REVIEW article

Front. Oncol., 13 November 2014

Sec. Neuro-Oncology and Neurosurgical Oncology

Volume 4 - 2014 | https://doi.org/10.3389/fonc.2014.00328

Immune Responses to Non-Tumor Antigens in the Central Nervous System

  • Department of Neurology, University of Michigan Medical School, Ann Arbor, MI, USA

Abstract

The central nervous system (CNS), once viewed as an immune-privileged site protected by the blood–brain barrier (BBB), is now known to be a dynamic immunological environment through which immune cells migrate to prevent and respond to events such as localized infection. During these responses, endogenous glial cells, including astrocytes and microglia, become highly reactive and may secrete inflammatory mediators that regulate BBB permeability and recruit additional circulating immune cells. Here, we discuss the various roles played by astrocytes, microglia, and infiltrating immune cells during host immunity to non-tumor antigens in the CNS, focusing first on bacterial and viral infections, and then turning to responses directed against self-antigens in the setting of CNS autoimmunity.

Introduction

The central nervous system (CNS) was previously viewed as an immune-privileged area, fully isolated from the immune system by the blood–brain barrier (BBB). In early studies, Ehrlich reported that while various organs were strongly stained following intravenous, intra-arterial, or subcutaneous injection of intravital dyes, the brain was only weakly stained or not at all (). Other studies found that tissue grafts were not rejected when implanted into the brains of test animals (), leading to the idea that the CNS was fully “immune-privileged.” This viewpoint had to be altered, however, after it was discovered that a graft within the CNS could be rejected if a second graft was placed subcutaneously into the same animal (). This finding clearly demonstrated that foreign antigens are recognized in the CNS if peripheral priming occurs (). It is now accepted that the BBB is a dynamic, interactive, and regulatory tissue interface that allows bi-directional communication between the CNS and the immune system (, ).

The BBB, formed by complex interactions between capillary endothelial cells (ECs), astrocyte end-feet, pericytes, and microglia (, ), is the largest and most stringent barrier that impedes the paracellular movement of ions, solutes, proteins, water, and leukocytes into the CNS (). However, the BBB can also be influenced by peripheral immune events, creating what has now come to be known as the neuro-immune axis (, , ). The neuro-immune axis is not only responsible for establishing the blood–CNS barrier at baseline, but it also regulates communication between the CNS and the immune system during pathological conditions such as viral or bacterial infections, ischemia, or inflammatory autoimmune disorders such as multiple sclerosis (MS) (). It achieves this state by responding to secreted factors from both immune and CNS cells, as well as by regulating the exchange of chemokines, cytokines, and immune cells between the blood and the CNS (, , ). Therefore, the original concept of the BBB being a purely anatomical barrier has now shifted to one where the BBB is considered a highly reactive interface controlled by signals from ECs, glial cells, pericytes, and neurons in the CNS, as well as from immune responses in the periphery ().

Structural characteristics of the BBB

The BBB is composed of capillary ECs ensheathed by astrocyte end-feet, pericytes, and microglia (, ). Astrocyte end-feet completely surround the abluminal surface of brain capillaries forming a layer known as the glial limitans, but direct contact with EC is inhibited by a dense basement membrane (). While astrocytes are necessary to maintain BBB integrity by secreting factors that alter barrier permeability (, ), they are not actually required to form the BBB, which develops even before these astrocytic processes are present (). Astrocytes control blood flow to the CNS by regulating vascular tone through fluctuating calcium currents (). Pericytes are essential to barrier formation, as the BBB is compromised in pericyte-deficient mice (, ). These cells regulate gene expression in EC and induce the polarization of astrocyte end-feet (). Microglia play a role at the BBB by regulating substrate transport across EC and by linking the brain to systemic immune activity ().

Blood–brain barrier EC forms a highly sophisticated barrier via a network of tight junctions (TJ) and adherens junctions (AJ) (, , ). The EC of the CNS are unique in that the TJ restrict the paracellular passage of solutes, have no pinocytic activity, and have few if any fenestrations (). This causes the BBB to have high endothelial electrical resistance (, ), some 50–100 times higher than peripheral microvessels (). The TJ are composed of a parallel network of intramembranous protein strands, composed of claudins, occludin, and zonula occludin (ZO) proteins (). Claudins, specifically claudin-3, -4, and -12, compose the TJ backbone (). Occludin is not required for TJ formation (); instead, it plays a role in “sealing” the junction thereby increasing electrical resistance (, ). CNS microvessel TJ are also abundant in ZO-2, and to a lesser extent, ZO-1, that are cytoplasmic accessory proteins that serve to anchor the transmembrane proteins of the TJ to the actin cytoskeleton of the ECs (, ).

The choroid plexus (CP) is a villous structure located on the roof of the four cerebral ventricles where cerebrospinal fluid (CSF) is actively secreted. The CP is highly vascular and contains the blood–CSF barrier (BCSFB) (). Unlike the BBB, however, the BCSFB arises from cuboidal choroid plexus epithelial cells (CPE) with a very different TJ structure. The CPE express ZO-1 and ZO-2 in different amounts (), and have a different claudin signature, expressing claudin-1, -2, -3, and -11 (, , ). Furthermore, capillaries within the CP villi are fenestrated (, , ), reflected by a much lower endothelial electrical resistance than the BBB (). For these reasons, the BBB is considered more of an absolute barrier, while the BCSFB may be where most normal immune surveillance of the CNS occurs ().

Immune surveillance and infiltration of the CNS

It is now accepted there is a constant need for immune surveillance of the normal CNS as part of host defense (, , ), with mechanisms present that simultaneously keep excessive inflammation in check (). To assist in maintaining this control, the healthy CNS is relatively devoid of antigen-presenting cells (APC), lacks constitutive human leukocyte antigen (HLA) class I and II protein expression on parenchymal cells, and does not maintain typical lymphatic vessels (). CD4+ T cells, having first encountered antigens in deep cervical lymph nodes (), carry out routine surveillance of the CNS by searching for their cognate antigens presented by macrophages in the CSF (, ). Resting lymphocytes fail to enter the CNS (), while activated T cells of all specificities can traverse the BBB and/or BCSFB (). Those cells that do not encounter their cognate antigen within a few hours then circulate out of the CNS (, ).

The first steps of pathogenic neuroinflammation involve changes at the BBB, including increased production of chemokines and up-regulation of adhesion molecules by the EC resulting in leukocytes traversing the BBB and accumulating in the perivascular space of post-capillary venules (, ). Even during these early events, however, cellular recruitment remains tightly controlled as parenchymal lymphocytes express a unique adhesion molecule profile, different from peripheral T cells (). Once in the perivascular space, T cells encounter the glial limitans as well as astrocytes that express and release factors that induce apoptosis (), inhibit proliferation (), induce differentiation into a regulatory (Treg) phenotype (). Microglia and neurons also assist in controlling neuroinflammation. Microglia do so by expressing a homolog of the co-stimulatory molecule B7, programed death protein (PD)-1, which negatively regulates T cell activation and cytokine production (). Neurons secrete transforming growth factor (TGF)-β, exert cell contact-dependent effects that support the conversion of CD4 T cells to Tregs, and can be induced to express the PD-1 ligand, PD-L1 (). Thus, while the BBB is not the impenetrable barrier it was once thought to be, CD4+ T cell surveillance of the CNS is still a tightly controlled process.

Host Immune Responses to Bacterial Infections of the CNS

Bacterial infections of the CNS are rare, but often life threatening, events (). Excluding direct inoculation following CNS trauma, bacteria typically gain CNS entry following hematogenous dissemination from distant sites (lungs and heart valves) or by direct extension from parameningeal foci of infection (inner ear and sinuses). Penetration of the BBB may occur via three potential mechanisms: (1) direct destruction of capillary ECs (, ), (2) disruption of intercellular TJ and migration in between ECs (), and (3) transcytosis via intracellular vesicles directly through ECs (). Once inside, numerous innate immune receptors and pathways are activated (Figure 1).

Figure 1

Microglia

Analogous to peripheral tissues, resident CNS immune cells known as microglia bear a wide range of innate immune receptors. Common bacterial motifs, referred to as pathogen associated molecular patterns (PAMP), are recognized by cognate pattern recognition receptors (PRR), including Toll-like receptors (TLR), on the surface and in the cytoplasm of microglia, and to a lesser extent, on astrocytes (). Microglial activation, triggered either by intact bacteria or bacterial cell wall antigens (, ), results in rapid changes in cellular morphology in vivo (). Similar to tissue resident macrophages found in the periphery, microglia can phagocytize bacteria and present bacterial antigens via HLA to infiltrating CD4 T cells in vivo (, , ). These cells also rapidly produce pro-inflammatory cytokines and chemokines that recruit peripheral leukocytes to the area of infection and activate astrocytes. For example, during both experimental Streptococcus pneumoniae and Staphylococcus aureus infections of the CNS, microglia produce tumor necrosis factor (TNF)-α, interleukin (IL)-6, IL-12, C-X-C motif ligand (CXCL)1, CXCL2, C-C motif ligand (CCL)2, CCL3, and CCL5 ex vivo, mediators that recruit neutrophils (CXCL1 and CXCL2), monocytes (CCL2 and CCL3), and T cells (CCL5) (, , ). These activated microglia also secrete matrix metalloproteinases (MMP) that enhance BBB breakdown and facilitate additional leukocyte extravasation into the CNS (). Finally, microglia can have direct bactericidal activity, being capable of producing reactive oxygen species (ROS), reactive nitrogen intermediates, and other proteases that kill bacteria in vivo ().

Astrocytes

Microglia partner with astrocytes to eliminate infection as quickly as possible in order to minimize neuronal damage (, , ). In the normal CNS, astrocytes contribute to gap junction stability of the BBB (). Their release of pro-inflammatory mediators such as IL-1β (, 101), nitric oxide (102), TGF-β (103), and MMPs () in vitro suggest these cells may compromise BBB integrity in the setting of bacterial infection. Astrocytes are activated by bacterial PAMP or mediators produced by microglia; this changes their morphology and further triggers their release of innate inflammatory mediators both in vitro and in vivo. These mediators can include complement proteins, IL-1β, IL-6, and the chemokines, CCL2, CCL3, CXCL1, and CXCL10 (104111), which further help recruit neutrophils, monocytes, and T cells. In response to interferon (IFN)-γ, TNF-α, and/or IL-1β, astrocytes also up-regulate the cell surface adhesion molecules, intercellular adhesion molecule (ICAM)-1, and vascular cell adhesion molecule (VCAM)-1 in vitro (112116), which would enhance the infiltration of monocytes and T cells into the CNS in vivo.

Neutrophils

As in the periphery (117, 118), neutrophils are one of the primary lines of host defense during CNS bacterial infections (112, 119, 120). Studies in knockout mice show that the main chemokines driving neutrophil recruitment to the CNS are the C-X-C motif receptor (CXCR)-2 ligands, CXCL1 and CXCL2 (121). Furthermore, CSF samples from patients with bacterial meningitis show elevated levels of neutrophil attracting chemokines compared to controls (122, 123). Neutrophils, like microglia, respond to PAMP through various TLR, and are activated by cytokines such as TNF-α and IFN-γ in vitro (124). Neutrophils activated in the periphery up-regulate adhesion molecules that enhance their migration into tissues (125), while BBB EC express E-selectin and P-selectin during CNS bacterial infection (126), suggesting a mechanism that allows for the migration of neutrophils during these infections. Once neutrophils recognize a bacterial pathogen, they can directly phagocytize these organisms (127), as well as release MMP, defensins, lytic enzymes, and anti-microbial peptides that aid in clearing the infection (128). The inflammatory cytokine, TNF-α, induces neutrophils to produce IL-6, IL-8, CXCL9, and CXCL10 in vivo (129, 130), thereby shifting the chemotactic profile toward the recruitment of T cells and driving the adaptive immune response.

T cells

Adaptive immune responses are important in fighting CNS bacterial infections (131). During bacterial meningitis, T cell production of IFN-γ leads to the generation of chemokines that preferentially recruit monocytes and more T cells (132), supporting the transition from an innate to an adaptive immune response. Furthermore, IFN-γ, potentially made locally by T cells, increases the antigen-presenting capacity of microglial cells in vitro via up-regulation of HLA class I and II molecules, the co-stimulatory molecules, B7-1 and B7-2, and CD40 (133, 134). Bacterial antigen presentation by microglia activates T cells (135), driving further T cell proliferation and greater production of IFN-γ.

Host Immune Responses to Viral Infections of the CNS

Viruses use a variety of mechanisms to gain entry into the CNS. In the case of alphaherpesviruses (i.e., herpes simplex virus and varicella-zoster virus) and rabies virus, infection of peripheral nerves allows viral particles to travel by anterograde axonal transport into the CNS. Human immunodeficiency virus and human T cell leukemia virus-I enter the CNS parenchyma by infecting host immune cells in the periphery, and using them as “Trojan horses” to carry viral particles across the BBB. Finally, Epstein–Barr virus and West Nile virus directly infect the ECs of the BBB, resulting in barrier disruption and enhanced migration of immune cells into the parenchyma (136).

Because viruses can infect microglia, astrocytes, oligodendrocytes, as well as terminally differentiated and non-renewable cells such as neurons, the ensuing immune response within the CNS must avoid extensive cytolytic damage of virus-infected target cells (137). In general, innate anti-viral immunity such as the generation of type-I IFN occurs very rapidly, while the adaptive immune response is slower because it must first develop in the periphery (138). Important components of adaptive anti-viral immunity involve IFN-γ production by T cells as well as the expansion and migration of virus-specific antibody secreting cells (ASC) (138, 139) (Figure 2).

Figure 2

Microglia, astrocytes, and oligodendrocytes

During CNS viral infections, virus-specific PAMP activate individual TLR present on microglia, astrocytes, and oligodendrocytes. The former two cell populations, in particular, respond by producing anti-viral and pro-inflammatory mediators. During experimental mouse hepatitis virus (MHV) infection, astrocytes and microglia produce both type-I IFN (IFN-α and IFN-β), as well as IL-6, TNF-α, IL-12, IL-1α, and IL-1β in vivo (140142). Furthermore, MHV infection triggers MMP-3 and MMP-12 release from astrocytes and oligodendrocytes (142), which along with IL-6 and the up-regulation of adhesion molecules on cerebrovascular endothelium, enhance cellular migration across the BBB (143). Astrocytes produce CXCL10, CXCL11, and CCL5 in vivo that recruit virus-specific CD4+ and CD8+ T cells (144146), as well as ASC (147, 148), to the CNS to promote viral clearance. CXCL9 production from microglia is dependent on IFN-γ, while CXCL10 and CXCL11 are up-regulated by type-I IFN and TNF-α (149152).

Myeloid lineage cells

Neutrophils and macrophages are recruited to the CNS following viral infection (153, 154). Thus far, macrophages appear to have more limited anti-viral activity in the CNS (155), but neutrophils contribute to the breakdown of the BBB by interacting with EC via adhesion molecules to promote the disassembly of tight junction complexes (156). Neutrophils also secrete MMP-9 that degrades the extracellular matrix and basal lamina of the BBB and further opens the BBB (157). This has been most clearly demonstrated in the MHV model, where depletion of MMP-9 inhibited lymphocyte infiltration into the CNS (157, 158). Dendritic cells (DC) are seen in the CNS within a few days after CNS viral infection. These cells rely on the chemokine CCL3 to migrate to cervical lymph nodes draining the CNS, where they prime virus-specific T cells (159).

T cells

In the MHV model, virus-specific CD8+ T cells are detected in local lymph nodes prior to CNS infiltration and then accumulate in the CNS (160). Both CD4+ and CD8+ T cells are in part recruited to the CNS by the chemokines, CXCL9 and CXCL10, acting through their cognate receptor, CXCR3 (161163). T cell expression of CCR2 and CCR5 likely contribute to CNS recruitment as well (164, 165). The role of CD4+ T cells in this setting is to support CD8+ T cell function via the production of IFN-γ (166). CD8+ T cells are the main anti-viral effector cells in the CNS during infection and are essential for clearing virus from glial cells (142, 167, 168). CD8+ T cells produce IFN-γ and lytic molecules, including granzyme B and perforin (169). These lytic molecules eliminate virally infected astrocytes (170), while IFN-γ serves to control viral replication in oligodendrocytes (171, 172). In both the MHV and Sindbis virus (SINV) encephalitis models, T cells promote B cell proliferation and differentiation (173, 174), in part by secreting the cytokines, IL-10 and IL-21 (175177).

B cells and anti-viral antibodies

Virus-specific ASC help control viruses in the CNS through potent complement-independent, non-cytolytic mechanisms (141, 178183). These ASC arise either from ectopic lymphoid follicle-like structures within the CNS (152) or migrate from cervical lymph nodes where they have expanded and up-regulated CXCR3 and CXCR4 on their surface prior to entering the CNS (184). ASC recruitment to the CNS has been most extensively studied in the SINV encephalitis model. The initial ASC entering the CNS have an HLA class II positive, plasmablast-like phenotype, but these cells gradually lose HLA class II expression and acquire a more plasma cell-like phenotype (139, 141). Virus-specific antibodies function to neutralize both extracellular virus as well as virus particles budding from infected cell membranes. During SINV infection, antibodies that bind the E2 viral envelope glycoprotein inhibit virus replication (185) and prevent viral budding from infected neurons without actually killing target cells (182, 186). Similarly, during rabies virus infection, antibodies against the RV glycoprotein inhibit viral RNA transcription and prevent cell-to-cell viral spread (187). Antibodies can also trigger natural killer (NK) cells and macrophages to induce antibody dependent cell-mediated cytolysis of virally infected cells (152). Finally, in exchange for non-cytolytic viral clearance in the acute setting, virus-specific ASC must persist in the CNS long term to prevent viral reactivation at a later date since viral RNA is never fully eradicated from target tissues (139).

Host Immune Responses to Self (Myelin) Antigens in the CNS

Multiple sclerosis

Multiple sclerosis, an autoimmune disease characterized by infiltrating immune cells targeting myelin antigens in the CNS, is the most common cause of neurologic disability in persons younger than 40 years of age (188). Pathologically, MS lesions are characterized by focal inflammation, demyelination, and axonal damage (189). MS is a complex disease whose occurrence and progression are influenced by both genetic (190192) and environmental (193, 194) risk factors. Evidence derived from both human genetic studies and a related mouse model, experimental autoimmune encephalomyelitis (EAE), suggest that encephalitogenic CD4+ T cells are primary initiators of disease. Genome-wide association studies show that MS risk alleles are confined to immune related genes governing antigen presentation as well as the proliferation and survival of T cells, including HLA class II (HLA-DRB1*1501), IL-2R, and IL-7R (190192). Moreover, EAE in mice is induced by immunizing animals with various myelin peptides (195), or via the adoptive transfer of myelin-specific CD4+ T cells, resulting in a disease having some clinical and pathological similarities to human MS (196, 197). In MS patients, CD4+ T cells localize within CNS lesions present in the brain (198) and spinal cord (199), and elevated frequencies of myelin-reactive CD4+ T cells can be found in circulating the blood (200, 201). Although not described in detail here due to space constraints, many MS lesions also contain abundant CD8+ T cells whose specificity and role in disease pathogenesis remain poorly understood. Likewise, therapies targeted specifically at B cells have proven highly effective in MS patients, highlighting an emerging role for this cell type in both relapsing and progressive forms of disease.

Role of CD4+ T cells in autoimmune inflammation of the CNS

During both MS and EAE, self-reactive T cells are likely activated in the periphery (189), where they undergo initial differentiation and expansion (124). Upon entry into the CNS, these cells are reactivated by myelin epitopes presented by an as of yet unidentified local DC (202, 203). Production of cytokines such as IFN-γ and TNF-α from activated CD4+ T cells results in local activation of resting microglia, leading to the up-regulation of HLA class I and II as well as co-stimulatory molecules (B7-1, B7-2, and CD40) on the surface of these cells (133, 134, 204, 205). These activated microglia are capable of serving as APC for infiltrating myelin-specific CD4+ T cells in vivo thus sustaining this pathogenic local T cell response (). Production of cytokines, chemokines, and MMPs by microglia (206) facilitate local inflammation by causing BBB breakdown and recruiting more immune cells into the CNS. These include circulating monocytes capable of differentiating into inflammatory DC and macrophages upon tissue entry (207), culminating in demyelination (124). Furthermore, microglial production of IL-23 and IL-1β promotes granulocyte macrophage colony-stimulating factor (GM-CSF) secretion by CD4+ T cells (208). GM-CSF has been shown in EAE to promote CNS inflammation by mobilizing Ly6Chi monocytes from the bone marrow into the periphery, thereby increasing the number of circulating monocytes available for recruitment to the CNS (207). GM-CSF can also increase HLA class II expression and pro-inflammatory cytokine production by microglia, macrophages, and DC in vitro (209, 210). IL-17 producing T cells have been detected within CNS lesions during both EAE and MS (211, 212). IL-17 promotes brain inflammation, inducing the production of pro-inflammatory cytokines, TNF-α, IL-6, and IL-1β most probably from astrocytes, microglia, or macrophages. It also stimulates the release of chemokines responsible for recruiting neutrophils to the CNS, particularly CXCL1 and CXCL2 (213, 214). Finally, IL-17 can disrupt TJ in the BBB, allowing further migration of CD4+ T cells to the CNS (212, 215).

Role of glial cells in autoimmune inflammation of the CNS

Microglia

Microglia play important roles in augmenting CNS inflammation, demyelination, and neuronal damage in both EAE and MS (, 216218). Activation of microglia occurs rapidly following the induction of EAE and results in the release of cytokines, chemokines, ROS, and tissue-degrading MMP (206). One mediator, TNF-like weak inducer of apoptosis (TWEAK), triggers proliferation, angiogenesis, inflammation, is associated with extensive myelin loss, and induces astrocyte cell death during MS (219). IL-17 produced by microglia (220) worsens brain inflammation by stimulating GM-CSF production, as well as increasing IL-6, inflammatory proteins, nitric oxide, and adhesion molecule expression by macrophages. Moreover, expression of myeloperoxidase (MPO) and ROS by microglia results in direct myelin degradation and neuronal damage (216, 218). Paradoxically, microglia also can play a neuroprotective role during CNS autoimmunity. These cells can promote remyelination, protect neurons, and suppress the adaptive immune response within the CNS (221, 222). Within MS lesions, microglia and macrophages express the neurotrophic factors, nerve growth factor (NGF), and brain-derived neurotrophic factor (BDNF), supporting neuronal survival (220, 223, 224). Furthermore, microglia secrete the anti-inflammatory cytokines, IL-10 and TGF-β, and express the inhibitory receptor, PD-L1, responsible for inhibiting T cell proliferation and cytokine production (, 225).

Astrocytes

Astrocytes are a major source of CCL2 and CXCL10 in the CNS, regulating the migration of monocytes into the brain (CCL2) and microglia into the lesion site (CXCL10) (111, 226228). One study suggested these cells play a more prominent role in regulating the recruitment of peripheral monocytes into the CNS (229). CXCL12, a chemokine that induces the expression of CXCL8 and CCL2, is also expressed by astrocytes in MS lesions (230). CXCL12 can be cleaved by MMP-2, also expressed by astrocytes in MS and EAE, into a neurotoxic peptide that causes further neuronal damage (231). Similar to microglia, astrocytes also play a protective role during MS and EAE. Homeostatic astrocyte functions include buffering potassium, removing extracellular glutamate that can accumulate to toxic levels, adjusting water balance, and controlling synaptic activity and blood flow in the CNS (). These cells are also able to produce neurotrophins and the anti-inflammatory cytokine, IL-10 (232).

Conclusion

The vast complexity of cellular interconnections within the CNS, and the non-renewable nature of many neural cells, mandate that some local immune responses be tightly controlled while others (i.e., cytolytic ones) be excluded to the fullest extent possible. The BBB is a dynamic and highly regulated tissue interface that helps make the CNS a unique immunological environment. It responds to signals from both neurons and glial cells on one side while simultaneously being able to sample immunological events passing through intravascular compartments. Immune cells perform normal surveillance of the CNS by searching for antigens previously encountered in extraneural sites such as the deep cervical lymph nodes. Pathological conditions such as infections caused by viruses or bacteria elicit changes at the BBB, including the up-regulation of a unique subset of adhesion molecules as well as heightened release of chemokines by ECs. Mediators produced by astrocytes and microglia further increase BBB permeability and recruit additional circulating leukocytes into the CNS. The ensuing immune response must then be tightly controlled in order to avoid collateral tissue damage. As such, astrocytes and microglia maintain mechanisms to dampen inflammatory responses. In some settings, immune cells such as ASC persist long term within the CNS to prevent viral reactivation. When normal control mechanisms fail, neuroinflammatory diseases such as MS can result. For this reason alone, it is imperative that the complexity of immune reactions within the CNS be better understood.

Statements

Conflict of interest

The authors declare that the research was conducted in the absence of any commercial or financial relationships that could be construed as a potential conflict of interest.

References

  • 1

    EhrlichPBolduanC. Collected Studies on Immunity. 1st ed. New York, NY: John Wiley & Sons (1906). 586 p.

  • 2

    MurphyJBSturmE. Conditions determining the transplantability of tissues in the brain. J Exp Med (1923) 38(2):18397.10.1084/jem.38.2.183

  • 3

    MedawarPB. Immunity to homologous grafted skin; the fate of skin homografts transplanted to the brain, to subcutaneous tissue, and to the anterior chamber of the eye. Br J Exp Pathol (1948) 29(1):5869.

  • 4

    BanksWA. The blood-brain barrier in neuroimmunology: tales of separation and assimilation. Brain Behav Immun (2014).10.1016/j.bbi.2014.08.007

  • 5

    AbbottNJMendoncaLLDolmanDE. The blood-brain barrier in systemic lupus erythematosus. Lupus (2003) 12(12):90815.10.1191/0961203303lu501oa

  • 6

    AbbottNJRonnbackLHanssonE. Astrocyte-endothelial interactions at the blood-brain barrier. Nat Rev Neurosci (2006) 7(1):4153.10.1038/nrn1824

  • 7

    BrownRCMorrisAPO’NeilRG. Tight junction protein expression and barrier properties of immortalized mouse brain microvessel endothelial cells. Brain Res (2007) 1130(1):1730.10.1016/j.brainres.2006.10.083

  • 8

    De BockMVandenbrouckeREDecrockECulotMCecchelliRLeybaertL. A new angle on blood-CNS interfaces: a role for connexins?FEBS Lett (2014) 588(8):125970.10.1016/j.febslet.2014.02.060

  • 9

    EngelhardtB. The blood-central nervous system barriers actively control immune cell entry into the central nervous system. Curr Pharm Des (2008) 14(16):155565.10.2174/138161208784705432

  • 10

    GreenwoodJHeasmanSJAlvarezJIPratALyckREngelhardtB. Review: leucocyte-endothelial cell crosstalk at the blood-brain barrier: a prerequisite for successful immune cell entry to the brain. Neuropathol Appl Neurobiol (2011) 37(1):2439.10.1111/j.1365-2990.2010.01140.x

  • 11

    EngelhardtBRansohoffRM. The ins and outs of T-lymphocyte trafficking to the CNS: anatomical sites and molecular mechanisms. Trends Immunol (2005) 26(9):48595.10.1016/j.it.2005.07.004

  • 12

    AbbottNJPatabendigeAADolmanDEYusofSRBegleyDJ. Structure and function of the blood-brain barrier. Neurobiol Dis (2010) 37(1):1325.10.1016/j.nbd.2009.07.030

  • 13

    LokJGuptaPGuoSKimWJWhalenMJvan LeyenKet alCell-cell signaling in the neurovascular unit. Neurochem Res (2007) 32(12):203245.10.1007/s11064-007-9342-9

  • 14

    AmarJBurcelinRRuidavetsJBCaniPDFauvelJAlessiMCet alEnergy intake is associated with endotoxemia in apparently healthy men. Am J Clin Nutr (2008) 87(5):121923.

  • 15

    AncutaPKamatAKunstmanKJKimEYAutissierPWurcelAet alMicrobial translocation is associated with increased monocyte activation and dementia in AIDS patients. PLoS One (2008) 3(6):e2516.10.1371/journal.pone.0002516

  • 16

    BrenchleyJMPriceDASchackerTWAsherTESilvestriGRaoSet alMicrobial translocation is a cause of systemic immune activation in chronic HIV infection. Nat Med (2006) 12(12):136571.10.1038/nm1511

  • 17

    GhoshalSWittaJZhongJde VilliersWEckhardtE. Chylomicrons promote intestinal absorption of lipopolysaccharides. J Lipid Res (2009) 50(1):907.10.1194/jlr.M800156-JLR200

  • 18

    MaesMKuberaMLeunisJC. The gut-brain barrier in major depression: intestinal mucosal dysfunction with an increased translocation of LPS from gram negative enterobacteria (leaky gut) plays a role in the inflammatory pathophysiology of depression. Neuro Endocrinol Lett (2008) 29(1):11724.

  • 19

    NgQYLeeKWByrneCHoTFLimCL. Plasma endotoxin and immune responses during a 21-km road race under a warm and humid environment. Ann Acad Med Singapore (2008) 37(4):30714.

  • 20

    SikkelandLISkogstadMOvstebøRBruslettoBHaugKBKongerudJet alCirculating lipopolysaccharides in the blood from “bioprotein” production workers. Occup Environ Med (2008) 65(3):2114.10.1136/oem.2007.032938

  • 21

    ZhangRMillerRGGasconRChampionSKatzJLanceroMet alCirculating endotoxin and systemic immune activation in sporadic amyotrophic lateral sclerosis (sALS). J Neuroimmunol (2009) 206(1–2):1214.10.1016/j.jneuroim.2008.09.017

  • 22

    SimardMArcuinoGTakanoTLiuQSNedergaardM. Signaling at the gliovascular interface. J Neurosci (2003) 23(27):925462.

  • 23

    GimsaUMitchisonNABrunner-WeinzierMC. Immune privilege as an intrinsic CNS property: astrocytes protect the CNS against T-cell-mediated neuroinflammation. Mediators Inflamm (2013) 2013:320519.10.1155/2013/320519

  • 24

    BechmannIGaleaIPerryVH. What is the blood-brain barrier (not)?Trends Immunol (2007) 28(1):511.10.1016/j.it.2006.11.007

  • 25

    SaundersNRHabgoodMDDziegielewskaKM. Barrier mechanisms in the brain, II. Immature brain. Clin Exp Pharmacol Physiol (1999) 26(2):8591.10.1046/j.1440-1681.1999.02987.x

  • 26

    SaundersNREkCJHabgoodMDDziegielewskaKM. Barriers in the brain: a renaissance?Trends Neurosci (2008) 31(6):27986.10.1016/j.tins.2008.03.003

  • 27

    MulliganSJMacVicarBA. Calcium transients in astrocyte endfeet cause cerebrovascular constrictions. Nature (2004) 431(7005):1959.10.1038/nature02827

  • 28

    ArmulikAGenovéGMäeMNisanciogluMHWallgardENiaudetCet alPericytes regulate the blood-brain barrier. Nature (2010) 468(7323):55761.10.1038/nature09522

  • 29

    DanemanRZhouLKebedeAABarresBA. Pericytes are required for blood-brain barrier integrity during embryogenesis. Nature (2010) 468(7323):5626.10.1038/nature09513

  • 30

    Sa-PereiraIBritesDBritoMA. Neurovascular unit: a focus on pericytes. Mol Neurobiol (2012) 45(2):32747.10.1007/s12035-012-8244-2

  • 31

    EngelhardtSPatkarSOgunsholaOO. Cell-specific blood-brain barrier regulation in health and disease: a focus on hypoxia. Br J Pharmacol (2014) 171(5):121030.10.1111/bph.12489

  • 32

    MuoioVPerssonPBSendeskiMM. The neurovascular unit – concept review. Acta Physiol (Oxf) (2014) 210(4):7908.10.1111/apha.12250

  • 33

    Antonelli-OrlidgeASaundersKBSmithSRD’AmorePA. An activated form of transforming growth factor beta is produced by cocultures of endothelial cells and pericytes. Proc Natl Acad Sci U S A (1989) 86(12):45448.10.1073/pnas.86.12.4544

  • 34

    FrigerioSGelatiMCiusaniECorsiniEDufourAMassaGet alImmunocompetence of human microvascular brain endothelial cells: cytokine regulation of IL-1beta, MCP-1, IL-10, sICAM-1 and sVCAM-1. J Neurol (1998) 245(11):72730.10.1007/s004150050275

  • 35

    BrightmanMWReeseTS. Junctions between intimately apposed cell membranes in the vertebrate brain. J Cell Biol (1969) 40(3):64877.10.1083/jcb.40.3.648

  • 36

    ReeseTSKarnovskyMJ. Fine structural localization of a blood-brain barrier to exogenous peroxidase. J Cell Biol (1967) 34(1):20717.10.1083/jcb.34.1.207

  • 37

    GeSSongLPachterJS. Where is the blood-brain barrier really?J Neurosci Res (2005) 79(4):4217.10.1002/jnr.20313

  • 38

    EkCJDziegielewskaKMStolpHSaundersNR. Functional effectiveness of the blood-brain barrier to small water-soluble molecules in developing and adult opossum (Monodelphis domestica). J Comp Neurol (2006) 496(1):1326.10.1002/cne.20885

  • 39

    RibattiDNicoBCrivellatoEArticoM. Development of the blood-brain barrier: a historical point of view. Anat Rec B New Anat (2006) 289(1):38.10.1002/ar.b.20087

  • 40

    BradburyMW. The blood-brain barrier. Exp Physiol (1993) 78(4):45372.

  • 41

    CroneCOlesenSP. Electrical resistance of brain microvascular endothelium. Brain Res (1982) 241(1):4955.10.1016/0006-8993(82)91227-6

  • 42

    DejanaE. Endothelial cell-cell junctions: happy together. Nat Rev Mol Cell Biol (2004) 5(4):26170.10.1038/nrm1357

  • 43

    NagasawaKChibaHFujitaHKojimaTSaitoTEndoTet alPossible involvement of gap junctions in the barrier function of tight junctions of brain and lung endothelial cells. J Cell Physiol (2006) 208(1):12332.10.1002/jcp.20647

  • 44

    PratABiernackiKWosikKAntelJP. Glial cell influence on the human blood-brain barrier. Glia (2001) 36(2):14555.10.1002/glia.1104

  • 45

    WolburgHLippoldtA. Tight junctions of the blood-brain barrier: development, composition and regulation. Vascul Pharmacol (2002) 38(6):32337.10.1016/S1537-1891(02)00200-8

  • 46

    NittaTHataMGotohSSeoYSasakiHHashimotoNet alSize-selective loosening of the blood-brain barrier in claudin-5-deficient mice. J Cell Biol (2003) 161(3):65360.10.1083/jcb.200302070

  • 47

    LippoldtALiebnerSAndbjerBKalbacherHWolburgHHallerHet alOrganization of choroid plexus epithelial and endothelial cell tight junctions and regulation of claudin-1, -2 and -5 expression by protein kinase C. Neuroreport (2000) 11(7):142731.10.1097/00001756-200005150-00015

  • 48

    SaitouMFuruseMSasakiHSchulzkeJDFrommMTakanoHet alComplex phenotype of mice lacking occludin, a component of tight junction strands. Mol Biol Cell (2000) 11(12):413142.10.1091/mbc.11.12.4131

  • 49

    McCarthyMWoodCFedoseyevaLWhittemoreSR. Media components influence viral gene expression assays in human fetal astrocyte cultures. J Neurovirol (1995) 1(3–4):27585.10.3109/13550289509114024

  • 50

    DaviesDC. Blood-brain barrier breakdown in septic encephalopathy and brain tumours. J Anat (2002) 200(6):63946.10.1046/j.1469-7580.2002.00065.x

  • 51

    KratzerIVasiljevicAReyCFevre-MontangeMSaundersNStrazielleNet alComplexity and developmental changes in the expression pattern of claudins at the blood-CSF barrier. Histochem Cell Biol (2012) 138(6):86179.10.1007/s00418-012-1001-9

  • 52

    HawkinsBTDavisTP. The blood-brain barrier/neurovascular unit in health and disease. Pharmacol Rev (2005) 57(2):17385.10.1124/pr.57.2.4

  • 53

    JohanssonPADziegielewskaKMLiddelowSASaundersNR. The blood-CSF barrier explained: when development is not immaturity. Bioessays (2008) 30(3):23748.10.1002/bies.20718

  • 54

    RedzicZ. Molecular biology of the blood-brain and the blood-cerebrospinal fluid barriers: similarities and differences. Fluids Barriers CNS (2011) 8(1):3.10.1186/2045-8118-8-3

  • 55

    DelMR. Bigio, ependymal cells: biology and pathology. Acta Neuropathol (2010) 119(1):5573.10.1007/s00401-009-0624-y

  • 56

    DermietzelR. Junctions in the central nervous system of the cat. IV. Interendothelial junctions of cerebral blood vessels from selected areas of the brain. Cell Tissue Res (1975) 164(1):4562.

  • 57

    SaitoYWrightEM. Regulation of bicarbonate transport across the brush border membrane of the bull-frog choroid plexus. J Physiol (1984) 350:32742.

  • 58

    ShechterRLondonASchwartzM. Orchestrated leukocyte recruitment to immune-privileged sites: absolute barriers versus educational gates. Nat Rev Immunol (2013) 13(3):20618.10.1038/nri3391

  • 59

    GaleaIBechmannIPerryVH. What is immune privilege (not)?Trends Immunol (2007) 28(1):128.10.1016/j.it.2006.11.004

  • 60

    RansohoffRMEngelhardtB. The anatomical and cellular basis of immune surveillance in the central nervous system. Nat Rev Immunol (2012) 12(9):62335.10.1038/nri3265

  • 61

    LiblauRSGonzalez-DuniaDWiendlHZippF. Neurons as targets for T cells in the nervous system. Trends Neurosci (2013) 36(6):31524.10.1016/j.tins.2013.01.008

  • 62

    WellerROEngelhardtBPhillipsMJ. Lymphocyte targeting of the central nervous system: a review of afferent and efferent CNS-immune pathways. Brain Pathol (1996) 6(3):27588.10.1111/j.1750-3639.1996.tb00855.x

  • 63

    HickeyWFHsuBLKimuraH. T-lymphocyte entry into the central nervous system. J Neurosci Res (1991) 28(2):25460.10.1002/jnr.490280213

  • 64

    WekerleHLiningtonCLassmannHMeyermannR. Cellular immune reactivity within the CNS. Trends Neurosci (1986) 9(6):2717.10.1016/0166-2236(86)90077-9

  • 65

    HickeyWF. Migration of hematogenous cells through the blood-brain barrier and the initiation of CNS inflammation. Brain Pathol (1991) 1(2):97105.10.1111/j.1750-3639.1991.tb00646.x

  • 66

    McMenaminPG. Distribution and phenotype of dendritic cells and resident tissue macrophages in the dura mater, leptomeninges, and choroid plexus of the rat brain as demonstrated in wholemount preparations. J Comp Neurol (1999) 405(4):55362.10.1002/(SICI)1096-9861(19990322)405:4<553::AID-CNE8>3.0.CO;2-6

  • 67

    TranEHHoekstraKvan RooijenNDijkstraCDOwensT. Immune invasion of the central nervous system parenchyma and experimental allergic encephalomyelitis, but not leukocyte extravasation from blood, are prevented in macrophage-depleted mice. J Immunol (1998) 161(7):376775.

  • 68

    RaineCSCannellaBDuijvestijnAMCrossAH. Homing to central nervous system vasculature by antigen-specific lymphocytes. II. Lymphocyte/endothelial cell adhesion during the initial stages of autoimmune demyelination. Lab Invest (1990) 63(4):47689.

  • 69

    ZeineROwensT. Direct demonstration of the infiltration of murine central-nervous-system by Pgp-1/Cd44high Cd45rblow Cd4+ T-cells that induce experimental allergic encephalomyelitis. J Neuroimmunol (1992) 40(1):5770.10.1016/0165-5728(92)90213-5

  • 70

    EngelhardtBMartin-SimonetMTRottLSButcherECMichieSA. Adhesion molecule phenotype of T lymphocytes in inflamed CNS. J Neuroimmunol (1998) 84(1):92104.10.1016/S0165-5728(97)00237-3

  • 71

    EngelhardtBConleyFKKilshawPJButcherEC. Lymphocytes infiltrating the CNS during inflammation display a distinctive phenotype and bind to VCAM-1 but not to MAdCAM-1. Int Immunol (1995) 7(3):48191.10.1093/intimm/7.3.481

  • 72

    BechmannIMorGNilsenJElizaMNitschRNaftolinF. FasL (CD95L, Apo1L) is expressed in the normal rat and human brain: evidence for the existence of an immunological brain barrier. Glia (1999) 27(1):6274.10.1002/(SICI)1098-1136(199907)27:1<62::AID-GLIA7>3.0.CO;2-S

  • 73

    MeinlEAloisiFErtlBWeberFde Waal MalefytRWekerleHet alMultiple sclerosis. Immunomodulatory effects of human astrocytes on T cells. Brain (1994) 117(Pt 6):132332.10.1093/brain/117.6.1323

  • 74

    MagnusTSchreinerBKornTJackCGuoHAntelJet alMicroglial expression of the B7 family member B7 homolog 1 confers strong immune inhibition: implications for immune responses and autoimmunity in the CNS. J Neurosci (2005) 25(10):253746.10.1523/JNEUROSCI.4794-04.2005

  • 75

    LiuYTeigeIBirnirBIssazadeh-NavikasS. Neuron-mediated generation of regulatory T cells from encephalitogenic T cells suppresses EAE. Nat Med (2006) 12(5):51825.10.1038/nm1402

  • 76

    SarrazinJLBonnevilleFMartin-BlondelG. Brain infections. Diagn Interv Imaging (2012) 93(6):47390.10.1016/j.diii.2012.04.020

  • 77

    CoureuilMMikatyGMillerFLécuyerHBernardCBourdoulousSet alMeningococcal type IV pili recruit the polarity complex to cross the brain endothelium. Science (2009) 325(5936):837.10.1126/science.1173196

  • 78

    MarriottHMMitchellTJDockrellDH. Pneumolysin: a double-edged sword during the host-pathogen interaction. Curr Mol Med (2008) 8(6):497509.10.2174/156652408785747924

  • 79

    AttaliCDurmortCVernetTDi GuilmiAM. The interaction of Streptococcus pneumoniae with plasmin mediates transmigration across endothelial and epithelial monolayers by intercellular junction cleavage. Infect Immun (2008) 76(11):53506.10.1128/IAI.00184-08

  • 80

    RingAWeiserJNTuomanenEI. Pneumococcal trafficking across the blood-brain barrier. Molecular analysis of a novel bidirectional pathway. J Clin Invest (1998) 102(2):34760.10.1172/JCI2406

  • 81

    KoedelU. Toll-like receptors in bacterial meningitis. Curr Top Microbiol Immunol (2009) 336:1540.10.1007/978-3-642-00549-7_2

  • 82

    BsibsiMRavidRGvericDvan NoortJM. Broad expression of Toll-like receptors in the human central nervous system. J Neuropathol Exp Neurol (2002) 61(11):101321.

  • 83

    DengGMLiuZQTarkowskiA. Intracisternally localized bacterial DNA containing CpG motifs induces meningitis. J Immunol (2001) 167(8):461626.10.4049/jimmunol.167.8.4616

  • 84

    HanischUKPrinzMAngstwurmKHäuslerKGKannOKettenmannHet alThe protein tyrosine kinase inhibitor AG126 prevents the massive microglial cytokine induction by pneumococcal cell walls. Eur J Immunol (2001) 31(7):210415.10.1002/1521-4141(200107)31:7<2104::AID-IMMU2104>3.0.CO;2-3

  • 85

    RockRBGekkerGHuSShengWSCheeranMLokensgardJRet alRole of microglia in central nervous system infections. Clin Microbiol Rev (2004) 17(4):94264.10.1128/CMR.17.4.942-964.2004

  • 86

    KreutzbergGW. Microglia, the first line of defence in brain pathologies. Arzneimittelforschung (1995) 45(3A):35760.

  • 87

    PetersonPKGekkerGHuSShengWSAndersonWRUlevitchRJet alCD14 receptor-mediated uptake of nonopsonized Mycobacterium tuberculosis by human microglia. Infect Immun (1995) 63(4):1598602.

  • 88

    RockRBHuSGekkerGShengWSMayBKapurVet alMycobacterium tuberculosis-induced cytokine and chemokine expression by human microglia and astrocytes: effects of dexamethasone. J Infect Dis (2005) 192(12):20548.10.1086/498165

  • 89

    KielianTMayesPKielianM. Characterization of microglial responses to Staphylococcus aureus: effects on cytokine, costimulatory molecule, and toll-like receptor expression. J Neuroimmunol (2002) 130(1–2):8699.10.1016/S0165-5728(02)00216-3

  • 90

    KielianTEsenNBeardenED. Toll-like receptor 2 (TLR2) is pivotal for recognition of S. aureus peptidoglycan but not intact bacteria by microglia. Glia (2005) 49(4):56776.10.1002/glia.20144

  • 91

    KielianTPhulwaniNKEsenNSyedMMHaneyACMcCastlainKet alMyD88-dependent signals are essential for the host immune response in experimental brain abscess. J Immunol (2007) 178(7):452837.10.4049/jimmunol.178.7.4528

  • 92

    LeppertDLindbergRLKapposLLeibSL. Matrix metalloproteinases: multifunctional effectors of inflammation in multiple sclerosis and bacterial meningitis. Brain Res Brain Res Rev (2001) 36(2–3):24957.10.1016/S0165-0173(01)00101-1

  • 93

    BanatiRBGehrmannJSchubertPKreutzbergGW. Cytotoxicity of microglia. Glia (1993) 7(1):1118.10.1002/glia.440070117

  • 94

    BanatiRBRotheGValetGKreutzbergGW. Detection of lysosomal cysteine proteinases in microglia: flow cytometric measurement and histochemical localization of cathepsin B and L. Glia (1993) 7(2):18391.10.1002/glia.440070208

  • 95

    ColtonCAGilbertDL. Microglia, an in vivo source of reactive oxygen species in the brain. Adv Neurol (1993) 59:3216.

  • 96

    ColtonCAKeriJEChenWTMonskyWL. Protease production by cultured microglia: substrate gel analysis and immobilized matrix degradation. J Neurosci Res (1993) 35(3):297304.10.1002/jnr.490350309

  • 97

    AloisiF. Immune function of microglia. Glia (2001) 36(2):16579.10.1002/glia.1106

  • 98

    SofroniewMVVintersHV. Astrocytes: biology and pathology. Acta Neuropathol (2010) 119(1):735.10.1007/s00401-009-0619-8

  • 99

    AlvarezJIKatayamaTPratA. Glial influence on the blood brain barrier. Glia (2013) 61(12):193958.10.1002/glia.22575

  • 100

    JohnGRScemesESuadicaniSOLiuJSCharlesPCLeeSCet alIL-1beta differentially regulates calcium wave propagation between primary human fetal astrocytes via pathways involving P2 receptors and gap junction channels. Proc Natl Acad Sci U S A (1999) 96(20):116138.10.1073/pnas.96.20.11613

  • 101

    DuffyHSJohnGRLeeSCBrosnanCFSprayDC. Reciprocal regulation of the junctional proteins claudin-1 and connexin43 by interleukin-1beta in primary human fetal astrocytes. J Neurosci (2000) 20(23):RC114.

  • 102

    BolanosJPMedinaJM. Induction of nitric oxide synthase inhibits gap junction permeability in cultured rat astrocytes. J Neurochem (1996) 66(5):20919.10.1046/j.1471-4159.1996.66052091.x

  • 103

    ReussBUnsickerK. Regulation of gap junction communication by growth factors from non-neural cells to astroglia: a brief review. Glia (1998) 24(1):328.10.1002/(SICI)1098-1136(199809)24:1<32::AID-GLIA4>3.0.CO;2-2

  • 104

    AllamanIBelangerMMagistrettiPJ. Astrocyte-neuron metabolic relationships: for better and for worse. Trends Neurosci (2011) 34(2):7687.10.1016/j.tins.2010.12.001

  • 105

    McKimmieCSGrahamGJ. Astrocytes modulate the chemokine network in a pathogen-specific manner. Biochem Biophys Res Commun (2010) 394(4):100611.10.1016/j.bbrc.2010.03.111

  • 106

    LobsigerCSClevelandDW. Glial cells as intrinsic components of non-cell-autonomous neurodegenerative disease. Nat Neurosci (2007) 10(11):135560.10.1038/nn1988

  • 107

    VesceSRossiDBrambillaLVolterraA. Glutamate release from astrocytes in physiological conditions and in neurodegenerative disorders characterized by neuroinflammation. Int Rev Neurobiol (2007) 82:5771.10.1016/S0074-7742(07)82003-4

  • 108

    BonifatiDMKishoreU. Role of complement in neurodegeneration and neuroinflammation. Mol Immunol (2007) 44(5):9991010.10.1016/j.molimm.2006.03.007

  • 109

    PanenkaWJijonHHerxLMArmstrongJNFeighanDWeiTet alP2X7-like receptor activation in astrocytes increases chemokine monocyte chemoattractant protein-1 expression via mitogen-activated protein kinase. J Neurosci (2001) 21(18):713542.

  • 110

    LiuMTChenBPOertelPBuchmeierMJArmstrongDHamiltonTAet alThe T cell chemoattractant IFN-inducible protein 10 is essential in host defense against viral-induced neurologic disease. J Immunol (2000) 165(5):232730.10.4049/jimmunol.165.5.2327

  • 111

    RansohoffRMHamiltonTATaniMStolerMHShickHEMajorJAet alAstrocyte expression of mRNA encoding cytokines IP-10 and JE/MCP-1 in experimental autoimmune encephalomyelitis. FASEB J (1993) 7(6):592600.

  • 112

    CarpentierPABegolkaWSOlsonJKElhofyAKarpusWJMillerSD. Differential activation of astrocytes by innate and adaptive immune stimuli. Glia (2005) 49(3):36074.10.1002/glia.20117

  • 113

    GirvinAMGordonKBWelshCJClipstoneNAMillerSD. Differential abilities of central nervous system resident endothelial cells and astrocytes to serve as inducible antigen-presenting cells. Blood (2002) 99(10):3692701.10.1182/blood-2001-12-0229

  • 114

    LeeSJParkJYHouJBenvenisteEN. Transcriptional regulation of the intercellular adhesion molecule-1 gene by proinflammatory cytokines in human astrocytes. Glia (1999) 25(1):2132.10.1002/(SICI)1098-1136(19990101)25:1<21::AID-GLIA3>3.0.CO;2-R

  • 115

    RosenmanSJShrikantPDubbLBenvenisteENRansohoffRM. Cytokine-induced expression of vascular cell adhesion molecule-1 (VCAM-1) by astrocytes and astrocytoma cell lines. J Immunol (1995) 154(4):188899.

  • 116

    ShrikantPChungIYBallestasMEBenvenisteEN. Regulation of intercellular adhesion molecule-1 gene expression by tumor necrosis factor-alpha, interleukin-1 beta, and interferon-gamma in astrocytes. J Neuroimmunol (1994) 51(2):20920.10.1016/0165-5728(94)90083-3

  • 117

    BorregaardN. Neutrophils, from marrow to microbes. Immunity (2010) 33(5):65770.10.1016/j.immuni.2010.11.011

  • 118

    NathanC. Neutrophils and immunity: challenges and opportunities. Nat Rev Immunol (2006) 6(3):17382.10.1038/nri1785

  • 119

    LacroixSFeinsteinDRivestS. The bacterial endotoxin lipopolysaccharide has the ability to target the brain in upregulating its membrane CD14 receptor within specific cellular populations. Brain Pathol (1998) 8(4):62540.10.1111/j.1750-3639.1998.tb00189.x

  • 120

    RameshGMacLeanAGPhilippMT. Cytokines and chemokines at the crossroads of neuroinflammation, neurodegeneration, and neuropathic pain. Mediators Inflamm (2013) 2013:480739.10.1155/2013/480739

  • 121

    KielianTBarryBHickeyWF. CXC chemokine receptor-2 ligands are required for neutrophil-mediated host defense in experimental brain abscesses. J Immunol (2001) 166(7):463443.10.4049/jimmunol.166.7.4634

  • 122

    KastenbauerSAngeleBSporerBPfisterHWKoedelU. Patterns of protein expression in infectious meningitis: a cerebrospinal fluid protein array analysis. J Neuroimmunol (2005) 164(1–2):1349.10.1016/j.jneuroim.2005.03.009

  • 123

    SpanausKSNadalDPfisterHWSeebachJWidmerUFreiKet alC-X-C and C-C chemokines are expressed in the cerebrospinal fluid in bacterial meningitis and mediate chemotactic activity on peripheral blood-derived polymorphonuclear and mononuclear cells in vitro. J Immunol (1997) 158(4):195664.

  • 124

    RansohoffRMBrownMA. Innate immunity in the central nervous system. J Clin Invest (2012) 122(4):116471.10.1172/JCI58644

  • 125

    MantovaniACassatellaMACostantiniCJaillonS. Neutrophils in the activation and regulation of innate and adaptive immunity. Nat Rev Immunol (2011) 11(8):51931.10.1038/nri3024

  • 126

    Bernardes-SilvaMAnthonyDCIssekutzACPerryVH. Recruitment of neutrophils across the blood-brain barrier: the role of E- and P-selectins. J Cereb Blood Flow Metab (2001) 21(9):111524.10.1097/00004647-200109000-00009

  • 127

    NealJWGasqueP. How does the brain limit the severity of inflammation and tissue injury during bacterial meningitis?J Neuropathol Exp Neurol (2013) 72(5):37085.10.1097/NEN.0b013e3182909f2f

  • 128

    CederlundAGudmundssonGHAgerberthB. Antimicrobial peptides important in innate immunity. FEBS J (2011) 278(20):394251.10.1111/j.1742-4658.2011.08302.x

  • 129

    CardonaAELiMLiuLSavarinCRansohoffRM. Chemokines in and out of the central nervous system: much more than chemotaxis and inflammation. J Leukoc Biol (2008) 84(3):58794.10.1189/jlb.1107763

  • 130

    MüllerMCarterSHoferMJCampbellIL. Review: the chemokine receptor CXCR3 and its ligands CXCL9, CXCL10 and CXCL11 in neuroimmunity – a tale of conflict and conundrum. Neuropathol Appl Neurobiol (2010) 36(5):36887.10.1111/j.1365-2990.2010.01089.x

  • 131

    KwokLYMileticHLütjenSSoltekSDeckertMSchlüterD. Protective immunosurveillance of the central nervous system by Listeria-specific CD4 and CD8 T cells in systemic listeriosis in the absence of intracerebral Listeria. J Immunol (2002) 169(4):20109.10.4049/jimmunol.169.4.2010

  • 132

    HäuslerKGPrinzMNolteCWeberJRSchumannRRKettenmannHet alInterferon-gamma differentially modulates the release of cytokines and chemokines in lipopolysaccharide- and pneumococcal cell wall-stimulated mouse microglia and macrophages. Eur J Neurosci (2002) 16(11):211322.10.1046/j.1460-9568.2002.02287.x

  • 133

    AloisiFRiaFPennaGAdoriniL. Microglia are more efficient than astrocytes in antigen processing and in Th1 but not Th2 cell activation. J Immunol (1998) 160(10):467180.

  • 134

    FreiKSieplCGroscurthPBodmerSSchwerdelCFontanaA. Antigen presentation and tumor cytotoxicity by interferon-gamma-treated microglial cells. Eur J Immunol (1987) 17(9):12718.10.1002/eji.1830170909

  • 135

    FordALFoulcherELemckertFASedgwickJD. Microglia induce CD4 T lymphocyte final effector function and death. J Exp Med (1996) 184(5):173745.10.1084/jem.184.5.1737

  • 136

    KoyuncuOOHogueIBEnquistLW. Virus infections in the nervous system. Cell Host Microbe (2013) 13(4):37993.10.1016/j.chom.2013.03.010

  • 137

    WraithDCNicholsonLB. The adaptive immune system in diseases of the central nervous system. J Clin Invest (2012) 122(4):11729.10.1172/JCI58648

  • 138

    GriffinDEMetcalfT. Clearance of virus infection from the CNS. Curr Opin Virol (2011) 1(3):21621.10.1016/j.coviro.2011.05.021

  • 139

    MetcalfTUGriffinDE. Alphavirus-induced encephalomyelitis: antibody-secreting cells and viral clearance from the nervous system. J Virol (2011) 85(21):11490501.10.1128/JVI.05379-11

  • 140

    SavarinCBergmannCC. Neuroimmunology of central nervous system viral infections: the cells, molecules and mechanisms involved. Curr Opin Pharmacol (2008) 8(4):4729.10.1016/j.coph.2008.05.002

  • 141

    TschenSIStohlmanSARamakrishnaCHintonDRAtkinsonRDBergmannCC. CNS viral infection diverts homing of antibody-secreting cells from lymphoid organs to the CNS. Eur J Immunol (2006) 36(3):60312.10.1002/eji.200535123

  • 142

    BergmannCCLaneTEStohlmanSA. Coronavirus infection of the central nervous system: host-virus stand-off. Nat Rev Microbiol (2006) 4(2):12132.10.1038/nrmicro1343

  • 143

    IshiharaKHiranoT. IL-6 in autoimmune disease and chronic inflammatory proliferative disease. Cytokine Growth Factor Rev (2002) 13(4–5):35768.10.1016/S1359-6101(02)00027-8

  • 144

    LaneTEHardisonJLWalshKB. Functional diversity of chemokines and chemokine receptors in response to viral infection of the central nervous system. Curr Top Microbiol Immunol (2006) 303:127.

  • 145

    KleinRSLinEZhangBLusterADTollettJSamuelMAet alNeuronal CXCL10 directs CD8+ T-cell recruitment and control of West Nile virus encephalitis. J Virol (2005) 79(17):1145766.10.1128/JVI.79.17.11457-11466.2005

  • 146

    GlassWGLimJKCholeraRPletnevAGGaoJLMurphyPM. Chemokine receptor CCR5 promotes leukocyte trafficking to the brain and survival in West Nile virus infection. J Exp Med (2005) 202(8):108798.10.1084/jem.20042530

  • 147

    LaneTEAsensioVCYuNPaolettiADCampbellILBuchmeierMJ. Dynamic regulation of alpha- and beta-chemokine expression in the central nervous system during mouse hepatitis virus-induced demyelinating disease. J Immunol (1998) 160(2):9708.

  • 148

    PharesTWStohlmanSAHintonDRBergmannCC. Astrocyte-derived CXCL10 drives accumulation of antibody-secreting cells in the central nervous system during viral encephalomyelitis. J Virol (2013) 87(6):338292.10.1128/JVI.03307-12

  • 149

    OhJWSchwiebertLMBenvenisteEN. Cytokine regulation of CC and CXC chemokine expression by human astrocytes. J Neurovirol (1999) 5(1):8294.10.3109/13550289909029749

  • 150

    ColeKEStrickCAParadisTJOgborneKTLoetscherMGladueRPet alInterferon-inducible T cell alpha chemoattractant (I-TAC): a novel non-ELR CXC chemokine with potent activity on activated T cells through selective high affinity binding to CXCR3. J Exp Med (1998) 187(12):200921.10.1084/jem.187.12.2009

  • 151

    LusterADRavetchJV. Biochemical characterization of a gamma interferon-inducible cytokine (IP-10). J Exp Med (1987) 166(4):108497.10.1084/jem.166.4.1084

  • 152

    PharesTWStohlmanSABergmannCC. Intrathecal humoral immunity to encephalitic RNA viruses. Viruses (2013) 5(2):73252.10.3390/v5020732

  • 153

    TempletonSPKimTSO’MalleyKPerlmanS. Maturation and localization of macrophages and microglia during infection with a neurotropic murine coronavirus. Brain Pathol (2008) 18(1):4051.10.1111/j.1750-3639.2007.00098.x

  • 154

    ZuoJStohlmanSAHoskinJBHintonDRAtkinsonRBergmannCC. Mouse hepatitis virus pathogenesis in the central nervous system is independent of IL-15 and natural killer cells. Virology (2006) 350(1):20615.10.1016/j.virol.2006.01.027

  • 155

    XueSSunNVan RooijenNPerlmanS. Depletion of blood-borne macrophages does not reduce demyelination in mice infected with a neurotropic coronavirus. J Virol (1999) 73(8):632734.

  • 156

    KjeldsenLSengeløvHLollikeKNielsenMHBorregaardN. Isolation and characterization of gelatinase granules from human neutrophils. Blood (1994) 83(6):16409.

  • 157

    ZhouJStohlmanSAHintonDRMartenNW. Neutrophils promote mononuclear cell infiltration during viral-induced encephalitis. J Immunol (2003) 170(6):33316.10.4049/jimmunol.170.6.3331

  • 158

    ZhouJStohlmanSAAtkinsonRHintonDRMartenNW. Matrix metalloproteinase expression correlates with virulence following neurotropic mouse hepatitis virus infection. J Virol (2002) 76(15):737484.10.1128/JVI.76.15.7374-7384.2002

  • 159

    TrifiloMJLaneTE. The CC chemokine ligand 3 regulates CD11c+ CD11b+CD8alpha- dendritic cell maturation and activation following viral infection of the central nervous system: implications for a role in T cell activation. Virology (2004) 327(1):815.10.1016/j.virol.2004.06.027

  • 160

    MartenNWStohlmanSAZhouJBergmannCC. Kinetics of virus-specific CD8+ -T-cell expansion and trafficking following central nervous system infection. J Virol (2003) 77(4):27758.10.1128/JVI.77.4.2775-2778.2003

  • 161

    StilesLNHoskingMPEdwardsRAStrieterRMLaneTE. Differential roles for CXCR3 in CD4+ and CD8+ T cell trafficking following viral infection of the CNS. Eur J Immunol (2006) 36(3):61322.10.1002/eji.200535509

  • 162

    StilesLNLiuMTKaneJALaneTE. CXCL10 and trafficking of virus-specific T cells during coronavirus-induced demyelination. Autoimmunity (2009) 42(6):48491.10.1080/08916930902810708

  • 163

    WalshKBEdwardsRARomeroKMKotlajichMVStohlmanSALaneTE. Expression of CXC chemokine ligand 10 from the mouse hepatitis virus genome results in protection from viral-induced neurological and liver disease. J Immunol (2007) 179(2):115565.10.4049/jimmunol.179.2.1155

  • 164

    ChenBPKuzielWALaneTE. Lack of CCR2 results in increased mortality and impaired leukocyte activation and trafficking following infection of the central nervous system with a neurotropic coronavirus. J Immunol (2001) 167(8):458592.10.4049/jimmunol.167.8.4585

  • 165

    GlassWGLaneTE. Functional expression of chemokine receptor CCR5 on CD4+ T cells during virus-induced central nervous system disease. J Virol (2003) 77(1):1918.10.1128/JVI.77.1.191-198.2003

  • 166

    WeingerJGMarroBSHoskingMPLaneTE. The chemokine receptor CXCR2 and coronavirus-induced neurologic disease. Virology (2013) 435(1):1107.10.1016/j.virol.2012.08.049

  • 167

    BergmannCCAltmanJDHintonDStohlmanSA. Inverted immunodominance and impaired cytolytic function of CD8+ T cells during viral persistence in the central nervous system. J Immunol (1999) 163(6):337987.

  • 168

    BergmannCCParraBHintonDRChandranRMorrisonMStohlmanSA. Perforin-mediated effector function within the central nervous system requires IFN-gamma-mediated MHC up-regulation. J Immunol (2003) 170(6):320413.10.4049/jimmunol.170.6.3204

  • 169

    RamakrishnaCStohlmanSAAtkinsonRAHintonDRBergmannCC. Differential regulation of primary and secondary CD8+ T cells in the central nervous system. J Immunol (2004) 173(10):626573.10.4049/jimmunol.173.10.6265

  • 170

    LinMTStohlmanSAHintonDR. Mouse hepatitis virus is cleared from the central nervous systems of mice lacking perforin-mediated cytolysis. J Virol (1997) 71(1):38391.

  • 171

    GonzálezJMBergmannCCRamakrishnaCHintonDRAtkinsonRHoskinJet alInhibition of interferon-gamma signaling in oligodendroglia delays coronavirus clearance without altering demyelination. Am J Pathol (2006) 168(3):796804.10.2353/ajpath.2006.050496

  • 172

    ParraBHintonDRMartenNWBergmannCCLinMTYangCSet alIFN-gamma is required for viral clearance from central nervous system oligodendroglia. J Immunol (1999) 162(3):16417.

  • 173

    LintermanMABeatonLYuDRamiscalRRSrivastavaMHoganJJet alIL-21 acts directly on B cells to regulate Bcl-6 expression and germinal center responses. J Exp Med (2010) 207(2):35363.10.1084/jem.20091738

  • 174

    SabatRGrützGWarszawskaKKirschSWitteEWolkKet alBiology of interleukin-10. Cytokine Growth Factor Rev (2010) 21(5):33144.10.1016/j.cytogfr.2010.09.002

  • 175

    PharesTWMarquesCPStohlmanSAHintonDRBergmannCC. Factors supporting intrathecal humoral responses following viral encephalomyelitis. J Virol (2011) 85(6):258998.10.1128/JVI.02260-10

  • 176

    MetcalfTUBaxterVKNilaratanakulVGriffinDE. Recruitment and retention of B cells in the central nervous system in response to alphavirus encephalomyelitis. J Virol (2013) 87(5):24209.10.1128/JVI.01769-12

  • 177

    PuntambekarSSBergmannCCSavarinCKarpCLPharesTWParraGIet alShifting hierarchies of interleukin-10-producing T cell populations in the central nervous system during acute and persistent viral encephalomyelitis. J Virol (2011) 85(13):670213.10.1128/JVI.00200-11

  • 178

    GriffinDLevineBTyorWUbolSDesprèsP. The role of antibody in recovery from alphavirus encephalitis. Immunol Rev (1997) 159:15561.10.1111/j.1600-065X.1997.tb01013.x

  • 179

    RamakrishnaCBergmannCCAtkinsonRStohlmanSA. Control of central nervous system viral persistence by neutralizing antibody. J Virol (2003) 77(8):46708.10.1128/JVI.77.8.4670-4678.2003

  • 180

    HooperDCPharesTWFabisMJRoyA. The production of antibody by invading B cells is required for the clearance of rabies virus from the central nervous system. PLoS Negl Trop Dis (2009) 3(10):e535.10.1371/journal.pntd.0000535

  • 181

    FragkoudisRBallanyCMBoydAFazakerleyJK. In Semliki Forest virus encephalitis, antibody rapidly clears infectious virus and is required to eliminate viral material from the brain, but is not required to generate lesions of demyelination. J Gen Virol (2008) 89(Pt 10):25658.10.1099/vir.0.2008/002238-0

  • 182

    LevineBHardwickJMTrappBDCrawfordTOBollingerRCGriffinDE. Antibody-mediated clearance of alphavirus infection from neurons. Science (1991) 254(5033):85660.10.1126/science.1658936

  • 183

    LeeHSundenYOchiaiKUmemuraT. Experimental intracerebral vaccination protects mouse from a neurotropic virus by attracting antibody secreting cells to the CNS. Immunol Lett (2011) 139(1–2):1029.10.1016/j.imlet.2011.05.008

  • 184

    MarquesCPKapilPHintonDRHindingerCNuttSLRansohoffRMet alCXCR3-dependent plasma blast migration to the central nervous system during viral encephalomyelitis. J Virol (2011) 85(13):613647.10.1128/JVI.00202-11

  • 185

    GriffinDE. Recovery from viral encephalomyelitis: immune-mediated noncytolytic virus clearance from neurons. Immunol Res (2010) 47(1–3):12333.10.1007/s12026-009-8143-4

  • 186

    UbolSLevineBLeeSHGreenspanNSGriffinDE. Roles of immunoglobulin valency and the heavy-chain constant domain in antibody-mediated downregulation of Sindbis virus replication in persistently infected neurons. J Virol (1995) 69(3):19903.

  • 187

    DietzscholdBKaoMZhengYMChenZYMaulGFuZFet alDelineation of putative mechanisms involved in antibody-mediated clearance of rabies virus from the central nervous system. Proc Natl Acad Sci U S A (1992) 89(15):72526.10.1073/pnas.89.15.7252

  • 188

    NiedzielaNdamczyk-SowaMAPierzchalaK. Epidemiology and clinical record of multiple sclerosis in selected countries: a systematic review. Int J Neurosci (2014) 124(5):32230.10.3109/00207454.2013.840618

  • 189

    PiersonESimmonsSBCastelliLGovermanJM. Mechanisms regulating regional localization of inflammation during CNS autoimmunity. Immunol Rev (2012) 248(1):20515.10.1111/j.1600-065X.2012.01126.x

  • 190

    IslamTGaudermanWJCozenWHamiltonASBurnettMEMackTM. Differential twin concordance for multiple sclerosis by latitude of birthplace. Ann Neurol (2006) 60(1):5664.10.1002/ana.20871

  • 191

    PatsopoulosNABarcellosLFHintzenRQSchaeferCvan DuijnCMNobleJAet alFine-mapping the genetic association of the major histocompatibility complex in multiple sclerosis: HLA and non-HLA effects. PLoS Genet (2013) 9(11):e1003926.10.1371/journal.pgen.1003926

  • 192

    International Multiple Sclerosis Genetics Consortium (IMSGC)BeechamAHPatsopoulosNAXifaraDKDavisMFKemppinenAet alAnalysis of immune-related loci identifies 48 new susceptibility variants for multiple sclerosis. Nat Genet (2013) 45(11):135360.10.1038/ng.2770

  • 193

    van der MeiIAPonsonbyALDwyerTBlizzardLSimmonsRTaylorBVet alPast exposure to sun, skin phenotype, and risk of multiple sclerosis: case-control study. BMJ (2003) 327(7410):316.10.1136/bmj.327.7410.316

  • 194

    LassmannHNiedobitekGAloisiFMiddeldorpJMNeuroproMiSe EBV Working Group. Epstein-Barr virus in the multiple sclerosis brain: a controversial issue – report on a focused workshop held in the Centre for Brain Research of the Medical University of Vienna, Austria. Brain (2011) 134(Pt 9):277286.10.1093/brain/awr197

  • 195

    StromnesIMGovermanJM. Active induction of experimental allergic encephalomyelitis. Nat Protoc (2006) 1(4):18109.10.1038/nprot.2006.285

  • 196

    StromnesIMGovermanJM. Passive induction of experimental allergic encephalomyelitis. Nat Protoc (2006) 1(4):195260.10.1038/nprot.2006.284

  • 197

    KroenkeMACarlsonTJAndjelkovicAVSegalBM. IL-12- and IL-23-modulated T cells induce distinct types of EAE based on histology, CNS chemokine profile, and response to cytokine inhibition. J Exp Med (2008) 205(7):153541.10.1084/jem.20080159

  • 198

    OksenbergJRPanzaraMABegovichABMitchellDErlichHAMurrayRSet alSelection for T-cell receptor V beta-D beta-J beta gene rearrangements with specificity for a myelin basic protein peptide in brain lesions of multiple sclerosis. Nature (1993) 362(6415):6870.10.1038/362068a0

  • 199

    VogtJPaulFAktasOMüller-WielschKDörrJDörrSet alLower motor neuron loss in multiple sclerosis and experimental autoimmune encephalomyelitis. Ann Neurol (2009) 66(3):31022.10.1002/ana.21719

  • 200

    OtaKMatsuiMMilfordELMackinGAWeinerHLHaflerDA. T-cell recognition of an immunodominant myelin basic protein epitope in multiple sclerosis. Nature (1990) 346(6280):1837.10.1038/346183a0

  • 201

    AllegrettaMNicklasJASriramSAlbertiniRJ. T cells responsive to myelin basic protein in patients with multiple sclerosis. Science (1990) 247(4943):71821.10.1126/science.1689076

  • 202

    LeechMDBarrTATurnerDGBrownSO’ConnorRAGrayDet alCutting edge: IL-6-dependent autoimmune disease: dendritic cells as a sufficient, but transient, source. J Immunol (2013) 190(3):8815.10.4049/jimmunol.1202925

  • 203

    GreterMHeppnerFLLemosMPOdermattBMGoebelsNLauferTet alDendritic cells permit immune invasion of the CNS in an animal model of multiple sclerosis. Nat Med (2005) 11(3):32834.10.1038/nm1197

  • 204

    OlsonJKMillerSD. Microglia initiate central nervous system innate and adaptive immune responses through multiple TLRs. J Immunol (2004) 173(6):391624.10.4049/jimmunol.173.6.3916

  • 205

    OlsonJKGirvinAMMillerSD. Direct activation of innate and antigen-presenting functions of microglia following infection with Theiler’s virus. J Virol (2001) 75(20):97809.10.1128/JVI.75.20.9780-9789.2001

  • 206

    MayoLQuintanaFJWeinerHL. The innate immune system in demyelinating disease. Immunol Rev (2012) 248(1):17087.10.1111/j.1600-065X.2012.01135.x

  • 207

    KingILDickendesherTLSegalBM. Circulating Ly-6C+ myeloid precursors migrate to the CNS and play a pathogenic role during autoimmune demyelinating disease. Blood (2009) 113(14):31907.10.1182/blood-2008-07-168575

  • 208

    LiJGranBZhangGXVenturaESSiglientiIRostamiAet alDifferential expression and regulation of IL-23 and IL-12 subunits and receptors in adult mouse microglia. J Neurol Sci (2003) 215(1–2):95103.10.1016/S0022-510X(03)00203-X

  • 209

    El-BehiMCiricBDaiHYanYCullimoreMSafaviFet alThe encephalitogenicity of T(H)17 cells is dependent on IL-1- and IL-23-induced production of the cytokine GM-CSF. Nat Immunol (2011) 12(6):56875.10.1038/ni.2031

  • 210

    CodarriLGyülvésziGTosevskiVHesskeLFontanaAMagnenatLet alRORgammat drives production of the cytokine GM-CSF in helper T cells, which is essential for the effector phase of autoimmune neuroinflammation. Nat Immunol (2011) 12(6):5607.10.1038/ni.2027

  • 211

    KomiyamaYNakaeSMatsukiTNambuAIshigameHKakutaSet alIL-17 plays an important role in the development of experimental autoimmune encephalomyelitis. J Immunol (2006) 177(1):56673.10.4049/jimmunol.177.1.566

  • 212

    KebirHKreymborgKIferganIDodelet-DevillersACayrolRBernardMet alHuman TH17 lymphocytes promote blood-brain barrier disruption and central nervous system inflammation. Nat Med (2007) 13(10):11735.10.1038/nm1651

  • 213

    YePRodriguezFHKanalySStockingKLSchurrJSchwarzenbergerPet alRequirement of interleukin 17 receptor signaling for lung CXC chemokine and granulocyte colony-stimulating factor expression, neutrophil recruitment, and host defense. J Exp Med (2001) 194(4):51927.10.1084/jem.194.4.519

  • 214

    KimizukaYKimuraSSagaTIshiiMHasegawaNBetsuyakuTet alRoles of interleukin-17 in an experimental Legionella pneumophila pneumonia model. Infect Immun (2012) 80(3):11217.10.1128/IAI.05544-11

  • 215

    HuppertJCloshenDCroxfordAWhiteRKuligPPietrowskiEet alCellular mechanisms of IL-17-induced blood-brain barrier disruption. FASEB J (2010) 24(4):102334.10.1096/fj.09-141978

  • 216

    BauerJSminiaTWouterloodFGDijkstraCD. Phagocytic activity of macrophages and microglial cells during the course of acute and chronic relapsing experimental autoimmune encephalomyelitis. J Neurosci Res (1994) 38(4):36575.10.1002/jnr.490380402

  • 217

    BenvenisteEN. Cytokines: influence on glial cell gene expression and function. Chem Immunol (1997) 69:3175.10.1159/000058653

  • 218

    HuizingaRvan der StarBJKippMJongRGerritsenWClarnerTet alPhagocytosis of neuronal debris by microglia is associated with neuronal damage in multiple sclerosis. Glia (2012) 60(3):42231.10.1002/glia.22276

  • 219

    SerafiniBMagliozziRRosicarelliBReynoldsRZhengTSAloisiF. Expression of TWEAK and its receptor Fn14 in the multiple sclerosis brain: implications for inflammatory tissue injury. J Neuropathol Exp Neurol (2008) 67(12):113748.10.1097/NEN.0b013e31818dab90

  • 220

    KawanokuchiJShimizuKNittaAYamadaKMizunoTTakeuchiHet alProduction and functions of IL-17 in microglia. J Neuroimmunol (2008) 194(1–2):5461.10.1016/j.jneuroim.2007.11.006

  • 221

    DoringAYongVW. The good, the bad and the ugly. Macrophages/microglia with a focus on myelin repair. Front Biosci (Schol Ed) (2011) 3:84656.10.2741/191

  • 222

    KettenmannHHanischUKNodaMVerkhratskyA. Physiology of microglia. Physiol Rev (2011) 91(2):461553.10.1152/physrev.00011.2010

  • 223

    RansohoffRMPerryVH. Microglial physiology: unique stimuli, specialized responses. Annu Rev Immunol (2009) 27:11945.10.1146/annurev.immunol.021908.132528

  • 224

    StadelmannCKerschensteinerMMisgeldTBrückWHohlfeldRLassmannH. BDNF and gp145trkB in multiple sclerosis brain lesions: neuroprotective interactions between immune and neuronal cells?Brain (2002) 125(Pt 1):7585.10.1093/brain/awf015

  • 225

    DuncanDSMillerSD. CNS expression of B7-H1 regulates pro-inflammatory cytokine production and alters severity of Theiler’s virus-induced demyelinating disease. PLoS One (2011) 6(4):e18548.10.1371/journal.pone.0018548

  • 226

    Van Der VoornPTekstraJBeelenRHTensenCPVan Der ValkPDe GrootCJ. Expression of MCP-1 by reactive astrocytes in demyelinating multiple sclerosis lesions. Am J Pathol (1999) 154(1):4551.10.1016/S0002-9440(10)65249-2

  • 227

    MajumderSZhouLZRansohoffRM. Transcriptional regulation of chemokine gene expression in astrocytes. J Neurosci Res (1996) 45(6):75869.10.1002/(SICI)1097-4547(19960915)45:6<758::AID-JNR12>3.0.CO;2-S

  • 228

    GlabinskiARBalasingamVTaniMKunkelSLStrieterRMYongVWet alChemokine monocyte chemoattractant protein-1 is expressed by astrocytes after mechanical injury to the brain. J Immunol (1996) 156(11):43638.

  • 229

    Toft-HansenHFuchtbauerLOwensT. Inhibition of reactive astrocytosis in established experimental autoimmune encephalomyelitis favors infiltration by myeloid cells over T cells and enhances severity of disease. Glia (2011) 59(1):16676.10.1002/glia.21088

  • 230

    CalderonTMEugeninEALopezLKumarSSHesselgesserJRaineCSet alA role for CXCL12 (SDF-1alpha) in the pathogenesis of multiple sclerosis: regulation of CXCL12 expression in astrocytes by soluble myelin basic protein. J Neuroimmunol (2006) 177(1–2):2739.10.1016/j.jneuroim.2006.05.003

  • 231

    ZhangKMcQuibbanGASilvaCButlerGSJohnstonJBHoldenJet alHIV-induced metalloproteinase processing of the chemokine stromal cell derived factor-1 causes neurodegeneration. Nat Neurosci (2003) 6(10):106471.10.1038/nn1127

  • 232

    NashBIoannidouKBarnettSC. Astrocyte phenotypes and their relationship to myelination. J Anat (2011) 219(1):4452.10.1111/j.1469-7580.2010.01330.x

Summary

Keywords

neuroimmunology, non-tumor antigens, glial cells, CNS autoimmunity, blood–brain barrier, CNS infections

Citation

Huber AK, Duncker PC and Irani DN (2014) Immune Responses to Non-Tumor Antigens in the Central Nervous System. Front. Oncol. 4:328. doi: 10.3389/fonc.2014.00328

Received

02 October 2014

Accepted

30 October 2014

Published

13 November 2014

Volume

4 - 2014

Edited by

Lois A. Lampson, Harvard Medical School, USA

Reviewed by

Thomas E. Lane, University of Utah, USA; Cornelia Bergmann, Cleveland Clinic, USA

Copyright

*Correspondence: David N. Irani, Department of Neurology, University of Michigan Medical School, 109 Zina Pitcher Place, 4007 Biomedical Sciences Research Building, Ann Arbor, MI 48109-2200, USA e-mail:

This article was submitted to Neuro-Oncology, a section of the journal Frontiers in Oncology.

Disclaimer

All claims expressed in this article are solely those of the authors and do not necessarily represent those of their affiliated organizations, or those of the publisher, the editors and the reviewers. Any product that may be evaluated in this article or claim that may be made by its manufacturer is not guaranteed or endorsed by the publisher.

Outline

Figures

Cite article

Copy to clipboard


Export citation file


Share article

Article metrics