CORRECTION article

Front. Immunol., 23 August 2024

Sec. Molecular Innate Immunity

Volume 15 - 2024 | https://doi.org/10.3389/fimmu.2024.1476204

Corrigendum: Genetic investigation of Nordic patients with complement-mediated kidney diseases

  • Department of Pediatrics, Clinical Sciences Lund, Lund University, Lund, Sweden

In the published article, there was an error in Table 3 as published. Under the heading C3, rowc.4030-4C>G was under the ACMG classification stated as “P” when it should be “LB”. Under the heading CFHR2, row R141S, “c.423G>A” should have been written as “c.423G>T”. And finally, under the heading CLU, row K444Q, “c.1339A>C” should be corrected to “c.1330A>C”. The corrected Table 3 and its caption appear below.

Table 3

Variant or deletionNucleotide shiftType of variantdbSNPDomainMinor Allele frequencyFunctional studiesACMG classificationReference
CFH
D693N ac.2077G>AMissensers148403790SCR120.0001592Conflicting(48)
Q950Hc.2850G>TMissensers149474608SCR160.003911NPELP(45, 51)
N1050Ybc.3148A>TMissensers35274867SCR180.01469NPELB(45, 54)
S1209Tc.3625T>AMissensers561146868SCR200.00000398LB(48)
C3
K155Qc.463A>CMissensers147859257MG20.002705GoFLP(58, 59)
V326Mcc.976G>AMissensers375264020MG30.00004779VUSThis study
Q1061Hc.3183A>TMissensers373054812TED0.00007704VUSThis study
E1516Ac.4547A>CMissensers1019532370C345C0.00001193VUSThis study
W1631*c.4893G>AStopNAC345CLoFP(61)
c.4030-4C>GSplice acceptor siteNABetween CUB and MG8LB(55)
CFI
c.1534+5G>TIntronic splicers114013791Intron 120.00866(33)
G328Rc.981G>AMissensers144164794Linker 2LoFLP(55, 65)
CD46
A353Va,bc.1013C>TMissensers35366573TM0.01541LoF, NFEConflicting(33, 73)
C5
P233Lc.698C>TMissensers531284110MG30.0000252VUS(81)
L354Mc.1060C>AMissensers34552775MG40.0055B(82)
G385Rc.1153G>CMissenseMG4UnknownThis study
CFHR1
DeletionDeletionLB(76)
Exon 6 duplicationDuplicationLBThis study. Other duplications reported in (83)
CFHR2
R141Sc.423G>TMissensers142929868SCR20.002947This study
CFHR3
DeletionDeletion(76)
CFHR4
Y43Fdc.128A>TMissensers202234955SCR10.001747LBThis study
c.799+3A>CIntronic spliceRs1968766310.001286LB(82)
CFHR5
E163Kfs*10c.485_486dupFrameshift (insertion)rs565457964SCR30.006750NPE(77)
E226Dfs*7c.678delDeletionrs1438537910SCR40.000007964PThis study
Y279Nc.835T>AMissensers143240067SCR50.0001274Conflicting(78)
R356Hbc.1067G>AMissensers35662416SCR60.01633NPELB(77, 84)
CFP
D299Nc.895G>AMissensers61737993TSP t1 50.001472B(85)
CLU
K444Qc.1330A>CMissensers2612311022β-chain0.0001026--This study
PLG
R89Kc.266G>AMissensers143079629PAN0.006191B(48)
R261Hc.782G>AMissensers4252187Kringle 20.002501Conflicting(80)

Variants in C3G patients included in this study.

a, Mentioned in the complement database (www.complement-db.org) with reference to (4). b, Minor allele frequency > 1% but this variant was previously associated with aHUS. c, Previously reported in the ClinVar database in association with age-related macular degeneration and aHUS. d, Previously reported in the ClinVar database in association with aHUS. CFH, Complement factor H; C3, Complement C3; CFB, Complement factor B; CFI, Complement factor I; CD46, CD46/Membrane cofactor protein; C5, Complement C5; CFHR1-5, Complement factor H related 1-5; CFP, Complement factor properdin; PLG, Plasminogen. Domains, SCR, Short consensus repeats; MG1-8, Macroglobulin domain 1-8; TED, Thiol ester-containing domain; C345C, C345C/NTR domain; CUB: C1r/C1s, Urchin embryonic growth factor, Bone morphogenetic protein 1; TM, Transmembrane protein; TSP t1, Thrombospondin type-1 1-5; PAN, Plasminogen-Apple-Nematode; NPE, No phenotypic effect; GoF, Gain of function; LOF, Loss of function (including low plasma concentration); VUS, Variant of unknown significance; LP, Likely pathogenic; LB, Likely benign; P, Pathogenic.

In the published article, there was an error in Supplementary Table 1. The C3 level of patient 314 was given as “normal” when it should have been written as “low”. The corrected Supplementary Material File has now been published.

The authors apologize for these errors and state that they do not change the scientific conclusions of the article in any way. The original article has been updated.

Statements

Publisher’s note

All claims expressed in this article are solely those of the authors and do not necessarily represent those of their affiliated organizations, or those of the publisher, the editors and the reviewers. Any product that may be evaluated in this article, or claim that may be made by its manufacturer, is not guaranteed or endorsed by the publisher.

Summary

Keywords

complement, atypical hemolytic uremic syndrome, C3 glomerulopathy, membranoproliferative glomerulonephritis, genes

Citation

Rydberg V, Aradottir SS, Kristoffersson A-C, Svitacheva N and Karpman D (2024) Corrigendum: Genetic investigation of Nordic patients with complement-mediated kidney diseases. Front. Immunol. 15:1476204. doi: 10.3389/fimmu.2024.1476204

Received

05 August 2024

Accepted

08 August 2024

Published

23 August 2024

Volume

15 - 2024

Edited and reviewed by

Francesca Granucci, University of Milano-Bicocca, Italy

Updates

Copyright

*Correspondence: Diana Karpman,

Disclaimer

All claims expressed in this article are solely those of the authors and do not necessarily represent those of their affiliated organizations, or those of the publisher, the editors and the reviewers. Any product that may be evaluated in this article or claim that may be made by its manufacturer is not guaranteed or endorsed by the publisher.

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