Cells. Cel Death Differ10, 718728. 10.1038/sj.cdd.4401219

  • 105

    KnudsenE. S.KumarasamyV.ChungS.RuizA.VailP.TzetzoS.et al (2021). Targeting Dual Signalling Pathways in Concert with Immune Checkpoints for the Treatment of Pancreatic Cancer. Gut70 (1), 127138. 10.1136/gutjnl-2020-321000

  • 106

    KnudsenE. S.VailP.BalajiU.NgoH.BotrosI. W.MakarovV.et al (2017). Stratification of Pancreatic Ductal Adenocarcinoma: Combinatorial Genetic, Stromal, and Immunologic Markers. Clin. Cancer Res.23 (15), 44294440. 10.1158/1078-0432.ccr-17-0162

  • 107

    KonnoH.YamauchiS.BerglundA.PutneyR. M.MuléJ. J.BarberG. N. (2018). Suppression of STING Signaling through Epigenetic Silencing and Missense Mutation Impedes DNA Damage Mediated Cytokine Production. Oncogene37 (15), 20372051. 10.1038/s41388-017-0120-0

  • 108

    KuraharaH.ShinchiH.MatakiY.MaemuraK.NomaH.KuboF.et al (2011). Significance of M2-Polarized Tumor-Associated Macrophage in Pancreatic Cancer. J. Surg. Res.167 (2), e211e219. 10.1016/j.jss.2009.05.026

  • 109

    LeD. T.DurhamJ. N.SmithK. N.WangH.BartlettB. R.AulakhL. K.et al (2017). Mismatch Repair Deficiency Predicts Response of Solid Tumors to PD-1 Blockade. Science357 (6349), 409413. 10.1126/science.aan6733

  • 110

    LeD. T.PicozziV. J.KoA. H.WainbergZ. A.KindlerH.Wang-GillamA.et al (2019). Results from a Phase IIb, Randomized, Multicenter Study of GVAX Pancreas and CRS-207 Compared with Chemotherapy in Adults with Previously Treated Metastatic Pancreatic Adenocarcinoma (ECLIPSE Study). Clin. Cancer Res.25 (18), 54935502. 10.1158/1078-0432.ccr-18-2992

  • 111

    LeD. T.UramJ. N.WangH.BartlettB. R.KemberlingH.EyringA. D.et al (2015). PD-1 Blockade in Tumors with Mismatch-Repair Deficiency. N. Engl. J. Med.372 (26), 25092520. 10.1056/nejmoa1500596

  • 112

    LemosH.OuR.McCardleC.LinY.CalverJ.MinettJ.et al (2020). Overcoming Resistance to STING Agonist Therapy to Incite Durable Protective Antitumor Immunity. J. Immunother. Cancer8 (2), e001182. 10.1136/jitc-2020-001182

  • 113

    LiJ.DuranM. A.DhanotaN.ChatilaW. K.BettigoleS. E.KwonJ.et al (2021). Metastasis and Immune Evasion from Extracellular cGAMP Hydrolysis. Cancer Discov.11 (5), 12121227. 10.1158/2159-8290.cd-20-0387

  • 114

    LiX.ShuC.YiG.ChatonC. T.SheltonC. L.DiaoJ.et al (2013). Cyclic GMP-AMP Synthase Is Activated by Double-Stranded DNA-Induced Oligomerization. Immunity39 (6), 10191031. 10.1016/j.immuni.2013.10.019

  • 115

    LiangK.AbtE. R.LeT. M.ChoA.DannA. M.CuiJ.et al (2021). TING-driven Interferon Signaling Triggers Metabolic Alterations in Pancreas Cancer Cells Visualized by [18F]FLT PET Imaging. PNAS11 (36), e2105390118.

  • 116

    LiddicoatB. J.PiskolR.ChalkA. M.RamaswamiG.HiguchiM.HartnerJ. C.et al (2015). RNA Editing by ADAR1 Prevents MDA5 Sensing of Endogenous dsRNA as Nonself. Science349 (6252), 11151120. 10.1126/science.aac7049

  • 117

    LimS. M.HongM. H.KimH. R. (2020). Immunotherapy for Non-small Cell Lung Cancer: Current Landscape and Future Perspectives. Immune Netw.20 (1), e10. 10.4110/in.2020.20.e10

  • 118

    LiuC.ChengH.LuoG.LuY.JinK.GuoM.et al (2017). Circulating Regulatory T Cell Subsets Predict Overall Survival of Patients with Unresectable Pancreatic Cancer. Int. J. Oncol.51, 686694. 10.3892/ijo.2017.4032

  • 119

    LiuS.CaiX.WuJ.CongQ.ChenX.LiT.et al (2015). Phosphorylation of Innate Immune Adaptor Proteins MAVS, STING, and TRIF Induces IRF3 Activation. Science347 (6227), aaa2630. 10.1126/science.aaa2630

  • 120

    LiuT.HanC.WangS.FangP.MaZ.XuL.et al (2019). Cancer-associated Fibroblasts: an Emerging Target of Anti-cancer Immunotherapy. J. Hematol. Oncol.12, 86. 10.1186/s13045-019-0770-1

  • 121

    LiuW. M.FowlerD. W.SmithP.DalgleishA. G. (2010). Pre-treatment with Chemotherapy Can Enhance the Antigenicity and Immunogenicity of Tumours by Promoting Adaptive Immune Responses. Br. J. Cancer102 (1), 115123. 10.1038/sj.bjc.6605465

  • 122

    LorenziS.MatteiF.SistiguA.BracciL.SpadaroF.SanchezM.et al (2011). Type I IFNs Control Antigen Retention and Survival of CD8α+ Dendritic Cells after Uptake of Tumor Apoptotic Cells Leading to Cross-Priming. J.I.186, 51425150. 10.4049/jimmunol.1004163

  • 123

    LuchiniC.CapelliP.ScarpaA. (2016). Pancreatic Ductal Adenocarcinoma and its Variants. Surg. Pathol. Clin.9 (4), 547560. 10.1016/j.path.2016.05.003

  • 124

    LugadeA. A.MoranJ. P.GerberS. A.RoseR. C.FrelingerJ. G.LordE. M. (2005). Local Radiation Therapy of B16 Melanoma Tumors Increases the Generation of Tumor Antigen-specific Effector Cells that Traffic to the Tumor. J. Immunol.174, 75167523. 10.4049/jimmunol.174.12.7516

  • 125

    LutzE.YeoC. J.LillemoeK. D.BiedrzyckiB.KobrinB.HermanJ.et al (2011). A Lethally Irradiated Allogeneic Granulocyte-Macrophage colony Stimulating Factor-Secreting Tumor Vaccine for Pancreatic Adenocarcinoma. A Phase II Trial of Safety, Efficacy, and Immune Activation. Ann. Surg.253 (2), 328335. 10.1097/SLA.0b013e3181fd271c

  • 126

    LutzE. R.WuA. A.BigelowE.SharmaR.MoG.SoaresK.et al (2014). Immunotherapy Converts Nonimmunogenic Pancreatic Tumors into Immunogenic Foci of Immune Regulation. Cancer Immunol. Res.2 (7), 616631. 10.1158/2326-6066.cir-14-0027

  • 127

    MaD.YangM.WangQ.SunC.ShiH.JingW.et al (2021). Arginine Methyltransferase PRMT5 Negatively Regulates cGAS-Mediated Antiviral Immune Response. Sci. Adv.7 (13), eabc1834. 10.1126/sciadv.abc1834

  • 128

    MaJ.SunD.WangJ.HanC.QianY.ChenG.et al (2020). Immune Checkpoint Inhibitors Combined with Chemotherapy for the Treatment of Advanced Pancreatic Cancer Patients. Cancer Immunol. Immunother.69 (3), 365372. 10.1007/s00262-019-02452-3

  • 129

    MaciejowskiJ.HatchE. M. (2020). Nuclear Membrane Rupture and its Consequences. Annu. Rev. Cel Dev. Biol.36, 85114. 10.1146/annurev-cellbio-020520-120627

  • 130

    MackenzieK. J.CarrollP.MartinC.-A.MurinaO.FluteauA.SimpsonD. J.et al (2017). cGAS Surveillance of Micronuclei Links Genome Instability to Innate Immunity. Nature548, 461465. 10.1038/nature23449

  • 131

    MandiliG.CurcioC.BulfamanteS.FolliaL.FerreroG.MazzaE.et al (2020). In Pancreatic Cancer, Chemotherapy Increases Antitumor Responses to Tumor-Associated Antigens and Potentiates DNA Vaccination. J. Immunother. Cancer8 (2), e001071. 10.1136/jitc-2020-001071

  • 132

    MarconF.ZuoJ.PearceH.NicolS.Margielewska-DaviesS.FarhatM.et al (2020). NK Cells in Pancreatic Cancer Demonstrate Impaired Cytotoxicity and a Regulatory IL-10 Phenotype. Oncoimmunology9 (1), 1845424. 10.1080/2162402x.2020.1845424

  • 133

    MavrakisK. J.McDonaldE. R.SchlabachM. R.BillyE.HoffmanG. R.deWeckA.et al (2016). Disordered Methionine Metabolism in MTAP/CDKN2A-deleted Cancers Leads to Dependence on PRMT5. Science351 (6278), 12081213. 10.1126/science.aad5944

  • 134

    McGuiganA.KellyP.TurkingtonR. C.JonesC.ColemanH. G.McCainR. S. (2018). Pancreatic Cancer: A Review of Clinical Diagnosis, Epidemiology, Treatment and Outcomes. Wjg24 (43), 48464861. 10.3748/wjg.v24.i43.4846

  • 135

    SasakiS.KitagawaY.SekidoY.MinnaC.KuwanoH. G.YokotaJ.et al (2003). Molecular processes of chromosome 9p21 deletions in human cancers.Oncogene22, 37923798.

  • 136

    MedranoR. F. V.HungerA.MendonçaS. A.BarbutoJ. A. M.StraussB. E. (2017). Immunomodulatory and Antitumor Effects of Type I Interferons and Their Application in Cancer Therapy. Oncotarget8 (41), 7124971284. 10.18632/oncotarget.19531

  • 137

    MehdipourP.MarhonS. A.EttayebiI.ChakravarthyA.HosseiniA.WangY.et al (2020). Epigenetic Therapy Induces Transcription of Inverted SINEs and ADAR1 Dependency. Nature588 (7836), 169173. 10.1038/s41586-020-2844-1

  • 138

    MeiJ.WangR.XiaD.YangX.ZhouW.WangH.et al (2020). BRCA1 Is a Novel Prognostic Indicator and Associates with Immune Cell Infiltration in Hepatocellular Carcinoma. DNA Cel Biol.39 (10), 18381849. 10.1089/dna.2020.5644

  • 139

    MenderI.ZhangA.RenZ.HanC.DengY.SiteniS.et al (2020). Telomere Stress Potentiates STING-dependent Anti-tumor Immunity. Cancer Cell38 (3), 400411. e6. 10.1016/j.ccell.2020.05.020

  • 140

    MetzgerP.KirchleitnerS. V.KlugeM.KoenigL. M.HörthC.RambuscheckC. A.et al (2019). Immunostimulatory RNA Leads to Functional Reprogramming of Myeloid-Derived Suppressor Cells in Pancreatic Cancer. J. Immunotherapy Cancer7 (1), 288. 10.1186/s40425-019-0778-7

  • 141

    MichaelisK. A.NorgardM. A.ZhuX.LevasseurP. R.SivagnanamS.LiudahlS. M.et al (2019). The TLR7/8 Agonist R848 Remodels Tumor and Host Responses to Promote Survival in Pancreatic Cancer. Nat. Commun.10 (1), 4682. 10.1038/s41467-019-12657-w

  • 142

    MillerA. M.Lemke-MiltnerC. D.BlackwellS.Tomanek-ChalkleyA.Gibson-CorelyK. N.ColemanK. L.et al (2021). Intraperitoneal CMP-001: A Novel Immunotherapy for Treating Peritoneal Carcinomatosis of Gastrointestinal and Pancreaticobiliary Cancer. Ann. Surg. Oncol.28 (2), 11871197. 10.1245/s10434-020-08591-7

  • 143

    MirzaM. R.MonkB. J.HerrstedtJ.OzaA. M.MahnerS.RedondoA.et al (2016). Niraparib Maintenance Therapy in Platinum-Sensitive, Recurrent Ovarian Cancer. N. Engl. J. Med.375 (22), 21542164. 10.1056/nejmoa1611310

  • 144

    MoffittR. A.MarayatiR.FlateE. L.VolmarK. E.LoezaS. G. H.HoadleyK. A.et al (2015). Virtual Microdissection Identifies Distinct Tumor- and Stroma-specific Subtypes of Pancreatic Ductal Adenocarcinoma. Nat. Genet.47 (10), 11681178. 10.1038/ng.3398

  • 145

    MohammadA. A. (2018). Advanced Pancreatic Cancer: The Standard of Care and New Opportunities. Oncol. Rev.12 (2), 370. 10.4081/oncol.2018.370

  • 146

    MohrL.ToufektchanE.von MorgenP.ChuK.KapoorA.MaciejowskiJ. (2021). ER-directed TREX1 Limits cGAS Activation at Micronuclei. Mol. Cel81 (4), 724738. e9. 10.1016/j.molcel.2020.12.037

  • 147

    MoskovitzA. H.LinfordN. J.BrentnallT. A.BronnerM. P.StorerB. E.PotterJ. D.et al (2003). Chromosomal Instability in Pancreatic Ductal Cells from Patients with Chronic Pancreatitis and Pancreatic Adenocarcinoma. Genes Chromosome Cancer37 (2), 201206. 10.1002/gcc.10189

  • 148

    MullinsS. R.VasilakosJ. P.DeschlerK.GrigsbyI.GillisP.JohnJ.et al (2019). Intratumoral Immunotherapy with TLR7/8 Agonist MEDI9197 Modulates the Tumor Microenvironment Leading to Enhanced Activity when Combined with Other Immunotherapies. J. Immunotherapy Cancer7, 244. 10.1186/s40425-019-0724-8

  • 149

    MusellaM.ManicG.De MariaR.VitaleI.SistiguA. (2017). Type-I-interferons in Infection and Cancer: Unanticipated Dynamics with Therapeutic Implications. Oncoimmunology6 (5), e1314424. 10.1080/2162402x.2017.1314424

  • 150

    MuthalaguN.MonteverdeT.Raffo-IraolagoitiaX.WiesheuR.WhyteD.HedleyA.et al (2020). Repression of the Type I Interferon Pathway Underlies MYC- and KRAS-dependent Evasion of NK and B Cells in Pancreatic Ductal Adenocarcinoma. Cancer Discov.10 (6), 872887. 10.1158/2159-8290.cd-19-0620

  • 151

    NixonN. A.BlaisN.ErnstS.KollmannsbergerC.BebbG.ButlerM.et al (2018). Current Landscape of Immunotherapy in the Treatment of Solid Tumours, with Future Opportunities and Challenges. Curr. Oncol.25 (5), 373384. 10.3747/co.25.3840

  • 152

    NomiT.ShoM.AkahoriT.HamadaK.KuboA.KanehiroH.et al (2007). Clinical Significance and Therapeutic Potential of the Programmed Death-1 Ligand/programmed Death-1 Pathway in Human Pancreatic Cancer. Clin. Cancer Res.13 (7), 21512157. 10.1158/1078-0432.ccr-06-2746

  • 153

    NyweningT. M.BeltB. A.CullinanD. R.PanniR. Z.HanB. J.SanfordD. E.et al (2018). Targeting Both Tumour-Associated CXCR2+ Neutrophils and CCR2+ Macrophages Disrupts Myeloid Recruitment and Improves Chemotherapeutic Responses in Pancreatic Ductal Adenocarcinoma. Gut67, 11121123. 10.1136/gutjnl-2017-313738

  • 154

    O'ReillyE. M.LeeJ. W.ZalupskiM.CapanuM.ParkJ.GolanT.et al (2020). Randomized, Multicenter, Phase II Trial of Gemcitabine and Cisplatin with or without Veliparib in Patients with Pancreas Adenocarcinoma and a Germline BRCA/PALB2 Mutation. J. Clin. Oncol.38 (13), 13781388. 10.1200/JCO.19.02931

  • 155

    OkamuraR.KatoS.LeeS.JimenezR. E.SicklickJ. K.KurzrockR. (2020). ARID1Aalterations Function as a Biomarker for Longer Progression-free Survival after Anti-PD-1/pd-L1 Immunotherapy. J. Immunother. Cancer8 (1), e000438. 10.1136/jitc-2019-000438

  • 156

    ParselsL. A.EngelkeC. G.ParselsJ.FlanaganS. A.ZhangQ.TanskaD.et al (2021). Combinatorial Efficacy of Olaparib with Radiation and ATR Inhibitor Requires PARP1 Protein in Homologous Recombination-Proficient Pancreatic Cancer. Mol. Cancer Ther.20 (2), 263273. 10.1158/1535-7163.mct-20-0365

  • 157

    PiadelK.DagleishA. G.SmithP. L. (2020). Gemcitabine in the Era of Cancer Immunotherapy. J. Clinc Haematol.1 (4), 1.

  • 158

    PichlmairA.Reis e SousaC. (2007). Innate Recognition of Viruses. Immunity27, 370383. 10.1016/j.immuni.2007.08.012

  • 159

    PikorL.ThuK.VucicE.LamW. (2013). The Detection and Implication of Genome Instability in Cancer. Cancer Metastasis Rev.32 (3), 341352. 10.1007/s10555-013-9429-5

  • 160

    PishvaianM. J.BrodyJ. R. (2017). Therapeutic Implications of Molecular Subtyping for Pancreatic Cancer. Oncology (Williston Park)31 (3), 159168.

  • 161

    PishvaianM. J.BlaisE. M.BrodyJ. R.RahibL.LyonsE.De ArbeloaP.et al (2019). Outcomes in Patients with Pancreatic Adenocarcinoma with Genetic Mutations in DNA Damage Response Pathways: Results from the Know Your Tumor Program. JCO Precision Oncol.1, 110. 10.1200/po.19.00115

  • 162

    PlateJ. M.HarrisJ. (2004). Effects of Gemcitabine Treatment on Immune Cells and Functions in Pancreatic Cancer Patients. Cancer Immunol. Immunother.54 (9), 915925. 10.1007/s00262-004-0638-1

  • 163

    PlateJ. M. D.PlateA. E.ShottS.BogradS.HarrisJ. E. (2005). Effect of Gemcitabine on Immune Cells in Subjects with Adenocarcinoma of the Pancreas. Cancer Immunol. Immunother.54 (9), 915925. 10.1007/s00262-004-0638-1

  • 164

    PrincipeD. R.NarbutisM.KumarS.ParkA.ViswakarmaN.DormanM. J.et al (2020). Long-Term Gemcitabine Treatment Reshapes the Pancreatic Tumor Microenvironment and Sensitizes Murine Carcinoma to Combination Immunotherapy. Cancer Res.80 (15), 31013115. 10.1158/0008-5472.can-19-2959

  • 165

    Pylayeva-GuptaY.LeeK. E.HajduC. H.MillerG.Bar-SagiD. (2012). Oncogenic Kras-Induced GM-CSF Production Promotes the Development of Pancreatic Neoplasia. Cancer Cell21 (6), 836847. 10.1016/j.ccr.2012.04.024

  • 166

    QinY.HuQ.XuJ.JiS.DaiW.LiuW.et al (2019). PRMT5 Enhances Tumorigenicity and Glycolysis in Pancreatic Cancer via the FBW7/cMyc axis. Cell Commun Signal17 (1), 30. 10.1186/s12964-019-0344-4

  • 167

    RanoaD. R. E.ParekhA. D.PitrodaS. P.HuangX.DargaT.WongA. C.et al (2016). Cancer Therapies Activate RIG-I-like Receptor Pathway through Endogenous Non-coding RNAs. Oncotarget7, 2649626515. 10.18632/oncotarget.8420

  • 168

    ReckM. (2018). Standard Chemotherapy: A Synergy with I/O?Geneva, Switzerland: ESMO Immuno-Oncology Congress. (abstr ID 20).

  • 169

    ReikineS.NguyenJ. B.ModisY. (2014). Pattern Recognition and Signaling Mechanisms of RIG-I and MDA5. Front. Immunol.5, 342. 10.3389/fimmu.2014.00342

  • 170

    ReisländerT.GroellyF. J.TarsounasM. (2020). DNA Damage and Cancer Immunotherapy: A STING in the Tale. Mol. Cel80 (1), 2128. 10.1016/j.molcel.2020.07.026

  • 171

    RenD.QinG.ZhaoJ.SunY.ZhangB.LiD.et al (2020). Metformin Activates the STING/IRF3/IFN-β Pathway by Inhibiting AKT Phosphorylation in Pancreatic Cancer. Am. J. Cancer Res.10 (9), 28512864.

  • 172

    RenoufD. J.KnoxJ. J.KavanP.JonkerD.WelchS.CoutureF.et al (2020). LBA65 the Canadian Cancer Trials Group PA.7 Trial: Results of a Randomized Phase II Study of Gemcitabine (GEM) and Nab-Paclitaxel (Nab-P) vs GEM, Nab-P, Durvalumab (D) and Tremelimumab (T) as First Line Therapy in Metastatic Pancreatic Ductal Adenocarcinoma (mPDAC). Ann. Oncol.31, S1195. 10.1016/j.annonc.2020.08.2300

  • 173

    ReubenA.SpencerC. N.PrietoP. A.GopalakrishnanV.ReddyS. M.MillerJ. P.et al (2017). Genomic and Immune Heterogeneity Are Associated with Differential Responses to Therapy in Melanoma. Npj Genomic Med.2, 10. 10.1038/s41525-017-0013-8

  • 174

    RicciutiB.ArbourK. C.LinJ. J.VajdiA.VokesN.HongL.et al (2021). Diminished Efficacy of PD-(L)1 Inhibition in STK11- and KEAP1-Mutant Lung Adenocarcinoma Is Impacted by KRAS Mutation Status. J. Thorac. Oncol.S1556-0864 (21), 0328403286.

  • 175

    Roma-RodriguesC.MendesR.BaptistaP.FernandesA. (2019). Targeting Tumor Microenvironment for Cancer Therapy. Ijms20 (4), 840. 10.3390/ijms20040840

  • 176

    Rosewell ShawA.PorterC. E.YipT.MahW.-C.McKennaM. K.DystheM.et al (2021). Oncolytic Adeno-Immunotherapy Modulates the Immune System Enabling CAR T-Cells to Cure Pancreatic Tumors. Commun. Biol.4, 368. 10.1038/s42003-021-01914-8

  • 177

    RouloisD.Loo YauH.SinghaniaR.WangY.DaneshA.ShenS. Y.et al (2015). DNA-demethylating Agents Target Colorectal Cancer Cells by Inducing Viral Mimicry by Endogenous Transcripts. Cell162, 961973. 10.1016/j.cell.2015.07.056

  • 178

    RoyalR. E.LevyC.TurnerK.MathurA.HughesM.KammulaU. S.et al (2010). Phase 2 Trial of Single Agent Ipilimumab (Anti-CTLA-4) for Locally Advanced or Metastatic Pancreatic Adenocarcinoma. J. Immunother.33 (8), 828833. 10.1097/cji.0b013e3181eec14c

  • 179

    RyanD. P.HongT. S.BardeesyN. (2014). Pancreatic Adenocarcinoma. N. Engl. J. Med.371 (22), 21402141. 10.1056/NEJMc1412266

  • 180

    SahinI. H.LoweryM. A.StadlerZ. K.Salo-MullenE.Iacobuzio-DonahueC. A.KelsenD. P.et al (2016). Genomic Instability in Pancreatic Adenocarcinoma: a New Step towards Precision Medicine and Novel Therapeutic Approaches. Expert Rev. Gastroenterol. Hepatol.10 (8), 893905. 10.1586/17474124.2016.1153424

  • 181

    Salas-BenitoD.Pérez-GraciaJ. L.Ponz-SarviséM.Rodriguez-RuizM. E.Martínez-ForeroI.CastañónE.et al (2021). Paradigms on Immunotherapy Combinations with Chemotherapy. Cancer Discov.11 (6), 13531367. 10.1158/2159-8290.cd-20-1312

  • 182

    Salvador-BarberoB.Álvarez-FernándezM.Zapatero-SolanaE.El BakkaliA.MenéndezM. d. C.López-CasasP. P.et al (2020). CDK4/6 Inhibitors Impair Recovery from Cytotoxic Chemotherapy in Pancreatic Adenocarcinoma. Cancer Cell37 (3), 340353. e6. 10.1016/j.ccell.2020.01.007

  • 183

    SampsonL. L.HeuserJ.BrownE. J. (1991). Cytokine Regulation of Complement Receptor-Mediated Ingestion by Mouse Peritoneal Macrophages. M-CSF and IL-4 Activate Phagocytosis by a Common Mechanism Requiring Autostimulation by IFN-Beta. J. Immunol.146, 10051013.

  • 184

    SamsL.KrugerS.HeinemannV.BarariaD.HaebeS.AligS.et al (2021). Alterations in Regulatory T Cells and Immune Checkpoint Molecules in Pancreatic Cancer Patients Receiving FOLFIRINOX or Gemcitabine Plus Nab-Paclitaxel. Clin. Transl Oncol.23, 23942401. 10.1007/s12094-021-02620-x

  • 185

    SamsteinR. M.KrishnaC.MaX.PeiX.LeeK.-W.MakarovV.et al (2020). Mutations in BRCA1 and BRCA2 Differentially Affect the Tumor Microenvironment and Response to Checkpoint Blockade Immunotherapy. Nat. Cancer1, 11881203. 10.1038/s43018-020-00139-8

  • 186

    SantiagoI.YauC.HeijL.MiddletonM. R.MarkowetzF.GrabschH. I.et al (2019). Immunophenotypes of Pancreatic Ductal Adenocarcinoma: Meta‐analysis of Transcriptional Subtypes. Int. J. Cancer145 (4), 11251137. 10.1002/ijc.32186

  • 187

    Sato-KanekoF.YaoS.AhmadiA.ZhangS. S.HosoyaT.KanedaM. M.et al (2017). Combination Immunotherapy with TLR Agonists and Checkpoint Inhibitors Suppresses Head and Neck Cancer. JCI Insight2 (18), e93397. 10.1172/jci.insight.93397

  • 188

    SchadtL.SparanoC.SchweigerN. A.SilinaK.CecconiV.LucchiariG.et al (2019). Cancer-Cell-Intrinsic cGAS Expression Mediates Tumor Immunogenicity. Cel Rep.29 (5), 12361248. e7. 10.1016/j.celrep.2019.09.065

  • 189

    SchmidP.AdamsS.RugoH. S.SchneeweissA.BarriosC. H.IwataH.et al (2018). Atezolizumab and Nab-Paclitaxel in Advanced Triple-Negative Breast Cancer. N. Engl. J. Med.379 (22), 21082121. 10.1056/nejmoa1809615

  • 190

    SegalN. H.HamidO.HwuW.MassardC.ButlerM.AntoniaS.et al (2014). A Phase I Multi-Arm Dose-Expansion Study of the Anti-programmed Cell Death-Ligand-1 (Pd-L1) Antibody Medi4736: Preliminary Data. Ann. Oncol.25 (Suppl. 4), iv365. 10.1093/annonc/mdu342.11

  • 191

    SeoY. D.JiangX.SullivanK. M.JalikisF. G.SmytheK. S.AbbasiA.et al (2019). Mobilization of CD8+ T Cells via CXCR4 Blockade Facilitates PD-1 Checkpoint Therapy in Human Pancreatic Cancer. Clin. Cancer Res.25 (13), 39343945. 10.1158/1078-0432.ccr-19-0081

  • 192

    SethR. B.SunL.EaC.-K.ChenZ. J. (2005). Identification and Characterization of MAVS, a Mitochondrial Antiviral Signaling Protein that Activates NF-Κb and IRF3. Cell122 (5), 669682. 10.1016/j.cell.2005.08.012

  • 193

    SharmaP.DirixL.De Vos FyAllisonJ. P.DecosterL.ZauchaR.et al (2018). Efficacy and Tolerability of Tremelimumab in Patients with Metastatic Pancreatic Ductal Adenocarcinoma. J. Clin. Oncol.36 (4), 470. 10.1200/jco.2018.36.4_suppl.470

  • 194

    ShenJ.ZhaoW.JuZ.WangL.PengY.LabrieM.et al (2019). PARPi Triggers the STING-dependent Immune Response and Enhances the Therapeutic Efficacy of Immune Checkpoint Blockade Independent of BRCAness. Cancer Res.79 (2), 311319. 10.1158/0008-5472.can-18-1003

  • 195

    SiegelR. L.MillerK. D.FuchsH. E.JemalA. (2021). Cancer Statistics, 2021. CA A. Cancer J. Clin.71 (1), 733. 10.3322/caac.21654

  • 196

    SiemersN. O.HollowayJ. L.ChangH.ChasalowS. D.Ross-MacDonaldP. B.VolivaC. F.et al (2017). Genome-wide Association Analysis Identifies Genetic Correlates of Immune Infiltrates in Solid Tumors. Plos one12 (7), e0179726. 10.1371/journal.pone.0179726

  • 197

    SiolasD.VucicE.KurzE.HajduC.Bar-SagiD. (2021). Gain-of-function p53R172H Mutation Drives Accumulation of Neutrophils in Pancreatic Tumors, Promoting Resistance to Immunotherapy. Cel Rep.36 (8), 109578. 10.1016/j.celrep.2021.109578

  • 198

    SkoulidisF.GoldbergM. E.GreenawaltD. M.HellmannM. D.AwadM. M.GainorJ. F.et al (2018). STK11/LKB1 Mutations and PD-1 Inhibitor Resistance in KRAS-Mutant Lung Adenocarcinoma. Cancer Discov.8 (7), 822835. 10.1158/2159-8290.cd-18-0099

  • 199

    SmithP. L.YogaratnamY.SamadM.KasowS.DalgleishA. G. (2021). Effect of Gemcitabine Based Chemotherapy on the Immunogenicity of Pancreatic Tumour Cells and T-Cells. Clin. Transl Oncol.23 (1), 110121. 10.1007/s12094-020-02429-0

  • 200

    SønderstrupI. M. H.JensenM. B.EjlertsenB.EriksenJ. O.GerdesA. M.KruseT. A.et al (2019). Evaluation of Tumor-Infiltrating Lymphocytes and Association with Prognosis in BRCA-Mutated Breast Cancer. Acta Oncol.58 (3), 363370. 10.1080/0284186X.2018.1539239

  • 201

    StaggJ.DivisekeraU.McLaughlinN.SharkeyJ.PommeyS.DenoyerD.et al (2010). Anti-CD73 Antibody Therapy Inhibits Breast Tumor Growth and Metastasis. Proc. Natl. Acad. Sci.107 (4), 15471552. 10.1073/pnas.0908801107

  • 202

    SteeleC. W.KarimS. A.LeachJ. D. G.BaileyP.Upstill-GoddardR.RishiL.et al (2016). CXCR2 Inhibition Profoundly Suppresses Metastases and Augments Immunotherapy in Pancreatic Ductal Adenocarcinoma. Cancer Cell29 (6), 832845. 10.1016/j.ccell.2016.04.014

  • 203

    StetsonD. B.MedzhitovR. (2006). Recognition of Cytosolic DNA Activates an IRF3-dependent Innate Immune Response. Immunity24 (1), 93103. 10.1016/j.immuni.2005.12.003

  • 204

    StromnesI. M.HulbertA.PierceR. H.GreenbergP. D.HingoraniS. R. (2017). T-cell Localization, Activation, and Clonal Expansion in Human Pancreatic Ductal Adenocarcinoma. Cancer Immunol. Res.5 (11), 978991. 10.1158/2326-6066.cir-16-0322

  • 205

    SunQ.SunL.LiuH.-H.ChenX.SethR. B.FormanJ.et al (2006). The Specific and Essential Role of MAVS in Antiviral Innate Immune Responses. Immunity24 (5), 633642. 10.1016/j.immuni.2006.04.004

  • 206

    SunY.FanJ.WangB.MengZ.RenD.ZhaoJ.et al (2020). The Aberrant Expression of ADAR1 Promotes Resistance to BET Inhibitors in Pancreatic Cancer by Stabilizing C-Myc. Am. J. Cancer Res.10 (1), 148163.

  • 207

    SuzukiE.KapoorV.JassarA. S.KaiserL. R.AlbeldaS. M. (2005). Gemcitabine Selectively Eliminates Splenic Gr-1+/CD11b+ Myeloid Suppressor Cells in Tumor-Bearing Animals and Enhances Antitumor Immune Activity. Clin. Cancer Res.11 (18), 67136721. 10.1158/1078-0432.ccr-05-0883

  • 208

    SwannJ. B.HayakawaY.ZerafaN.SheehanK. C. F.ScottB.SchreiberR. D.et al (2007). Type I IFN Contributes to NK Cell Homeostasis, Activation, and Antitumor Function. J. Immunol.178 (12), 75407549. 10.4049/jimmunol.178.12.7540

  • 209

    TanY. S.SansanaphongprichaK.XieY.DonnellyC. R.LuoX.HeathB. R.et al (2018). Mitigating SOX2-Potentiated Immune Escape of Head and Neck Squamous Cell Carcinoma with a STING-Inducing Nanosatellite Vaccine. Clin. Cancer Res.24 (17), 42424255. 10.1158/1078-0432.ccr-17-2807

  • 210

    TaoS.-S.WuG.-C.ZhangQ.ZhangT.-P.LengR.-X.PanH.-F.et al (2019). TREX1 as a Potential Therapeutic Target for Autoimmune and Inflammatory Diseases. Cpd25 (30), 32393247. 10.2174/1381612825666190902113218

  • 211

    TeijaroJ. R. (2016). Type I Interferons in Viral Control and Immune Regulation. Curr. Opin. Virol.16, 3140. 10.1016/j.coviro.2016.01.001

  • 212

    ThyagarajanA.AlshehriM. S. A.MillerK. L. R.SherwinC. M.TraversJ. B.SahuR. P. (2019). Myeloid-Derived Suppressor Cells and Pancreatic Cancer: Implications in Novel Therapeutic Approaches. Cancers11 (11), 1627. 10.3390/cancers11111627

  • 213

    U'RenL.GuthA.KamstockD.DowS. (2010). Type I Interferons Inhibit the Generation of Tumor-Associated Macrophages. Cancer Immunol. Immunother.59 (4), 587598. 10.1007/s00262-009-0776-6

  • 214

    VijayanD.YoungA.TengM. W. L.SmythM. J. (2017). Targeting Immunosuppressive Adenosine in Cancer. Nat. Rev. Cancer17 (12), 709724. 10.1038/nrc.2017.86

  • 215

    VincentJ.MignotG.ChalminF.LadoireS.BruchardM.ChevriauxA.et al (2010). 5-Fluorouracil Selectively Kills Tumor-Associated Myeloid-Derived Suppressor Cells Resulting in Enhanced T Cell-dependent Antitumor Immunity. Cancer Res.70 (8), 30523061. 10.1158/0008-5472.can-09-3690

  • 216

    VitaleG.van EijckC. H. J.van Koetsveld IngP. M.ErdmannJ. I.SpeelE. J. M.van der Wansem IngK.et al (2007). Type I Interferons in the Treatment of Pancreatic Cancer. Ann. Surg.246 (2), 259268. 10.1097/01.sla.0000261460.07110.f2

  • 217

    VitaleI.ShemaE.LoiS.GalluzziL. (2021). Intratumoral Heterogeneity in Cancer Progression and Response to Immunotherapy. Nat. Med.27 (2), 212224. 10.1038/s41591-021-01233-9

  • 218

    Von HoffD. D.ErvinT.ArenaF. P.ChioreanE. G.InfanteJ.MooreM.et al (2013). Increased Survival in Pancreatic Cancer with Nab-Paclitaxel Plus Gemcitabine. N. Engl. J. Med.369 (18), 16911703. 10.1056/nejmoa1304369

  • 219

    VonderhaarE. P.BarnekowN. S.McAllisterD.McOlashL.EidM. A.RieseM. J.et al (2021). STING Activated Tumor-Intrinsic Type I Interferon Signaling Promotes CXCR3 Dependent Antitumor Immunity in Pancreatic Cancer. Cell Mol. Gastroenterol. Hepatol.12 (1), 4158. 10.1016/j.jcmgh.2021.01.018

  • 220

    WaddellN.PajicM.PajicM.PatchA.-M.ChangD. K.KassahnK. S.et al (2015). Whole Genomes Redefine the Mutational Landscape of Pancreatic Cancer. Nature518 (7540), 495501. 10.1038/nature14169

  • 221

    WainbergZ. A.HochsterH. S.KimE. J.GeorgeB.KaylanA.ChioreanE. G.et al (2020). Open-label, Phase I Study of Nivolumab Combined with Nab-Paclitaxel Plus Gemcitabine in Advanced Pancreatic Cancer. Clin. Cancer Res.26 (18), 48144822. 10.1158/1078-0432.ccr-20-0099

  • 222

    WanS.PestkaS.JubinR. G.LyuY. L.TsaiY.-C.LiuL. F. (2012). Chemotherapeutics and Radiation Stimulate MHC Class I Expression through Elevated Interferon-Beta Signaling in Breast Cancer Cells. PLoS One7 (3), e32542. 10.1371/journal.pone.0032542

  • 223

    WangL.QuJ.ZhouN.HouH.JiangM.ZhangX. (2020). Effect and Biomarker of Immune Checkpoint Blockade Therapy for ARID1A Deficiency Cancers. Biomed. Pharmacother.130, 110626. 10.1016/j.biopha.2020.110626

  • 224

    WangQ.LiX.QiR.BilliarT. (2017). RNA Editing, ADAR1, and the Innate Immune Response. Genes8 (1), 41. 10.3390/genes8010041

  • 225

    WangR.-F.WangH. Y. (2017). Immune Targets and Neoantigens for Cancer Immunotherapy and Precision Medicine. Cell Res27 (1), 1137. 10.1038/cr.2016.155

  • 226

    WangS.CamposJ.GallottaM.GongM.CrainC.NaikE.et al (2016). Intratumoral Injection of a CpG Oligonucleotide Reverts Resistance to PD-1 Blockade by Expanding Multifunctional CD8+ T Cells. Proc. Natl. Acad. Sci. U S A.113, e7240e7249. 10.1073/pnas.1608555113

  • 227

    WartenbergM.CibinS.ZlobecI.VassellaE.Eppenberger-CastoriS.TerraccianoL.et al (2018). Integrated Genomic and Immunophenotypic Classification of Pancreatic Cancer Reveals Three Distinct Subtypes with Prognostic/Predictive Significance. Clin. Cancer Res.24 (18), 44444454. 10.1158/1078-0432.ccr-17-3401

  • 228

    WeissG. J.BlaydornL.BeckJ.Bornemann-KolatzkiK.UrnovitzH.SchützE.et al (2018). Phase Ib/II Study of Gemcitabine, Nab-Paclitaxel, and Pembrolizumab in Metastatic Pancreatic Adenocarcinoma. Invest. New Drugs36 (1), 96102. 10.1007/s10637-017-0525-1

  • 229

    WellensteinM. D.de VisserK. E. (2018). Cancer-Cell-Intrinsic Mechanisms Shaping the Tumor Immune Landscape. Immunity48 (3), 399416. 10.1016/j.immuni.2018.03.004

  • 230

    WenW. X.LeongC.-O. (2019). Association of BRCA1- and BRCA2-Deficiency with Mutation burden, Expression of PD-L1/pd-1, Immune Infiltrates, and T Cell-Inflamed Signature in Breast Cancer. PLos One14 (4), e0215381. 10.1371/journal.pone.0215381

  • 231

    WuA. A.BeverK. M.HoW. J.FertigE. J.NiuN.ZhengL.et al (2020). A Phase II Study of Allogeneic GM-CSF-Transfected Pancreatic Tumor Vaccine (GVAX) with Ipilimumab as Maintenance Treatment for Metastatic Pancreatic Cancer. Clin. Cancer Res.26 (19), 51295139. 10.1158/1078-0432.ccr-20-1025

  • 232

    WuC.TanX.HuX.ZhouM.YanJ.DingC. (2020). Tumor Microenvironment Following Gemcitabine Treatment Favors Differentiation of Immunosuppressive Ly6Chigh Myeloid Cells. J.I.204 (1), 212223. 10.4049/jimmunol.1900930

  • 233

    WuS.ZhangQ.ZhangF.MengF.LiuS.ZhouR.et al (2019). HER2 Recruits AKT1 to Disrupt STING Signalling and Suppress Antiviral Defence and Antitumour Immunity. Nat. Cel Biol21 (8), 10271040. 10.1038/s41556-019-0352-z

  • 234

    YamamotoK.VenidaA.YanoJ.BiancurD. E.KakiuchiM.GuptaS.et al (2020). Autophagy Promotes Immune Evasion of Pancreatic Cancer by Degrading MHC-I. Nature581 (7806), 100105. 10.1038/s41586-020-2229-5

  • 235

    YangI.KremenT. J.GiovannoneA. J.PaikE.OdesaS. K.PrinsR. M.et al (2004). Modulation of Major Histocompatibility Complex Class I Molecules and Major Histocompatibility Complex-Bound Immunogenic Peptides Induced by Interferon-α and Interferon-γ Treatment of Human Glioblastoma Multiforme. J. Neurosurg.100 (2), 310319. 10.3171/jns.2004.100.2.0310

  • 236

    YumS.LiM.FangY.ChenZ. J. (2021). TBK1 Recruitment to STING Activates Both IRF3 and NF-Κb that Mediate Immune Defense against Tumors and Viral Infections. Proc. Natl. Acad. Sci. USA118 (14), e2100225118. 10.1073/pnas.2100225118

  • 237

    ZhangC.-x.HuangD.-j.BalocheV.ZhangL.XuJ.-x.LiB.-w.et al (2020). Galectin-9 Promotes a Suppressive Microenvironment in Human Cancer by Enhancing STING Degradation. Oncogenesis9 (7), 65. 10.1038/s41389-020-00248-0

  • 238

    ZhangQ.GreenM. D.LangX.LazarusJ.ParselsJ. D.WeiS.et al (2019). Inhibition of ATM Increases Interferon Signaling and Sensitizes Pancreatic Cancer to Immune Checkpoint Blockade Therapy. Cancer Res.79 (15), 39403951. 10.1158/0008-5472.can-19-0761

  • 239

    ZhongS.JeongJ.-H.ChenZ.ChenZ.LuoJ.-L. (2020). Targeting Tumor Microenvironment by Small-Molecule Inhibitors. Translational Oncol.13 (1), 5769. 10.1016/j.tranon.2019.10.001

  • 240

    ZhouZ.LiM. (2021). Evaluation of BRCA1 and BRCA2 as Indicators of Response to Immune Checkpoint Inhibitors. JAMA Netw. Open4 (5), e217728. 10.1001/jamanetworkopen.2021.7728

  • 241

    ZitvogelL.GalluzziL.KeppO.SmythM. J.KroemerG. (2015). Type I Interferons in Anticancer Immunity. Nat. Rev. Immunol.15 (7), 405414. 10.1038/nri3845

  • 242

    ZouS.-S.QiaoY.ZhuS.GaoB.YangN.LiuY.-J.et al (2021). Intrinsic Strategies for the Evasion of cGAS-STING Signaling-Mediated Immune Surveillance in Human Cancer: How Therapy Can Overcome Them. Pharmacol. Res.166, 105514. 10.1016/j.phrs.2021.105514

Summary

Keywords

innate immunity, PDAC, IFN-I, nucleic acid sensing, immunotherapy, tumor microenvironment

Citation

Cattolico C, Bailey P and Barry ST (2022) Modulation of Type I Interferon Responses to Influence Tumor-Immune Cross Talk in PDAC. Front. Cell Dev. Biol. 10:816517. doi: 10.3389/fcell.2022.816517

Received

16 November 2021

Accepted

31 January 2022

Published

22 February 2022

Volume

10 - 2022

Edited by

Xiaoqiang Tang, Sichuan University, China

Reviewed by

Daniel R. Principe, University of Illinois at Chicago, United States

Stéphanie Lebreton, Institut Pasteur, France

Updates

Copyright

*Correspondence: Simon T. Barry,

This article was submitted to Molecular and Cellular Pathology, a section of the journal Frontiers in Cell and Developmental Biology

Disclaimer

All claims expressed in this article are solely those of the authors and do not necessarily represent those of their affiliated organizations, or those of the publisher, the editors and the reviewers. Any product that may be evaluated in this article or claim that may be made by its manufacturer is not guaranteed or endorsed by the publisher.

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